title: Congenitally corrected transposition of the great arteries with anomalous inferior vena cava drainage: multimodality imaging.
abstract: Atrioventricular discordance with ventricular-arterial discordance is a rare cardiac anomaly known as congenitally corrected transposition of the great arteries (CCTGA). This malformation has a prevalence of 0.4-0.6% of all congenital heart disease cases. Complete heart block develops in up to 30% of patients with CCTGA. We present the case of a 62-year-old woman diagnosed with CCTGA who, on echocardiography, had anomalous venous drainage where the inferior vena cava (IVC) bypassed the right atrium and drained into the azygos system. Complementary images with magnetic resonance imaging demonstrated the unique anatomical relationship between the IVC, azygos venous system, and the superior vena cava.
authors.affiliation: Aurora Cardiovascular Services, Aurora Sinai/Aurora St. Luke's Medical Centers, University of Wisconsin School of Medicine and Public Health, Milwaukee, Wisconsin, USA.
authors.forename: Timothy E
authors.initials: TE
authors.lastname: Paterick
authors.forename: Matthew
authors.initials: M
authors.lastname: Schmidt
authors.forename: M Fuad
authors.initials: MF
authors.lastname: Jan
authors.forename: Christopher
authors.initials: C
authors.lastname: Kramer
authors.forename: Matt M
authors.initials: MM
authors.lastname: Umland
authors.forename: Daniel
authors.initials: D
authors.lastname: Bloomgarden
authors.forename: A Jamil
authors.initials: AJ
authors.lastname: Tajik
mesh_terms: D001401:Azygos Vein / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000473:pathology; D000080041:Congenitally Corrected Transposition of the Great Arteries; D003937:Diagnosis, Differential; D004452:Echocardiography / Q000379:methods*; D005260:Female; D005402:Fistula / Q000151:congenital / Q000175:diagnosis*; D006801:Humans; D019028:Magnetic Resonance Imaging, Cine / Q000379:methods*; D008875:Middle Aged; D014188:Transposition of Great Vessels / Q000150:complications* / Q000175:diagnosis*; D014682:Vena Cava, Inferior / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000473:pathology