title: The Wunderlich's syndrome secondary to massive bilateral angiomyolipomas associated with advanced tuberous sclerosis.
abstract: The Wunderlich Syndrome refers to spontaneous perirenal hemorrhage often associated with underlying renal pathology. We report the case of a 23-year-old female with advanced tuberous sclerosis who presented in hypovolemic shock secondary to rupture of one of her massive bilateral angiomyolipomas (AMLs). The patient was able to be managed conservatively and subsequently retained full renal function. A review of the literature with a discussion of types of clinical presentation, diagnostic criteria, and methods of management of AMLs is included.
authors.affiliation: Western Reserve Care System/Northeastern Ohio College of Medicine, OH, USA. Afirebrand@gmail.com
authors.forename: Dorothy
authors.initials: D
authors.lastname: Sparks
authors.forename: Daniel
authors.initials: D
authors.lastname: Chase
authors.forename: David
authors.initials: D
authors.lastname: Thomas
authors.forename: Jon
authors.initials: J
authors.lastname: Arnott
mesh_terms: D000328:Adult; D018207:Angiomyolipoma / Q000150:complications*; D001416:Back Pain / Q000209:etiology; D005260:Female; D006470:Hemorrhage / Q000209:etiology*; D006801:Humans; D007680:Kidney Neoplasms / Q000150:complications*; D012187:Retroperitoneal Space; D012422:Rupture, Spontaneous / Q000150:complications; D013577:Syndrome; D014402:Tuberous Sclerosis / Q000150:complications; D055815:Young Adult