title: Congenital extrahepatic portosystemic shunt (Abernethy malformation) treated endovascularly with vascular plug shunt closure.
abstract: A 3-year-old boy, who presented with progressive cyanosis and hypoxia, was diagnosed with a large congenital extrahepatic portosystemic shunt, interrupted IVC with azygos continuation, and multiple congenital anomalies. Traditionally open and laparoscopic surgical techniques have been used to treat this malformation. Endovascular repair using a 16-mm Amplatzer vascular plug (AGA Medical Corporation, Golden Valley, Minnesota, USA) was used to occlude the shunt. Immediate post-placement venography demonstrated cessation of flow within the shunt and increased portal venous flow. The patient's hypoxia and cyanosis decreased significantly, and he was discharged on the 5th post-procedure day in stable clinical condition. Three months follow-up evaluation demonstrated the vascular plug in place, unchanged in position.
authors: Division of Vascular and Interventional Radiology, Department of Diagnostic Radiology, University Hospitals Case Medical Center, 11100 Euclid Avenue, Cleveland, OH 44106-5056, USA.
authors: Matthew
authors: M
authors: Passalacqua
authors: Kevin T
authors: KT
authors: Lie
authors: Hooman
authors: H
authors: Yarmohammadi
mesh_terms: D002675:Child, Preschool; D057510:Endovascular Procedures / Q000379:methods*; D005500:Follow-Up Studies; D006801:Humans; D008297:Male; D010690:Phlebography; D011167:Portacaval Shunt, Surgical / Q000379:methods*; D011169:Portal Vein / Q000002:abnormalities* / Q000000981:diagnostic imaging; D014057:Tomography, X-Ray Computed; D054079:Vascular Malformations / Q000000981:diagnostic imaging / Q000601:surgery*; D014682:Vena Cava, Inferior / Q000002:abnormalities* / Q000000981:diagnostic imaging