title: Cerebellar dentate dysplasia.
abstract: Dysplasia of the cerebellar dentate nucleus is a state of apparent maturational arrest that involves the cerebellar dentate nucleus. Origins include Joubert syndrome, other disorders of axon guidance and dentato-olivary dysplasia. An overview is given, linking the diverse etiologies.
authors: Emma Children's Hospital/AMC, University of Amsterdam, Meibergdreef 9, 1105 AZ Amsterdam, The Netherlands. p.g.barth@amc.uva.nl
authors: Peter G
authors: PG
authors: Barth
mesh_terms: D000015:Abnormalities, Multiple; D002526:Cerebellar Diseases / Q000150:complications / Q000209:etiology / Q000473:pathology* / Q000503:physiopathology*; D002529:Cerebellar Nuclei / Q000002:abnormalities* / Q000033:anatomy & histology / Q000196:embryology* / Q000503:physiopathology*; D002531:Cerebellum / Q000002:abnormalities; D005124:Eye Abnormalities / Q000150:complications; D006801:Humans; D052177:Kidney Diseases, Cystic / Q000150:complications; D009421:Nervous System Malformations / Q000209:etiology / Q000473:pathology* / Q000503:physiopathology*; D009434:Neural Pathways / Q000002:abnormalities / Q000196:embryology; D009847:Olivary Nucleus / Q000002:abnormalities / Q000196:embryology / Q000503:physiopathology; D012160:Retina / Q000002:abnormalities