title: Thrombotic thrombocytopenic purpura in IgG4-related disease with severe deficiency of ADAMTS-13 activity and IgG4 autoantibody against ADAMTS-13.
authors.affiliation: Department of Internal Medicine, Nagaoka Red Cross Hospital,2-297-1 Senshu, Nagaoka, Niigata, Japan. saekit@nagaoka.jrc.or.jp
authors.forename: Takako
authors.initials: T
authors.lastname: Saeki
authors.forename: Tomoyuki
authors.initials: T
authors.lastname: Ito
authors.forename: Akira
authors.initials: A
authors.lastname: Youkou
authors.forename: Hajime
authors.initials: H
authors.lastname: Ishiguro
authors.forename: Naoko
authors.initials: N
authors.lastname: Sato
authors.forename: Hajime
authors.initials: H
authors.lastname: Yamazaki
authors.forename: Tadashi
authors.initials: T
authors.lastname: Koike
authors.forename: Hiroyo
authors.initials: H
authors.lastname: Kourakata
authors.forename: Silvia
authors.initials: S
authors.lastname: Ferrari
authors.forename: Friedrich
authors.initials: F
authors.lastname: Scheiflinger
authors.forename: Ichiei
authors.initials: I
authors.lastname: Narita
mesh_terms: D051722:ADAM Proteins / Q000172:deficiency* / Q000276:immunology; D000071120:ADAMTS13 Protein; D001323:Autoantibodies / Q000097:blood* / Q000276:immunology; D001327:Autoimmune Diseases / Q000097:blood / Q000150:complications* / Q000175:diagnosis / Q000276:immunology; D006801:Humans; D007074:Immunoglobulin G / Q000097:blood* / Q000276:immunology; D008297:Male; D008875:Middle Aged; D011697:Purpura, Thrombotic Thrombocytopenic / Q000097:blood / Q000150:complications* / Q000473:pathology / Q000628:therapy; D012720:Severity of Illness Index; D016896:Treatment Outcome
chemical_list: D001323:Autoantibodies; D007074:Immunoglobulin G; D051722:ADAM Proteins; D000071120:ADAMTS13 Protein; C099604:ADAMTS13 protein, human