title: Dental management in autosomal recessive (intermediate) osteopetrosis: a case report.
abstract: Osteopetrosis (Albers-Schonberg disease) is the name given to a group of diseases that affect the growth and remodeling of bones. It is characterized by overgrowth and sclerosis of bone, resulting in thickening and narrowing of the marrow cavities throughout the skeleton. The exact cause is unknown, although failure of bone resorption related to defective osteoclasts is considered to be the basis of the problem. These patients present a significant challenge to the dentist for management of jaw and dental problems, as the disease process demands special strategies which are often at variance with conventional dentistry. The purpose of this paper was to report the management and follow-up of a child with intermediate autosomal recessive osteopetrosis who primarily complained of dental problems.
authors.affiliation: Department of Oral and Maxillofacial Surgery, Subharti Dental College and Hospital, Meerut, Uttar Pradesh, India. drbansalvishal@rediffmail.com
authors.forename: Vishal
authors.initials: V
authors.lastname: Bansal
authors.forename: Sanjeev
authors.initials: S
authors.lastname: Kumar
authors.forename: K V
authors.initials: KV
authors.lastname: Arunkumar
authors.forename: Apoorva
authors.initials: A
authors.lastname: Mowar
authors.forename: Gagan
authors.initials: G
authors.lastname: Khare
mesh_terms: D000293:Adolescent; D017742:Dental Care for Chronically Ill / Q000379:methods*; D003779:Denture Design; D003824:Denture, Complete; D005260:Female; D006801:Humans; D007576:Jaw, Edentulous, Partially / Q000150:complications* / Q000000981:diagnostic imaging / Q000534:rehabilitation / Q000601:surgery; D008336:Mandibular Diseases / Q000150:complications* / Q000000981:diagnostic imaging / Q000601:surgery; D010019:Osteomyelitis / Q000209:etiology / Q000628:therapy; D010022:Osteopetrosis / Q000150:complications* / Q000235:genetics / Q000628:therapy; D011859:Radiography; D014097:Tooth, Unerupted / Q000000981:diagnostic imaging / Q000209:etiology* / Q000601:surgery