title: Uterus didelphys, hemihydrocolpos and empty ipsilateral lumbar fossa in a newborn girl: involuted dysplastic kidney rather than renal agenesis.
abstract: We report a case of Herlyn-Werner-Wunderlich syndrome diagnosed in the neonatal period. US revealed the classic association of a uterus didelphys with blind hemivagina and no ipsilateral kidney. The diagnosis was established by postnatal US and confirmed by MRI. Differential diagnoses are discussed. A trans-hymeneal resection of the vaginal septum was performed at 1 month of age. Intra operative endoscopy revealed no left hemitrigone but showed an atretic orifice in the ipsilateral blind hemivagina, probably corresponding to the insertion of an ectopic ureter. Follow-up was unremarkable.
authors.affiliation: Pediatric and Foetal Imaging Service, Department of Radiology, CHU Charles Nicolle, Rouen University Hospital, 1 rue de Germont, 76031, Rouen Cedex, France. pierre-hugues.vivier@chu-rouen.fr
authors.forename: Pierre-Hugues
authors.initials: PH
authors.lastname: Vivier
authors.forename: Agnès
authors.initials: A
authors.lastname: Liard
authors.forename: Marion
authors.initials: M
authors.lastname: Beurdeley
authors.forename: Marie
authors.initials: M
authors.lastname: Brasseur-Daudruy
authors.forename: Cécile
authors.initials: C
authors.lastname: Cellier
authors.forename: Patrick
authors.initials: P
authors.lastname: Le Dosseur
authors.forename: Jean-Nicolas
authors.initials: JN
authors.lastname: Dacher
mesh_terms: D000015:Abnormalities, Multiple / Q000175:diagnosis* / Q000000981:diagnostic imaging; D005260:Female; D006801:Humans; D007231:Infant, Newborn; D007668:Kidney / Q000002:abnormalities*; D008279:Magnetic Resonance Imaging; D014463:Ultrasonography; D014564:Urogenital Abnormalities / Q000175:diagnosis* / Q000000981:diagnostic imaging; D014591:Uterine Diseases / Q000175:diagnosis* / Q000000981:diagnostic imaging; D014599:Uterus / Q000002:abnormalities*; D014621:Vagina / Q000002:abnormalities*