title: Is Langerhan cell histiocytosis complicated with hydrops fetalis exclusively lethal in premature neonates?
abstract: Langerhans cell histiocytosis is a rare disease and is lethal in premature neonates. A male premature neonate born at gestational 33 weeks presented with generalized vesicles, hydrops fetalis with pleural effusion, bilateral cataracts, and severe respiratory distress syndrome complicated with persistent pulmonary hypertension. Skin biopsy confirmed the diagnosis of Langerhans cell histiocytosis.
authors: Department of Pediatrics, Shin Kong Wu Ho-Su Memorial Hospital, Taipei, Taiwan.
authors: I
authors: I
authors: Cheng
authors: Yi-Lin
authors: YL
authors: Chen
authors: Yu-Luan
authors: YL
authors: Tsai
authors: Yuh-Yu
authors: YY
authors: Chou
authors: Tseng-Chen
authors: TC
authors: Sung
authors: Shu-Chi
authors: SC
authors: Mu
mesh_terms: D002386:Cataract / Q000175:diagnosis; D017809:Fatal Outcome; D006646:Histiocytosis, Langerhans-Cell / Q000150:complications / Q000151:congenital / Q000175:diagnosis* / Q000473:pathology; D006801:Humans; D015160:Hydrops Fetalis / Q000175:diagnosis* / Q000209:etiology / Q000473:pathology; D006976:Hypertension, Pulmonary / Q000175:diagnosis / Q000209:etiology; D007231:Infant, Newborn; D007234:Infant, Premature; D008297:Male; D010996:Pleural Effusion / Q000175:diagnosis / Q000209:etiology; D012127:Respiratory Distress Syndrome, Newborn / Q000175:diagnosis / Q000209:etiology; D012720:Severity of Illness Index; D012871:Skin Diseases / Q000175:diagnosis / Q000473:pathology