title: Extraosseous chordoma of nasopharynx in paediatric age.
abstract: Intracranial chordomas are relatively rare locally aggressive tumours that probably originate from embryonic remnants of the notochord. They typically arise from the sacrum and secondly in the skull base/clivus region. When skull base chordomas occur at an extraosseous location (without lytic bone destruction), they may mimic other lesions of the nasopharynx. We present a case of primarily extraosseous chordoma in paediatric age, involving the nasopharynx, to improve preoperative diagnosis and postoperative management of this rare tumour.
authors: Servicio de Otorrinolaringología, Hospital Universitario de Alicante, Alicante, Spain. jhoxasagui@hotmail.com
authors: Jhonder Xavier
authors: JX
authors: Salazar Guilarte
authors: Manuela
authors: M
authors: Sancho Mestre
authors: Juan Ramón
authors: JR
authors: Gras Albert
mesh_terms: D002648:Child; D002817:Chordoma / Q000150:complications / Q000175:diagnosis / Q000532:radiotherapy / Q000601:surgery*; D003646:Debridement; D004724:Endoscopy; D005260:Female; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D008875:Middle Aged; D015508:Nasal Obstruction / Q000209:etiology; D009303:Nasopharyngeal Neoplasms / Q000150:complications / Q000175:diagnosis / Q000532:radiotherapy / Q000601:surgery*; D010034:Otitis Media with Effusion / Q000150:complications; D016634:Radiosurgery; D018714:Radiotherapy, Adjuvant; D050397:Radiotherapy, Intensity-Modulated; D012074:Remission Induction