title: Obstructive jaundice due to autoimmune cholangiopathy.
abstract: A 59-year-old man presented with upper abdominal pain, cholestasis and radiological evidence of common hepatic duct hilar stricture which was suggestive of cholangiocarcinoma. The patient initially underwent percutaneous drainage and a laparotomy. No evidence of malignancy was identified. He was noted to have retroperitoneal fibrosis, which was confirmed on histology. The combination of cholangiopathy and retroperitoneal fibrosis suggested an underlying autoimmune process. Although the investigations did not show any evidence of IgG4 related disease, the combination of a cholangiopathy and retroperitoneal fibrosis is in keeping with autoimmune cholangiopathy and a steroid regimen was commenced. Our patient is now symptom-free with no further episodes of cholangitis. He has commenced azathioprine to maintain long term remission.
authors.affiliation: Princess Royal University Hospital, General Surgery Department, Farnborough Common, Orpington BR6 8ND, UK.
authors.forename: Osama
authors.initials: O
authors.lastname: Naji
authors.forename: Abdulzahra
authors.initials: A
authors.lastname: Hussain
authors.forename: Dennis
authors.initials: D
authors.lastname: Baker
authors.forename: Naji
authors.initials: N
authors.lastname: Habib
authors.forename: Shamsi
authors.initials: S
authors.lastname: El-Hasani