title: Amyand's hernia in a child with permanent neonatal diabetes due to pancreatic agenesis.
abstract: Acute or perforated appendicitis within inguinal hernia is rarely encountered and it is known as Amyand's hernia. We report on the first case occurring in a 4-year-old boy affected by permanent neonatal diabetes mellitus due to pancreatic agenesis, an extremely rare condition. The initial suspicion of inguinal hernia was confirmed by ultrasound examination of the right inguinal region which revealed omental layers inside a swollen inguinal canal; this finding and the clinical presentation allowed a prompt and appropriate surgical management. The careful evaluation of this patient and early recognition of this unique presentation of appendicitis allowed trans-hernial appendectomy and immediate herniorrhaphy. Ultrasonography played a pivotal role to reach the correct diagnosis and to start a prompt treatment.
authors: Department of Pediatrics, University of Genoa, Giannina Gaslini Institute, Genova, Italy;
authors: Alessandro
authors: A
authors: Giannattasio
authors: Riccardo
authors: R
authors: Campus
authors: Monica
authors: M
authors: Muraca
authors: Giorgio
authors: G
authors: Lucigrai
authors: Alberto
authors: A
authors: Michelazzi
authors: Etayeb Mahmud
authors: EM
authors: Eljerbi
authors: Renata
authors: R
authors: Lorini
authors: Giuseppe
authors: G
authors: d'Annunzio
references: Pediatrics. 2008 Jun;121(6):e1541-7
references: 18519458
references: Hernia. 2007 Feb;11(1):31-5
references: 17001453
references: Orphanet J Rare Dis. 2007 Mar 09;2:12
references: 17349054
references: J Pept Sci. 2007 Feb;13(2):113-20
references: 17120268
references: Hernia. 2003 Jun;7(2):89-91
references: 12820031
references: Mol Cell Endocrinol. 2003 Aug 29;206(1-2):159-66
references: 12943998
references: J Clin Ultrasound. 2006 Nov-Dec;34(9):454-7
references: 17024670
references: Reprod Toxicol. 2006 May;21(4):399-409
references: 16580941
references: Am Surg. 2001 Jul;67(7):628-9
references: 11450774
references: Pediatr Int. 2003 Oct;45(5):595-6
references: 14521542
references: J Pediatr. 2002 Oct;141(4):462-3
references: 12378179
references: Nat Genet. 1997 Jan;15(1):106-10
references: 8988180
references: Emerg Radiol. 2005 Jun;11(4):231-2
references: 16133611
references: Hernia. 2006 Apr;10(2):152-5
references: 16172801
references: N Engl J Med. 1988 May 26;318(21):1402
references: 3285210