title: Skull base tumor in a patient with phacomatosis pigmentovascularis.
abstract: A 58-year-old man with clinical diagnosis of phacomatosis pigmentovascularis (PPV) experienced tinnitus and progressive hearing loss due to a jugular foramen tumor.Attached to the tumor capsule, were several pigmented spots. Pathological examination revealed a tumor composed by two different tissues, namely a Schwannoma grade I associated with a leptomeningeal blue nevus. The neuropathological aspects of this unusual association are discussed. The association of PPV with a pigmented skull base tumor has not been described to date and illustrates the importance of systemic examination in PPV.
authors: Carlos H
authors: CH
authors: Carvalho
authors: Leonardo M
authors: LM
authors: Batista
authors: Antje
authors: A
authors: Bornemann
authors: Marcus André
authors: MA
authors: Acioly
authors: Marcos
authors: M
authors: Tatagiba
mesh_terms: D006801:Humans; D008297:Male; D008577:Meningeal Neoplasms / Q000150:complications / Q000473:pathology* / Q000601:surgery; D008875:Middle Aged; D009378:Neoplasms, Multiple Primary / Q000473:pathology* / Q000601:surgery; D009442:Neurilemmoma / Q000150:complications / Q000473:pathology* / Q000601:surgery; D020752:Neurocutaneous Syndromes / Q000150:complications* / Q000473:pathology; D019635:Neurosurgical Procedures; D018329:Nevus, Blue / Q000150:complications / Q000473:pathology* / Q000601:surgery; D019292:Skull Base Neoplasms / Q000150:complications / Q000473:pathology* / Q000601:surgery