title: Congenital hepatic arteriovenous malformation presenting with severe persistent pulmonary hypertension.
abstract: Congenital hepatic arteriovenous malformation is a rarely seen vascular malformation with persistent pulmonary hypertension in neonates. The authors report a full-term female newborn presenting with intractable heart failure and respiratory distress soon after birth. Investigation by echocardiography showed severe persistent pulmonary hypertension of the newborn and patent ductus arteriosus. The hepatic angiogram revealed congenital hepatic arteriovenous malformation; therefore, secondary pulmonary artery hypertension complicated with 'steal' phenomenon was conclusively diagnosed.
authors: Division of Neonatology, Department of Pediatrics, Faculty of Medicine, Prince of Songkla University, Hat Yai, Songkhla 90110, Thailand. tanucha@medicine.psu.ac.th
authors: Anucha
authors: A
authors: Thatrimontrichai
authors: Prasin
authors: P
authors: Chanvitan
authors: Waricha
authors: W
authors: Janjindamai
authors: Supaporn
authors: S
authors: Dissaneevate
authors: Supika
authors: S
authors: Kritsaneepaiboon
authors: Keerati
authors: K
authors: Hongsakul
mesh_terms: D001165:Arteriovenous Malformations / Q000150:complications / Q000000981:diagnostic imaging*; D004374:Ductus Arteriosus, Patent / Q000150:complications / Q000000981:diagnostic imaging; D017809:Fatal Outcome; D005260:Female; D006499:Hepatic Artery / Q000002:abnormalities* / Q000000981:diagnostic imaging; D006503:Hepatic Veins / Q000002:abnormalities* / Q000000981:diagnostic imaging; D006801:Humans; D006976:Hypertension, Pulmonary / Q000000981:diagnostic imaging / Q000209:etiology*; D007231:Infant, Newborn; D011859:Radiography; D014463:Ultrasonography