title: Hypoplastic left heart syndrome in context.
abstract: Hypoplastic left heart syndrome is a rare condition requiring major cardiac surgery during the neonatal period to sustain life, with subsequent procedures culminating in completion of the Fontan circulation - the common pathway for all 'single ventricle' conditions. Algorithms for care of these children are now well defined with predictable medium-term outcomes with the majority achieving a Fontan circulation. Hypoplastic left heart syndrome is one of a group of conditions that require complex surgery as a neonate and require a similar perioperative approach. Antenatal diagnosis is common in this patient subgroup, and there is a significant body of work that can be drawn on to inform parental choice.
authors.affiliation: Heart Centre for Children, The Children's Hospital at Westmead, New South Wales, Australia. davidw@chw.edu.au
authors.forename: David S
authors.initials: DS
authors.lastname: Winlaw
authors.forename: Nadia
authors.initials: N
authors.lastname: Badawi
authors.forename: Stephen
authors.initials: S
authors.lastname: Jacobe
authors.forename: Nadine A
authors.initials: NA
authors.lastname: Kasparian
authors.forename: Stephen G
authors.initials: SG
authors.lastname: Cooper
authors.forename: David N
authors.initials: DN
authors.lastname: Murphy
authors.forename: Megan C
authors.initials: MC
authors.lastname: Sherwood
authors.forename: Philip
authors.initials: P
authors.lastname: Roberts
authors.forename: Karen
authors.initials: K
authors.lastname: Leclair
authors.forename: Gabbie
authors.initials: G
authors.lastname: Scarfe
authors.forename: Gary F
authors.initials: GF
authors.lastname: Sholler
mesh_terms: D018729:Fontan Procedure; D006801:Humans; D018636:Hypoplastic Left Heart Syndrome / Q000601:surgery*; D007223:Infant; D011379:Prognosis; D012307:Risk Factors; D016896:Treatment Outcome