title: Placement of an implantable cardioverter-defibrillator in an infant with congenital long QT syndrome: anesthetic considerations.
abstract: Sudden cardiac arrest (SCA) in children is a rare, but catastrophic event. Children with cardiac pathology at particular risk include those with congenital long QT syndrome (CLQTS) and hypertrophic cardiomyopathy. CLQTS is a genetic disorder of the cardiac ion channels and is associated with significant risk of malignant ventricular arrhythmias and SCA. For symptomatic, untreated patients, the mortality rate is approximately 20% for the first year and 50% at ten years. Use of an implantable cardioverter-defibrillator (ICD) is recommended for the prevention of SCA in this patient population. We report a case of CLQTS, who after successful resuscitation from SCA, underwent ICD placement at our center.
authors.affiliation: Department of Anesthesiology and Critical Care, Escorts Heart Institute and Research Center Ltd., New Delhi, India. drbhuvnesh@gmail.com
authors.forename: Bhuvnesh
authors.initials: B
authors.lastname: Kansara
authors.forename: Ajmer
authors.initials: A
authors.lastname: Singh
authors.forename: Sunil
authors.initials: S
authors.lastname: Kaushal
authors.forename: Anil
authors.initials: A
authors.lastname: Saxena
mesh_terms: D000758:Anesthesia; D000769:Anesthesia, Inhalation; D018685:Anesthetics, Inhalation; D018686:Anesthetics, Intravenous; D001794:Blood Pressure / Q000502:physiology; D001831:Body Temperature; D017147:Defibrillators, Implantable; D004562:Electrocardiography; D005283:Fentanyl; D006801:Humans; D006993:Hypnotics and Sedatives; D007223:Infant; D008133:Long QT Syndrome / Q000503:physiopathology / Q000601:surgery*; D008297:Male; D008738:Methyl Ethers; D008874:Midazolam; D009609:Nitrous Oxide; D019919:Prosthesis Implantation / Q000379:methods*; D012151:Resuscitation; D000077149:Sevoflurane
chemical_list: D018685:Anesthetics, Inhalation; D018686:Anesthetics, Intravenous; D006993:Hypnotics and Sedatives; D008738:Methyl Ethers; D000077149:Sevoflurane; D009609:Nitrous Oxide; D008874:Midazolam; D005283:Fentanyl