title: Mucous membrane pemphigoid with severe esophageal stricture.
abstract: Mucous membrane pemphigoid (MMP) is a rare nosological entity. MMP consists of a clinical phenotype in which several autoimmune subepidermal bullous diseases are classified. It occurs predominantly in the mucous membranes and usually results in scarring. Esophageal involvement in MMP is rare and is generally seen in patients in whom lesions are widespread. The most common alterations are multiple esophageal membranes or strictures. In the present case, the authors report on a patient with MMP without any skin lesions and with severe esophageal strictures who went into remission following use of intravenous immunoglobulin.
authors: Pedro Ernesto Teaching Hospital, State University of Rio de Janeiro (UERJ), Rio de Janeiro, RJ, Brazil. barbosalivia@terra.com.br
authors: Lívia do Nascimento
authors: Ldo N
authors: Barbosa
authors: Roberto Souto da
authors: RS
authors: Silva
authors: Gustavo Costa
authors: GC
authors: Verardino
authors: Alexandre Carlos
authors: AC
authors: Gripp
authors: Maria de Fátima Guimarães Scotelaro
authors: Mde F
authors: Alves
mesh_terms: D000368:Aged; D004940:Esophageal Stenosis / Q000175:diagnosis / Q000188:drug therapy / Q000209:etiology*; D005260:Female; D005938:Glucocorticoids / Q000627:therapeutic use; D006801:Humans; D016756:Immunoglobulins, Intravenous / Q000627:therapeutic use; D010390:Pemphigoid, Benign Mucous Membrane / Q000150:complications* / Q000175:diagnosis / Q000188:drug therapy; D011241:Prednisone / Q000627:therapeutic use; D012720:Severity of Illness Index
chemical_list: D005938:Glucocorticoids; D016756:Immunoglobulins, Intravenous; D011241:Prednisone