title: Noncompaction of the ventricular myocardium: characterization and follow-up of an affected population.
abstract: Noncompaction of the ventricular myocardium (NVM) is a rare congenital disease caused by an arrest in normal myocardial embryogenesis, leading to persistence of numerous prominent trabeculations which communicate with the left ventricle. It was first described as a congenital condition affecting children, but several cases have been reported of late presentation, and recent studies suggest it may be underdiagnosed. The main clinical manifestations are congestive heart failure, arrhythmias (supraventricular or ventricular) and systemic embolism. We describe a series of twenty patients, focusing on clinical history, echocardiography and follow-up.
authors.affiliation: Serviço de Cardiologia, Hospital de S.Teotónio EPE, Viseu, Portugal. emanuelbaptista@gmail.com
authors.forename: Emanuel
authors.initials: E
authors.lastname: Correia
authors.forename: Bruno
authors.initials: B
authors.lastname: Rodrigues
authors.forename: Luís
authors.initials: L
authors.lastname: Santos
authors.forename: Rita
authors.initials: R
authors.lastname: Faria
authors.forename: Pedro
authors.initials: P
authors.lastname: Ferreira
authors.forename: Pedro
authors.initials: P
authors.lastname: Gama
authors.forename: Celeste
authors.initials: C
authors.lastname: Nascimento
authors.forename: Odete
authors.initials: O
authors.lastname: Dionisio
authors.forename: Costa
authors.initials: C
authors.lastname: Cabral
authors.forename: Oliveira
authors.initials: O
authors.lastname: Santos
mesh_terms: D000293:Adolescent; D000328:Adult; D000368:Aged; D000369:Aged, 80 and over; D002648:Child; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D056830:Isolated Noncompaction of the Ventricular Myocardium / Q000175:diagnosis*; D008297:Male; D008875:Middle Aged; D055815:Young Adult