title: Primary pulmonary artery rhabdomyosarcoma.
abstract: A 69-year-old woman presented with a 4-month history of dyspnoea and radiating upper-right quadrant pain and oedema in her lower extremities for more than 20 days. The ultrasonographic study of the heart revealed the adherence of a substantive hypoechoic mass (73 x 34 mm) to the antelateral wall of the pulmonary artery and resultant pulmonary stenosis. Computed tomographic imaging of the pulmonary artery revealed an irregularly shaped filling defect (approximately 41 x 39 x 59 mm) in the main pulmonary artery. The boundary of the defect was irregular, but demarcation with healthy tissue was clear. After surgical treatment, the histologic and immunohistochemical assays revealed a primary pulmonary artery rhabdomyosarcoma. Pulmonary artery rhabdomyosarcomas are usually misdiagnosed as other pulmonary artery obstructive diseases. There should be a greater focus of clinical attention and resection is the appropriate surgical treatment for such malignant tumours.
authors: Department of Cardiology, China-Japan Union Hospital of Jilin University, Changchun, China.
authors: Daoyuan
authors: D
authors: Si
authors: Bomin
authors: B
authors: Zhang
authors: Xiuhe
authors: X
authors: Zhang
authors: Mingqiu
authors: M
authors: Zhang
authors: Lujia
authors: L
authors: Ni
authors: Ping
authors: P
authors: Yang
mesh_terms: D000368:Aged; D017809:Fatal Outcome; D005260:Female; D006801:Humans; D011651:Pulmonary Artery / Q000000981:diagnostic imaging; D012208:Rhabdomyosarcoma / Q000175:diagnosis* / Q000000981:diagnostic imaging / Q000473:pathology; D014057:Tomography, X-Ray Computed; D014463:Ultrasonography; D019043:Vascular Neoplasms / Q000175:diagnosis* / Q000000981:diagnostic imaging / Q000473:pathology