title: Idiopathic cardiomyopathies in Korean children. - 9-Year Korean Multicenter Study-.
abstract: BACKGROUND
  Idiopathic cardiomyopathies (CMPs) are an important heterogeneous group of diseases. With the advance of therapeutic strategies, epidemiologic data on CMP have become very important, but only a few have been reported in Asian children. We conducted a retrospective epidemiologic study of primary CMP in Korean children.
  
  
  RESULTS
  Using a multicenter survey, we studied primary CMP among Korean children from January 1998 to December 2006 based on classification (2006) of CMP by the American Heart Association. A total of 277 primary CMP patients were reported from 17 cardiovascular centers. The average annual occurrence of new cases of primary CMP was 0.28 per 100,000 Korean children younger than 15 years of age (95% confidence interval (CI) 0.24-0.31). Dilated CMP (DCMP) was 66.43%, hypertrophic CMP (HCMP) 23.47%, restrictive CMP (RCMP) 6.50% and others 3.61%. The point prevalence of primary CMP at the end of the study was estimated as 2.11/100,000 (95%CI 1.83-2.43), DCMP 1.39/100,000, HCMP 0.51/100,000, RCMP 0.16/100,000 and others 0.04/100,000. Survival rates over 9 years were 69.8% in DCMP, 90.3% in HCMP, and 47.2% in RCMP.
  
  
  CONCLUSIONS
  Recent point prevalence of childhood primary CMP in Korea was estimated as 2.11/100,000. Further epidemiologic study with a nationwide survey is necessary.
authors: Department of Pediatrics, The Catholic University of Korea, Seoul, Korean.
authors: Jin Hee
authors: JH
authors: Oh
authors: Young Mi
authors: YM
authors: Hong
authors: Jae Young
authors: JY
authors: Choi
authors: Soo Jin
authors: SJ
authors: Kim
authors: Jo Won
authors: JW
authors: Jung
authors: Sejung
authors: S
authors: Sohn
authors: Myung Chul
authors: MC
authors: Hyun
authors: Chung Il
authors: CI
authors: Noh
authors: Joo Won
authors: JW
authors: Lee
authors: In Sook
authors: IS
authors: Park
mesh_terms: D000293:Adolescent; D044466:Asian People; D002311:Cardiomyopathy, Dilated / Q000401:mortality* / Q000503:physiopathology; D002648:Child; D002675:Child, Preschool; D003625:Data Collection; D005260:Female; D006801:Humans; D015994:Incidence; D007223:Infant; D007231:Infant, Newborn; D008297:Male; D015995:Prevalence; D056910:Republic of Korea / Q000453:epidemiology; D012189:Retrospective Studies; D015996:Survival Rate