title: Macrodactyly with skin hypertrophy: a minimal form of the Proteus syndrome.
abstract: The Proteus syndrome was described 1983 . It has asymmetric gigantism of the limbs, verrucous epidermal naevi, cerebriform enlargement of the plantar region, vascular malformations and neoplasms, as lipomas. It received this denomination after Proteus from the Greek mythology, who had the ability to change his form . A 15 year-old boy, reported a congenital hypertrophy with syndactily of the second and third right fingers . The second case is a 35 year-old man, who reported that since birth the second right toe was bigger than the other toes, skin hypertrophy was also observed. These cases document a localized form if the Proteus syndrome, which may widen the spectrum of its variability.
authors: Federal University of Pelotas (UFPel), at the Catholic University of Pelotas (UCPEL), Brazil. hiramalmeidajr@hotmail.com
authors: Hiram Larangeira de
authors: HL
authors: Almeida
authors: Roberto Coswig
authors: RC
authors: Fiss
authors: Rudolf
authors: R
authors: Happle
mesh_terms: D000293:Adolescent; D000328:Adult; D005385:Fingers / Q000473:pathology; D006801:Humans; D008297:Male; D016715:Proteus Syndrome / Q000473:pathology*; D014034:Toes / Q000473:pathology