title: Goldston syndrome.
abstract: Goldston syndrome is a rare entity describing the association of polycystic kidneys and Dandy Walker malformation with or without hepatic fibrosis. A 28 years old pregnant woman came to radiology department for the first antenatal scan. Ultrasound showed a single fetus corresponding to 27 week of gestation. The fetal brain revealed deficient vermis with a posterior fossa cyst communicating with the 4th ventricle suggestive of Dandy-Walker malformation (DWM). The kidneys were enlarged, and echogenic containing small cysts with associated amniotic fluid index of 5 cm suggestive of oligohydramnios. A diagnosis of Goldston syndrome was suggested. These findings were confirmed on post natal head and renal ultrasound.
authors: Department of Radiology, The Aga Khan University Hospital, Karachi.
authors: Zainab
authors: Z
authors: Hussain
authors: Imrana
authors: I
authors: Masroor
authors: Qurrat-Ul-Ain
authors: QU
authors: Haider
authors: Tariq
authors: T
authors: Alam
mesh_terms: D000015:Abnormalities, Multiple / Q000000981:diagnostic imaging; D000328:Adult; D003616:Dandy-Walker Syndrome / Q000000981:diagnostic imaging; D005260:Female; D006801:Humans; D007231:Infant, Newborn; D010181:Pancreatic Cyst / Q000000981:diagnostic imaging; D011247:Pregnancy; D011256:Pregnancy Outcome; D016216:Ultrasonography, Prenatal