title: Right atrial myxoma associated with portal and splenic vein thrombosis in a patient with Budd-Chiari syndrome.
abstract: Budd-Chiari syndrome (BCS) is a rare disorder characterized by hepatic venous obstruction. A 41-year-old male patient presented with right upper quadrant pain, abdominal distension, and dyspnea. He had a history of BCS that was associated with polycythemia vera. Abdominal computed tomography showed hepatomegaly and a hypodense filling defect suggestive of thrombus formation in the hepatic, splenic, and portal veins, and suprahepatic part of the inferior vena cava. Transthoracic echocardiography performed to assess the extension of this pathological process and its relation with intracardiac structures showed a mass lesion in the right atrium, about 4 x 3 cm in diameter. The lesion manifested as an intracardiac thrombus extending from the inferior vena cava. The patient underwent surgical treatment to remove the atrial mass. At surgery, the lesion turned out to be an atrial tumor, which was diagnosed as atrial myxoma in histopathologic examination. The symptoms of the patient resolved after surgery.
authors.affiliation: Department of Cardiovascular Surgery, Florence Nightingale Hospital, İstanbul, Turkey. burakonan@hotmail.com
authors.forename: Burak
authors.initials: B
authors.lastname: Onan
authors.forename: Zehra
authors.initials: Z
authors.lastname: Bayramoğlu
authors.forename: Ismihan Selen
authors.initials: IS
authors.lastname: Onan
authors.forename: Belhhan
authors.initials: B
authors.lastname: Akpınar
mesh_terms: D000328:Adult; D006502:Budd-Chiari Syndrome; D003937:Diagnosis, Differential; D006325:Heart Atria; D006338:Heart Neoplasms / Q000150:complications / Q000175:diagnosis* / Q000000981:diagnostic imaging / Q000601:surgery; D006801:Humans; D008297:Male; D009232:Myxoma / Q000150:complications / Q000175:diagnosis* / Q000000981:diagnostic imaging / Q000601:surgery; D011169:Portal Vein; D013162:Splenic Vein; D014463:Ultrasonography; D020246:Venous Thrombosis / Q000150:complications / Q000175:diagnosis* / Q000000981:diagnostic imaging / Q000601:surgery