title: Hemangiopericytoma of maxilla in a pediatric patient: a case report.
abstract: The Hemangiopericytoma is a malignant vascular tumor arising from mesenchymal cells with pericytic differentiation. Hemangiopericytoma is most commonly seen in adults, and only 5% to 10% of cases occur in children. The tumor is extremely rare in the head and neck region (16%)1. Cytogenic abnormalities have been present in some hemangiopericytoma cases. Surgical resection remains the mainstay treatment. Adjuvant chemotherapy and radiotherapy is appropriate for cases of incomplete resections and life-threatening tumors particularly in children. Late relapses may occur and require long-term follow-up. A 4-year-old child patient with hemangiopericytoma of the maxilla presented with firm, recurrent, but painless jaw mass. Radiographic investigations revealed a poorly circumscribed radiolucency. The lesion biopsy showed well-circumscribed multiple lobules of tumor mass consisting of tightly packed, spindle-shaped cells. Chemotherapy and radiotherapy of the lesion was conducted. The role of the pediatric dental team is extensive in children with hemangiopericytoma, who require a regular dental review. The patient's oncologist should be immediately contacted if there is any suspicion of recurrence.
authors.affiliation: Department of Pedodontics, Sardar Patel Post Graduate Institute of Dental Sciences, Lucknow (UP), India. rohitanand555@yahoo.com
authors.forename: Rohit
authors.initials: R
authors.lastname: Anand
authors.forename: Sonal
authors.initials: S
authors.lastname: Gupta
mesh_terms: D001706:Biopsy; D017024:Chemotherapy, Adjuvant; D002675:Child, Preschool; D003937:Diagnosis, Differential; D006393:Hemangiopericytoma / Q000175:diagnosis*; D006801:Humans; D008297:Male; D008441:Maxillary Neoplasms / Q000175:diagnosis*; D020360:Neoadjuvant Therapy; D018714:Radiotherapy, Adjuvant; D014057:Tomography, X-Ray Computed; D014746:Vimentin / Q000032:analysis
chemical_list: D014746:Vimentin