title: Root dilation in patients with truncus arteriosus.
abstract: OBJECTIVE
  A dilated aortic root is a common finding in children and adults with some forms of congenital heart defects. No data exist on root dilation in truncus arteriosus. We sought to delineate root dimensions across a population of patients with truncus arteriosus.
  
  
  METHODS
  We performed a single-center retrospective review of all patients with truncus arteriosus. Demographic information, clinical history, and most recent echocardiographic data were evaluated.
  
  
  RESULTS
  We identified 76 patients whose most recent study was at a median age of 5.4 years (range 0--32.7 years). Mean truncal root z-score was 5.1 ± 2.3. All but three patients had truncal root z-scores greater than or equal to 2. Truncal root z-scores remained stable with increasing body surface area and age. There were no cases of dissection or rupture. Six patients underwent truncal root surgery, typically for indications of root dilation with significant truncal valve insufficiency and left ventricular dilation.
  
  
  CONCLUSIONS
  In conclusion, mean truncal root z-score was 5, and all but three patients had truncal root z-scores greater than or equal to 2. Although repeat surgical intervention was rare and major complications related to root dilation did not occur in our cohort, further studies with longitudinal follow-up into adulthood are needed.
authors.affiliation: Division of Pediatric Cardiology, The University of Alabama at Birmingham, Birmingham, AL, USA. wfcarlo@peds.uab.edu
authors.forename: Waldemar F
authors.initials: WF
authors.lastname: Carlo
authors.forename: E Dean
authors.initials: ED
authors.lastname: McKenzie
authors.forename: Timothy C
authors.initials: TC
authors.lastname: Slesnick
mesh_terms: D000293:Adolescent; D000328:Adult; D000367:Age Factors; D001830:Body Surface Area; D016009:Chi-Square Distribution; D002648:Child; D002675:Child, Preschool; D004108:Dilatation, Pathologic; D006801:Humans; D007223:Infant; D011379:Prognosis; D012044:Regression Analysis; D012189:Retrospective Studies; D013781:Texas; D014338:Truncus Arteriosus / Q000002:abnormalities / Q000473:pathology*; D014339:Truncus Arteriosus, Persistent / Q000473:pathology* / Q000628:therapy; D055815:Young Adult