title: [Intra-abdominal desmoid tumor mimicking a pancreatic tumor in a patient with familial colonic polyposis].
abstract: BACKGROUND
  Fibromatosis consists of a benign fibroblastic proliferation with local infiltrative growth. Two types are recognized: a superficial and a deep form, also known as desmoid tumor. The latter may occur sporadically or in association with familial adenomatous polyposis and Gardner's syndrome. Pancreatic presentation is exceptional and only eight cases have been described in the literature.
  
  
  METHODS
  We report the case of a 29-year-old woman with a history of familial colonic polyposis and two pancreatic lesions. In the surgical specimen, two poorly defined pancreatic lesions were observed with infiltration of neighboring organs. Histologically, the lesions corresponded to mesenchymal proliferation with a fusocellular pattern without cytological atypica, which were diagnosed as desmoid tumors.
  
  
  CONCLUSIONS
  The etiology of fibromatosis is unknown. In patients with familial colonic polyposis, the most common localization of desmoid tumor is intra-abdominal. Pancreatic presentation is unusual, requiring differential diagnosis with other pancreatic neoplasms.
authors.affiliation: Servicio de Patología, Hospital Universitario Joan XXIII, Tarragona, España. analiael@yahoo.com
authors.forename: Analía
authors.initials: A
authors.lastname: Elguezabal Rodriguez
authors.forename: Miriam
authors.initials: M
authors.lastname: Gené Hijós
authors.forename: Aleidis
authors.initials: A
authors.lastname: Caro Tarragó
authors.forename: Salomé
authors.initials: S
authors.lastname: Martínez González
mesh_terms: D000008:Abdominal Neoplasms / Q000150:complications* / Q000175:diagnosis*; D011125:Adenomatous Polyposis Coli / Q000150:complications*; D000328:Adult; D003937:Diagnosis, Differential; D005260:Female; D018222:Desmoid Tumors / Q000150:complications* / Q000175:diagnosis*; D006801:Humans; D010190:Pancreatic Neoplasms / Q000175:diagnosis*