title: Atypical hemolytic-uremic syndrome (HUS) with recovery after a long-lasting anuria: a case report.
abstract: We report a case of a seven-year-old girl who suffered from atypical Hemolytic Uremic Syndrome (aHUS) complicated by septicaemia, central nervous system involvement, and cholangiitis. She remained anuric requiring treatment with peritoneal dialysis (PD) for a five-month period. In addition to conventional therapeutic measures including fresh frozen plasma (FFP) and blood cells transfusions she also underwent to plasma exchange (PE) treatment. Following a stormy hospitalization period of 17 weeks, the patient finally regained renal function and three years later she remains well on antihypertensive treatment and free of dialysis.
authors: H
authors: H
authors: Georgaki-Angelaki
authors: N
authors: N
authors: Stergiou
authors: A
authors: A
authors: Kapogiannis
authors: I
authors: I
authors: Orfanou
authors: B
authors: B
authors: Grapsa
authors: E
authors: E
authors: Roma
references: Springer Semin Immunopathol. 2005 Nov;27(3):359-74
references: 16189652
references: J Pediatr. 1991 Feb;118(2):195-200
references: 1993944
references: Kidney Blood Press Res. 1996;19(3-4):205-8
references: 8887262
references: J Pediatr. 1993 Apr;122(4):532-7
references: 8463896
references: Am J Kidney Dis. 1993 Aug;22(2):264-6
references: 8352251
references: Arch Dis Child. 1983 Feb;58(2):101-5
references: 6830286
references: Pediatr Nephrol. 2007 Sep;22(9):1343-7
references: 17564728
references: Adv Nephrol Necker Hosp. 1993;22:141-68
references: 8427056
references: J Med Genet. 2003 Sep;40(9):676-81
references: 12960213
references: J Am Soc Nephrol. 2005 Apr;16(4):1035-50
references: 15728781
references: J Nephrol. 1998 Nov-Dec;11(6):300-10
references: 10048496
references: Pediatr Nephrol. 2008 Aug;23(8):1303-8
references: 18465151
references: Pediatr Nephrol. 2004 Feb;19(2):229-31
references: 14648326
references: Nephron. 1994;68(1):63-70
references: 7991042
references: Curr Opin Pediatr. 2005 Apr;17(2):200-4
references: 15800412
references: Kidney Int. 2001 Sep;60(3):831-46
references: 11532079