title: Keratosis follicularis spinulosa decalvans in a female.
abstract: Keratosis follicularis spinulosa decalvans (KFSD), is a rare follicular syndrome associated with widespread keratosis pilaris and progressive scarring alopecia. This genodermatoses often starts at infancy or early childhood with an X-linked mode of inheritance. Males are predominantly affected and females frequently show no disease or only a mild form. We describe this not so common entity of KFSD in a nine year old female child.
authors.affiliation: Department of Dermatology, St. John's Medical College and Hospital, Koramangala, Bangalore, Karnataka-560 034, India. dr_fiona@rediffmail.com
authors.forename: Fiona F
authors.initials: FF
authors.lastname: Sequeira
authors.forename: Elizabeth
authors.initials: E
authors.lastname: Jayaseelan
mesh_terms: D001706:Biopsy; D002610:Cheek / Q000473:pathology; D002648:Child; D005138:Eyebrows / Q000473:pathology; D005260:Female; D040181:Genetic Diseases, X-Linked; D006801:Humans; D007057:Ichthyosis / Q000473:pathology; D012535:Scalp / Q000473:pathology*; D012873:Skin Diseases, Genetic