title: Pulmonary hypertension: a fatal complication of neurofibromatosis type 1.
abstract: We report a very rare case of severe pulmonary arterial hypertension in a patient with neurofibromatosis type 1, and discuss the pathology, pathogenesis, current pulmonary hypertension classification system, and outcomes of pulmonary arterial hypertension in patients with neurofibromatosis  type 1.
authors: Department of Cardiovascular Medicine, Vilnius University Hospital Santariskiu Klinikos, Vilnius University, Vilnius, Lithuania. lina.gumbiene@santa.lt
authors: Lina
authors: L
authors: Gumbiene
authors: Zaneta
authors: Z
authors: Petrulioniene
authors: Kestutis
authors: K
authors: Rucinskas
authors: Vyte
authors: V
authors: Maneikiene
authors: Pranas
authors: P
authors: Serpytis
authors: Alicija
authors: A
authors: Dranenkiene
authors: Aleksandras
authors: A
authors: Laucevicius