title: [Epithelioid hemangioendothelioma of the inferior vena cava].
abstract: Epithelioid hemangioendothelioma is a rare endothelial cell-derived tumor of intermediate grade malignancy. It has an unpredictable outcome, independently of the usual histoprognostic criteria. Thirty-three cases with intravascular localisation are described in the literature. We describe a case occurring in a 31-year-old male, which developed an inferior veina cava tumor, with recurrence after incomplete surgical resection and chemotherapy. He was operated on again under extracorporeal circulation and complete surgical resection was then performed. Histologic examination found an intravascular epithelioid hemangioendothelioma developing in the vascular lumen without vascular wall infiltration. This entity represents a challenge not only for the vascular surgeon, but also for the pathologist given its difficult diagnosis.
authors: Service d'anatomie et cytologie pathologiques, hôpital européen Georges-Pompidou, 20, rue Leblanc, 75908 Paris cedex 15, France.
authors: Clarissa Rodriguez
authors: CR
authors: Henriquez
authors: Aurélie
authors: A
authors: Cazes
authors: Jean-Noël
authors: JN
authors: Fabiani
authors: Patrick
authors: P
authors: Bruneval
mesh_terms: D000328:Adult; D018906:Antineoplastic Agents, Alkylating / Q000627:therapeutic use; D003131:Combined Modality Therapy; D003937:Diagnosis, Differential; D004317:Doxorubicin / Q000627:therapeutic use; D018323:Hemangioendothelioma, Epithelioid / Q000175:diagnosis / Q000188:drug therapy / Q000473:pathology* / Q000601:surgery; D006394:Hemangiosarcoma / Q000175:diagnosis / Q000188:drug therapy / Q000601:surgery; D006801:Humans; D008297:Male; D009364:Neoplasm Recurrence, Local; D019043:Vascular Neoplasms / Q000175:diagnosis / Q000188:drug therapy / Q000473:pathology* / Q000601:surgery; D014682:Vena Cava, Inferior / Q000473:pathology* / Q000601:surgery
chemical_list: D018906:Antineoplastic Agents, Alkylating; D004317:Doxorubicin