title: Anesthesia for pheochromocytoma resection in a child with Fontan circulation.
abstract: OBJECTIVE
  To report the anesthetic management of a successful resection of a pheochromocytoma in a child with a completed Fontan circulation.
  
  
  METHODS
  The patient was an 11-yr-old boy with Ivemark syndrome who had undergone Fontan palliation at three years of age. Six weeks earlier, he had been diagnosed with a norepinephrine-producing pheochromocytoma, and he had been pretreated with oral propranolol and phenoxybenzamine. During surgery, intravenous administration of magnesium sulphate, esmolol, and phentolamine provided good hemodynamic control. Postoperatively, the patient tended to be hypotensive, and treatment with fluid administration resulted in prolonged intensive care.
  
  
  CONCLUSIONS
  Although intraoperative management was not problematic, postoperative care of this 11-yr old child with pheochromocytoma was complicated by residual sympathetic blockade.
authors.affiliation: Department of Anesthesiology and Pain Medicine, Seattle Children's Hospital and the University of Washington School of Medicine, 4800 Sand Point Way NE, Seattle, WA, 98105, USA.
authors.forename: Thomas R
authors.initials: TR
authors.lastname: Latendresse
authors.affiliation: Department of Surgery, Seattle Children's Hospital and the University of Washington School of Medicine, Seattle, WA, USA.
authors.forename: Adam B
authors.initials: AB
authors.lastname: Goldin
authors.affiliation: Department of Anesthesiology and Pain Medicine, Seattle Children's Hospital and the University of Washington School of Medicine, 4800 Sand Point Way NE, Seattle, WA, 98105, USA. christer.jonmarker@seattlechildrens.org.
authors.forename: Christer
authors.initials: C
authors.lastname: Jonmarker
mesh_terms: D000015:Abnormalities, Multiple / Q000601:surgery; D000758:Anesthesia / Q000379:methods*; D002648:Child; D018729:Fontan Procedure / Q000379:methods*; D006330:Heart Defects, Congenital / Q000601:surgery; D059446:Heterotaxy Syndrome; D006801:Humans; D007022:Hypotension / Q000209:etiology; D008297:Male; D009638:Norepinephrine / Q000378:metabolism; D010673:Pheochromocytoma / Q000601:surgery*; D011182:Postoperative Care / Q000379:methods; D011300:Preoperative Care / Q000379:methods; D013158:Splenic Diseases / Q000151:congenital / Q000601:surgery
chemical_list: D009638:Norepinephrine