title: [Cardiac malformations in patients with pentalogy of Cantrell and ectopia cordis].
abstract: We studied 21 patients who presented with a diagnosis of pentalogy of Cantrell. Their mean age was 40 days. All patients presented with congenital heart disease. Six presented with ectopia cordis. Every patient was subjected to echocardiography. Double outlet right ventricle, an atrial septal defect and dextrocardia were seen in 5 patients (24%). Four patients survived. Seventeen died, 12 from sepsis or septic shock. Autopsies were performed on 10 patients. All of the ectopia cordis patients died. Pentalogy of Cantrell is uncommon, and its association with ectopia cordis indicates poor prognosis. Full English text available from: www.revespcardiol.org.
authors.affiliation: Departamento de Cardiología, Instituto Nacional de Pediatría, México DF, México. derubens@hotmail.com
authors.forename: Jesús
authors.initials: J
authors.lastname: de Rubens Figueroa
authors.forename: Erika Flor
authors.initials: EF
authors.lastname: Sosa Cruz
authors.forename: Luisa
authors.initials: L
authors.lastname: Díaz García
authors.forename: Daniel
authors.initials: D
authors.lastname: Carrasco Daza
mesh_terms: D004452:Echocardiography; D015150:Echocardiography, Doppler; D054083:Ectopia Cordis / Q000150:complications* / Q000000981:diagnostic imaging / Q000473:pathology; D005260:Female; D006330:Heart Defects, Congenital / Q000150:complications* / Q000000981:diagnostic imaging / Q000473:pathology; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D008137:Longitudinal Studies; D008297:Male; D058502:Pentalogy of Cantrell / Q000150:complications* / Q000000981:diagnostic imaging / Q000473:pathology; D012189:Retrospective Studies; D054079:Vascular Malformations / Q000150:complications* / Q000000981:diagnostic imaging / Q000473:pathology