title: Rhabdomyoma of the interventricular septum presenting as a Brugada phenocopy.
abstract: Brugada syndrome is a channelopathy characterised electrocardiographically by distinctive coved ST-segment elevation in the right precordial leads and is associated with a predisposition for sudden death secondary to ventricular arrhythmias in otherwise healthy patients. Previously known as Brugada-like patterns, Brugada phenocopies include agents and conditions that mimic true Brugada syndrome, presenting with an acquired Brugada Type-1 ECG pattern. We describe the first reported case of a 17-month-old female with an asymptomatic rhabdomyoma of the interventricular septum that presented as a Brugada phenocopy.
authors.affiliation: Division of Cardiology, Kingston General Hospital, Queen's University, Canada.
authors.forename: Timothy
authors.initials: T
authors.lastname: Nguyen
authors.forename: John
authors.initials: J
authors.lastname: Smythe
authors.forename: Adrian
authors.initials: A
authors.lastname: Baranchuk
mesh_terms: D053840:Brugada Syndrome / Q000209:etiology*; D005260:Female; D006338:Heart Neoplasms / Q000150:complications*; D006801:Humans; D007231:Infant, Newborn; D012207:Rhabdomyoma / Q000150:complications*; D054088:Ventricular Septum