title: Pulmonary alveolar proteinosis in children: a case series.
abstract: Pulmonary alveolar proteinosis, (PAP) is a rare disease of unknown etiology, characterized by accumulation of intraalveolar proteinaceous material which is rich in lipid and positive on periodic acid-Schiff stain. Two clinically different pediatric types have been defined as congenital PAP which is fulminant and fatal, and a late-onset PAP which is similar to the adult form and less severe. Eight children with late-onset PAP were hospitalized from 1998 to 2005 in Mofid Children Hospital. Characteristics of these patients and the methods of diagnosis and treatment are presented in this case series.
authors.affiliation: Assistant Professor of Pediatrics, Pediatric Pulmonary Fellowship, Mofid Children Hospital, Shahid Beheshti Medical University, Tehran, Iran.
authors.forename: Seyyed Ahmad
authors.initials: SA
authors.lastname: Tabatabaei
authors.forename: Abdollah
authors.initials: A
authors.lastname: Karimi
authors.forename: Sedigheh Rafiee
authors.initials: SR
authors.lastname: Tabatabaei
authors.forename: Badiozzaman
authors.initials: B
authors.lastname: Radpay
authors.forename: Farzaneh
authors.initials: F
authors.lastname: Jadali
authors.forename: Farideh
authors.initials: F
authors.lastname: Shiva
authors.forename: Mana Hadipour
authors.initials: MH
authors.lastname: Jahromy