title: Erdheim-Chester disease: a case study and literature review.
abstract: Diagnosis and treatment of patients who present with respiratory compromise are challenging. What happens when these patients do not respond to your intervention, and their condition declines rapidly? Having a variety of differential diagnoses is key. An addition to your differential list can include a rare disorder of non-Langerhans cells histiocytosis also known as Erdheim-Chester disease. This disease often presents as an interstitial lung disease that fails many different treatment modalities. A full understanding of how this disease process works is still being investigated. Provided are a literature review and case study for better understanding of this disease.
authors.affiliation: Cleveland Clinic Critical Care Transport, Cleveland Clinic Foundation, USA. Kaa66@case.edu
authors.forename: Kevin
authors.initials: K
authors.lastname: Andrysek
mesh_terms: D000328:Adult; D003937:Diagnosis, Differential; D004417:Dyspnea / Q000188:drug therapy / Q000209:etiology; D031249:Erdheim-Chester Disease / Q000175:diagnosis* / Q000188:drug therapy; D005260:Female; D006801:Humans; D013256:Steroids / Q000627:therapeutic use
chemical_list: D013256:Steroids