title: Pulmonary Artery Leiomyosarcoma Diagnosed without Delay.
abstract: A 63-year-old female presented with abnormal lung shadows but had, apart from this, few symptoms. Computed tomography (CT) revealed multiple nodules and blockage of the pulmonary artery. She was immediately diagnosed with pulmonary artery sarcoma based on a careful differential diagnosis and underwent surgery. Her tumor was pathologically diagnosed as leiomyosarcoma (i.e. intimal sarcoma). Pulmonary artery sarcoma can be easily confounded with thromboembolism in a clinical setting and some cases are diagnosed post mortem only. In our case, clinical prediction scores (Wells score, Geneva score, and revised Geneva score) for the pulmonary embolism showed low probability. Moreover, chest CT showed uncommon findings for pulmonary thromboembolism, as the nodules were too big for thrombi. Because surgical resection can provide the only hope of long-term survival in cases of pulmonary artery sarcoma, clinicians should consider this possibility in the differential diagnosis of pulmonary embolism. Clinical prediction scores and CT findings might help to reach the correct diagnosis of pulmonary artery sarcoma.
authors: Department of Integrated Pulmonology, Graduate School of Medical and Dental Science, Tokyo Medical and Dental University, Tokyo, Japan.
authors: Motohisa
authors: M
authors: Yamasaki
authors: Yuki
authors: Y
authors: Sumi
authors: Yumi
authors: Y
authors: Sakakibara
authors: Meiyo
authors: M
authors: Tamaoka
authors: Yasunari
authors: Y
authors: Miyazaki
authors: Hirokumi
authors: H
authors: Arai
authors: Katsuo
authors: K
authors: Kojima
authors: Fusahiko
authors: F
authors: Itoh
authors: Tomonari
authors: T
authors: Amano
authors: Yasuyuki
authors: Y
authors: Yoshizawa
authors: Naohiko
authors: N
authors: Inase