title: Surgical treatment for congenital absence of the oval window with facial nerve anomalies.
abstract: Three patients with a middle ear malformation characterized by the absence of the oval window and complicated by facial nerve anomalies were treated by surgery. Hearing ability of all the patients was improved. A variety of facial nerve anomalies were observed. Fenestration of the vestibule above the facial nerve was performed in the case of 2 of the 3 patients. In the other patient, fenestration of the scala vestibuli below the facial nerve was performed. In the case of all the 3 patients, hearing ability improved after the surgery and remained stable for a long time. Surgery for this disease has been considered difficult because of a high risk of complications. Because all the 3 patients showed excellent long-term surgical results, we suggest that fenestration of the inner ear should be considered one of the main options for the management and treatment of an absent oval window associated with facial nerve anomalies.
authors.affiliation: Department of Otorhinolaryngology-Head and Neck Surgery, Tohoku University Graduate School of Medicine, Sendai, Japan. junha@orl.med.tohoku.ac.jp
authors.forename: Jun
authors.initials: J
authors.lastname: Hasegawa
authors.forename: Tetsuaki
authors.initials: T
authors.lastname: Kawase
authors.forename: Hiroshi
authors.initials: H
authors.lastname: Hidaka
authors.forename: Takeshi
authors.initials: T
authors.lastname: Oshima
authors.forename: Toshimitsu
authors.initials: T
authors.lastname: Kobayashi
mesh_terms: D001301:Audiometry, Pure-Tone; D001309:Auditory Threshold; D002648:Child; D002675:Child, Preschool; D003937:Diagnosis, Differential; D004429:Ear Ossicles / Q000002:abnormalities; D005154:Facial Nerve / Q000002:abnormalities*; D005260:Female; D005276:Fenestration, Labyrinth; D006801:Humans; D008297:Male; D008875:Middle Aged; D019933:Ossicular Replacement / Q000379:methods; D010046:Oval Window, Ear / Q000002:abnormalities* / Q000601:surgery*; D011183:Postoperative Complications / Q000209:etiology; D014433:Tympanoplasty / Q000379:methods