title: Extended replacement of a calcified ascending aorta in adulthood sporadic, diffuse type, supravalvular aortic stenosis.
abstract: The diffuse variant of supravalvular aortic stenosis (SVAS) is one of the most rare congenital vascular pathological conditions of adulthood. Due to its rarity, surgical treatment of this clinical entity is still a matter of debate because of the variable degree of aortic narrowing, presence of multilevel obstruction, and age at presentation, all factors that strongly influence the disease prognosis. We report a case of an adult patient with an extremely calcified diffuse SVAS who underwent successful replacement of the ascending aorta through the interposition of a tubular prosthesis. Six months' follow-up showed complete relief of the aortic gradient and an improvement in clinical performance.
authors.affiliation: Department of Cardiac Surgery, Santa Maria Hospital, Terni, Italy. v.borghetti@alice.it
authors.forename: Valentino
authors.initials: V
authors.lastname: Borghetti
authors.forename: Giancarlo
authors.initials: G
authors.lastname: D'Addario
authors.forename: Ilaria
authors.initials: I
authors.lastname: Bravi
authors.forename: Alessandro
authors.initials: A
authors.lastname: Pardinia
mesh_terms: D000792:Angiography; D001013:Aorta, Thoracic; D001018:Aortic Diseases / Q000150:complications / Q000175:diagnosis / Q000601:surgery*; D021921:Aortic Stenosis, Supravalvular / Q000151:congenital* / Q000175:diagnosis / Q000601:surgery; D001807:Blood Vessel Prosthesis; D002114:Calcinosis / Q000150:complications / Q000175:diagnosis / Q000601:surgery*; D003937:Diagnosis, Differential; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D021621:Imaging, Three-Dimensional; D008875:Middle Aged; D014057:Tomography, X-Ray Computed