title: A rare angiosarcoma: retiform haemangioendothelioma.
abstract: OBJECTIVE
  We report the case of a rare angiosarcoma, retiform haemangioendothelioma, in an 18-year-old young man, which presented as a recurrent ulcerating lesion of the left pinna.
  
  
  METHODS
  Case report and literature review of retiform haemangioendothelioma. This is a low grade angiosarcoma with a high local recurrence rate and low metastasis rate, and was first described in 1994 by Calonje et al.
  
  
  RESULTS
  This patient represents only the third report of lymph node metastasis in a case of retiform haemangioendothelioma. To date, 31 cases of the tumour have been reported. Histological diagnosis of this group of vascular neoplasms can be challenging, as their histopathological appearance is intermediate between haemangioma and angiosarcoma.
  
  
  CONCLUSIONS
  Surgical excision remains the primary treatment modality, with adjuvant radiotherapy recommended in patients with large tumour size, local recurrence and lymph node metastasis, as seen in this case.
authors: Department of Otorhinolaryngology, Royal Victoria Eye and Ear Hospital, Dublin, Ireland. fergaloduffy@hotmail.com
authors: F
authors: F
authors: O'Duffy
authors: C
authors: C
authors: Timon
authors: M
authors: M
authors: Toner
mesh_terms: D000293:Adolescent; D003937:Diagnosis, Differential; D054644:Ear Auricle / Q000473:pathology*; D004428:Ear Neoplasms / Q000175:diagnosis* / Q000473:pathology / Q000628:therapy; D006390:Hemangioendothelioma / Q000175:diagnosis* / Q000556:secondary / Q000628:therapy; D006394:Hemangiosarcoma / Q000175:diagnosis*; D006801:Humans; D008202:Lymphangioma / Q000175:diagnosis*; D008207:Lymphatic Metastasis; D008297:Male; D009364:Neoplasm Recurrence, Local; D018714:Radiotherapy, Adjuvant; D012008:Recurrence; D016896:Treatment Outcome