title: Do you know this syndrome?
abstract: Bloch-Sulzberger syndrome (incontinentia pigmenti) is a rare genodermatosis that affects predominantly females, since it is generally lethal to male fetuses in utero. It is characterized principally by skin lesions, but may also involve dental, ophthalmological and neurological abnormalities. The skin lesions are present in four different phases: vesicular, verrucous, hyperpigmented and atrophic/hypopigmented. Their sequence is irregular and overlapping of stages is common.
authors: Hospital Municipal Jesus (HMJ), Rio de Janeiro, Brazil. ibsucci@unisys.com.br
authors: Isabella Brasil
authors: IB
authors: Succi
authors: Fernando Colonna
authors: FC
authors: Rosman
authors: Elisa Fontenelle de
authors: EF
authors: Oliveira
mesh_terms: D005260:Female; D006801:Humans; D007184:Incontinentia Pigmenti / Q000473:pathology*; D007223:Infant