title: Ribbing disease: a case report and literature review.
abstract: Ribbing disease (RD) is a rare bone dysplasia characterized by benign endosteal and periosteal new bone formation confined to the diaphysis of the long bones of the lower extremities in young adults. The etiology and optimal treatment for the disease are unknown. It is often initially diagnosed as a low-grade osteomyelitis or a bone-forming neoplasia. It may also be confused with other causes of increased bone density. The onset is usually after puberty and the most common presenting symptom is pain that does not resolve with medical treatment and sometimes is intolerable. We report the case of a 22-year old woman with clinical and radiological manifestations of RD. In spite of different medical treatment modalities, pain did not resolve and the patient consulted multiple physicians. Intramedullary reaming of the tibia was performed to relieve the severe pain. To the authors' knowledge, in this report we present a case of RD for the third time in the orthopaedic literature and also she is the second case in the English literature to undergo a definite surgical treatment modality as intramedullary reaming for the solution of her pain. Owing to the rarity of the disease we aimed to report the complete findings of our encounter with the disease and to emphasize the role of an orthopaedic surgeon in consultation and intervention for the treatment of intolerable pain which is the most important symptom of this disease.
authors.affiliation: Department of Orthopedics and Traumatology, Ministry of Health, Istanbul Training and Research Hospital, Istanbul, Turkey. yozturkmen@yahoo.com.tr
authors.forename: Yusuf
authors.initials: Y
authors.lastname: Oztürkmen
authors.forename: Mahmut
authors.initials: M
authors.lastname: Karamehmetoğlu
mesh_terms: D000893:Anti-Inflammatory Agents / Q000627:therapeutic use*; D003966:Camurati-Engelmann Syndrome / Q000175:diagnosis / Q000188:drug therapy / Q000601:surgery; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D008279:Magnetic Resonance Imaging; D019637:Orthopedic Procedures; D010017:Osteoma, Osteoid / Q000175:diagnosis / Q000188:drug therapy / Q000601:surgery; D011379:Prognosis; D014057:Tomography, X-Ray Computed; D055815:Young Adult
chemical_list: D000893:Anti-Inflammatory Agents