title: Immunoglobulin G4-related periaortitis mimicking an intramural hematoma.
abstract: Immunoglobulin G4 (IgG4)-related sclerosing disease in the cardiovascular system is a recently proposed disease entity, which is still unfamiliar to most clinicians. We present a case of IgG4-related periaortitis of the ascending aorta mimicking an intramural hematoma in the computed tomography (CT) scan, which led to an unnecessary surgery. IgG4-related periaortitis needs to be considered in the differential diagnosis in a patient with thickened aortic wall because the disease should be treated medically in light of its good response to steroid therapy.
authors.affiliation: Division of Cardiology and Cardiac and Vascular Center, Sungkyunkwan University School of Medicine, Seoul, Republic of Korea.
authors.forename: Kyeongmin
authors.initials: K
authors.lastname: Byeon
authors.forename: Joungho
authors.initials: J
authors.lastname: Han
authors.forename: Jung-Sun
authors.initials: JS
authors.lastname: Kim
authors.forename: Wook Sung
authors.initials: WS
authors.lastname: Kim
authors.forename: Yeon Hyeon
authors.initials: YH
authors.lastname: Choe
authors.forename: Eun Jeong
authors.initials: EJ
authors.lastname: Lee
authors.forename: Duk-Kyung
authors.initials: DK
authors.lastname: Kim
mesh_terms: D000368:Aged; D000888:Antibodies, Anti-Idiotypic / Q000276:immunology / Q000378:metabolism*; D001013:Aorta, Thoracic; D001025:Aortitis / Q000175:diagnosis* / Q000276:immunology / Q000378:metabolism; D003937:Diagnosis, Differential; D003951:Diagnostic Errors; D005260:Female; D005500:Follow-Up Studies; D006406:Hematoma / Q000175:diagnosis*; D006801:Humans; D007074:Immunoglobulin G / Q000276:immunology* / Q000378:metabolism
chemical_list: D000888:Antibodies, Anti-Idiotypic; D007074:Immunoglobulin G