title: [Pycnodysostosis: a case report].
abstract: A 53-year-old man suffered maxillar osteomyelitis and removal of sequester was scheduled under general anesthesia. Pycnodysostosis had been diagnosed in childhood and body height and weight were 148 cm and 40 kg, respectively. He presented facial dysmorphia, hypomobile mandible and narrow oral cavity. At the pre-anesthetic visit, we planned awake fiberscopic intubation before the induction of general anesthesia. On the day of surgery, however, face-mask ventilation was easily established with 100-microg dose of fentanyl. Thus, 70 mg of propofol was administered to achieve hypnosis and naso-tracheal intubation using fibrescope was accomplished. The patient's trachea was easily intubated without a decrease of pulse oximetry values and marked changes in cardiovascular parameters. Pycnodysostosis is a rare clinical entity; however, the airway difficulty was mild in the present case.
authors.affiliation: Department of Anesthesia and Resuscitation, Hamamatsu University School of Medicine, Hamamatsu 431-3192.
authors.forename: Wakana
authors.initials: W
authors.lastname: Toriyama
authors.forename: Tadayoshi
authors.initials: T
authors.lastname: Kurita
authors.forename: Yushi
authors.initials: Y
authors.lastname: Adachi
authors.forename: Yuji
authors.initials: Y
authors.lastname: Suzuki
authors.forename: Yukako
authors.initials: Y
authors.lastname: Obata
authors.forename: Shigehito
authors.initials: S
authors.lastname: Sato
mesh_terms: D000768:Anesthesia, General / Q000379:methods*; D006801:Humans; D006991:Hypnosis, Anesthetic / Q000379:methods; D007442:Intubation, Intratracheal / Q000379:methods; D008297:Male; D008439:Maxillary Diseases / Q000601:surgery*; D008875:Middle Aged; D010019:Osteomyelitis / Q000601:surgery*; D058631:Pycnodysostosis / Q000150:complications*