title: Management of supraglottic dysgenesis presenting as laryngomalacia.
abstract: Laryngomalacia is a common source of stridor and can lead to significant upper airway obstruction and feeding disturbances in infants. We describe a unique case of supraglottic dysgenesis presenting as laryngomalacia featuring a prominent "s-shaped" epiglottis with both posterior edges fused to the right aryepiglottic fold/arytenoid complex. Although this anomaly is not accounted for in any of the current laryngomalacia classification schemes, modified laser supraglottoplasty was a satisfactory approach leading to successful decannulation. Laryngeal embryology and possible timing of the pathogenesis of this rare occurrence are reviewed as well.
authors: State University of New York Downstate Medical Center, Brooklyn, NY, United States. baynehchi@gmail.com
authors: Behrad B
authors: BB
authors: Aynehchi
authors: Nira A
authors: NA
authors: Goldstein
authors: Ari J
authors: AJ
authors: Goldsmith
mesh_terms: D000402:Airway Obstruction / Q000175:diagnosis / Q000209:etiology / Q000601:surgery; D003937:Diagnosis, Differential; D004825:Epiglottis / Q000002:abnormalities*; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D007223:Infant; D055092:Laryngomalacia / Q000175:diagnosis / Q000601:surgery*; D007828:Laryngoscopy / Q000379:methods; D053685:Laser Therapy / Q000379:methods*; D015619:Respiratory System Abnormalities / Q000175:diagnosis* / Q000601:surgery; D018570:Risk Assessment; D014139:Tracheostomy / Q000379:methods; D016896:Treatment Outcome