title: Renal primitive neuroectodermal tumour in childhood: Case report and review of literature.
abstract: Primitive neuroectodermal tumour (PNET) is presumed to be of neural crest origin, mostly presenting as bone or soft tissue masses. It usually occurs in the trunk or axial skeleton; while renal PNET is considered an extremely rare tumour. We report a case of 11-year-old male who presented with right flank pain and gross hematuria after suffering blunt trauma. During investigations, he was found to have a large renal mass on computed tomography. He underwent a right radical nephrectomy where the pathology report showed PNET of the kidney. The patient received chemotherapy afterwards. Despite the chemotherapy, he had a local tumour recurrence 3 months after and continued to deteriorate and developed distant metastasis. Primitive neuroectodermal tumour of the kidney is a distinct and rare entity. It is very aggressive, with a poor survival despite combined modality treatment.
authors.affiliation: Department of Urology, King Abdul Aziz University Hospital, Jeddah, Kingdom of Saudi Arabia.
authors.forename: Maeed
authors.initials: M
authors.lastname: Asiri
authors.forename: Ahmed
authors.initials: A
authors.lastname: Al-Sayyad