title: Complete recovery following sudden sensorineural hearing loss in a patient with sickle cell disease.
abstract: A sickle cell disease (SCD) patient with vaso-occlusive crisis (VOC) developed sudden senserinural hearing loss (SNHL), which responded well to a rapid course of corticosteroids along with exchange transfusions. The otolaryngologist should be aware of the otologic manifestations of SCD such as SNHL. A good response to steroids, which averted a permanent hearing loss, warrants further studies to define the augmentive benefits of such therapy along with exchange transfusions in patients with SCD in VOC who develop sudden SNHL.
authors: Department of Haematology, College of Medicine and Health Sciences, Sultan Qaboos University Hospital, Muscat, Oman. sskindi@yahoo.com
authors: Salam
authors: S
authors: Alkindi
authors: Najwa
authors: N
authors: Arafa
authors: M
authors: M
authors: Al Okbi
authors: Anil
authors: A
authors: Pathare
mesh_terms: D000284:Administration, Oral; D000328:Adult; D000755:Anemia, Sickle Cell / Q000150:complications* / Q000175:diagnosis / Q000188:drug therapy / Q000628:therapy*; D005078:Exchange Transfusion, Whole Blood; D005260:Female; D005938:Glucocorticoids / Q000627:therapeutic use; D006319:Hearing Loss, Sensorineural / Q000188:drug therapy / Q000209:etiology* / Q000628:therapy*; D003639:Hearing Loss, Sudden / Q000188:drug therapy / Q000209:etiology*; D006801:Humans; D011239:Prednisolone / Q000627:therapeutic use; D016896:Treatment Outcome
chemical_list: D005938:Glucocorticoids; D011239:Prednisolone