title: Cardiac arrest after anesthetic management in a patient with hereditary sensory autonomic neuropathy type IV.
abstract: Hereditary sensory autonomic neuropathy type IV is a rare disorder with an autosomal recessive transmission and characterized by self-mutilation due to a lack in pain and heat sensation. Recurrent hyperpyrexia and anhydrosis are seen in patients as a result of a lack of sweat gland innervation. Self-mutilation and insensitivity to pain result in orthopedic complications and patients undergone recurrent surgical interventions with anesthesia. However, these patients are prone to perioperative complications such as hyperthermia, hypothermia, and cardiac complications like bradycardia and hypotension. We report a 5-year-old boy with hereditary sensory autonomic neuropathy type IV, developing hyperpyrexia and cardiac arrest after anesthesia.
authors.affiliation: Division of Pediatric Neurology of Cerrahpaşa Medical Faculty, Istanbul University, Istanbul, Turkey.
authors.forename: Yakup
authors.initials: Y
authors.lastname: Ergül
authors.forename: Bariş
authors.initials: B
authors.lastname: Ekici
authors.forename: Sabiha
authors.initials: S
authors.lastname: Keskin