title: Proximal-type epithelioid sarcoma of the mons pubis: report of a case.
abstract: BACKGROUND
  Proximal-type epithelioid sarcoma (PES) represents an extremely rare and aggressive form of soft tissue neoplasm, typically presenting as a painless subcutaneous nodule in the trunk often located in the genital area.
  
  
  METHODS
  A 46-year-old female was subjected to the excision of a growing soft tissue mass in the mons pubis that, at histology, was identified as PES. The tumor showed an extreme aggressiveness involving subsequently adjoining structures and lymph nodes despite subsequent wide surgical resections during the following months.
  
  
  CONCLUSIONS
  Gynecologists should pay careful attention to all soft tissue masses of the perineal area or external genitalia. It is important to know the possible genital localization of PES which, although rare, is an aggressive high-grade soft tissue tumor with a deceitful behavior, poorly sensitive to chemotherapy and radiotherapy. Surgery, though wide and demolitive, often fails to obtain the necessary radicality.
authors.affiliation: Department of Gynecological Science and Reproductive Medicine, University of Padova, Padova, Italy. alessandra.andrisani@unipd.it
authors.forename: A
authors.initials: A
authors.lastname: Andrisani
authors.forename: A
authors.initials: A
authors.lastname: Serena
authors.forename: G
authors.initials: G
authors.lastname: Ambrosini
authors.forename: G
authors.initials: G
authors.lastname: Capobianco
authors.forename: S
authors.initials: S
authors.lastname: Chiarelli
mesh_terms: D005260:Female; D006801:Humans; D008875:Middle Aged; D009364:Neoplasm Recurrence, Local / Q000473:pathology* / Q000601:surgery; D010502:Perineum / Q000473:pathology; D012509:Sarcoma / Q000473:pathology* / Q000601:surgery; D012983:Soft Tissue Neoplasms / Q000473:pathology* / Q000601:surgery; D016896:Treatment Outcome; D014844:Vulva / Q000473:pathology