title: Cochlear implantation in patients affected by superficial hemosiderosis of the central nervous system.
abstract: The objectives of the study were to: report three more cases of cochlear implantation (CI) in patients affected by superficial hemosiderosis of the central nervous system (SH-CNS); assess whether CI may be a viable option in this disease. The study was conducted in a tertiary referral center. Pre-operative and post-operative clinical notes of three patients with SH-CNS were reviewed. Two out of three cases showed very good results with CI in sentence perception in noise over 90%. For the other case, hearing performance was very low. He showed only disyllabic word identification abilities in a closed set (40%). Cochlear implantation may be a viable option for patients with severe to profound sensorineural hearing loss due to SH-CNS. In these cases, an adequate pre-operative counseling, explaining the possibility of poor post-operative results and/or the worsening of the outcomes in the following years, is important.
authors: Otology and Cochlear Implant Unit, University-Hospital of Pisa, Cisanello, Via Paradisa 2, 56124 Pisa, Italy. s.berrettini@med.unipi.it
authors: S
authors: S
authors: Berrettini
authors: A
authors: A
authors: De Vito
authors: L
authors: L
authors: Bruschini
authors: S
authors: S
authors: Fortunato
authors: F
authors: F
authors: Forli
mesh_terms: D000328:Adult; D000368:Aged; D001301:Audiometry, Pure-Tone; D002493:Central Nervous System Diseases / Q000150:complications* / Q000175:diagnosis / Q000601:surgery; D019929:Cochlear Implantation; D006319:Hearing Loss, Sensorineural / Q000175:diagnosis / Q000209:etiology / Q000601:surgery*; D006486:Hemosiderosis / Q000150:complications* / Q000175:diagnosis / Q000601:surgery; D006801:Humans; D020300:Intracranial Hemorrhages / Q000150:complications* / Q000175:diagnosis / Q000601:surgery; D008279:Magnetic Resonance Imaging; D008297:Male; D013346:Subarachnoid Space / Q000473:pathology