title: Obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome with a single uterus.
abstract: OBJECTIVE
  To describe an unusual case of obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome with a single uterus.
  
  
  METHODS
  Case report.
  
  
  METHODS
  Major academic medical center.
  
  
  METHODS
  A 12-year-old girl with OHVIRA syndrome.
  
  
  METHODS
  None.
  
  
  METHODS
  None.
  
  
  RESULTS
  A 12-year-old girl presented with presumed OHVIRA syndrome and had surgical correction of the obstructed hemivagina. Two years later she presented with increasing pelvic pain and underwent laparoscopy for presumed endometriosis. A single uterus with a broad flat fundus was found as well as endometriosis.
  
  
  CONCLUSIONS
  OHVIRA syndrome is typically associated with a didelphys uterus with two cervices and two vaginas, one of which is obstructed. The obstruction usually occurs on the same side as the renal anomaly. We report a rare congenital anomaly of the female reproductive tract: OHVIRA syndrome with a single uterus. From a fertility standpoint, cases of a single uterus with two cervices are managed differently than two uteri with two cervices. Healthcare providers managing complex reproductive tract anomalies should be aware of this potential variant.
authors: Division of Reproductive Endocrinology and Infertility, Department of Obstetrics and Gynecology, Brigham and Women's Hospital, Boston, Massachusetts, USA.
authors: Divya K
authors: DK
authors: Shah
authors: Marc R
authors: MR
authors: Laufer