title: Successfully treated case of epithelioid sarcoma of the vulva.
abstract: Epithelioid sarcoma of the vulva is an extremely rare and aggressive tumor. This tumor most commonly occurs on the labia majora in women of reproductive age. The molecular pathogenesis remains largely unknown. Only 20 cases of vulvar epithelioid sarcoma have been reported to date and more than half have had poor outcomes. We report a successfully treated case of vulvar epithelioid sarcoma in a 33-year-old woman. We performed a radical vulvectomy with flap reconstruction. Three years after surgery, the patient remains well, showing no evidence of recurrence. Early tissue diagnosis of vulvar epithelioid sarcoma is essential because this tumor can be clinically misdiagnosed as a benign lesion. Gynecologists should be aware of this rare tumor variant and carefully plan the treatment.
authors.affiliation: Department of Obstetrics and Gynecology, Tokyo Dental College Ichikawa General Hospital, Chiba, Japan.
authors.forename: Tatsuyuki
authors.initials: T
authors.lastname: Chiyoda
authors.forename: Mitsuya
authors.initials: M
authors.lastname: Ishikawa
authors.forename: Masaru
authors.initials: M
authors.lastname: Nakamura
authors.forename: Mariko
authors.initials: M
authors.lastname: Ogawa
authors.forename: Kiyoshi
authors.initials: K
authors.lastname: Takamatsu
mesh_terms: D000328:Adult; D005260:Female; D006801:Humans; D012509:Sarcoma / Q000473:pathology / Q000601:surgery*; D016896:Treatment Outcome; D014844:Vulva / Q000473:pathology / Q000601:surgery*; D014846:Vulvar Neoplasms / Q000473:pathology / Q000601:surgery*