title: Diagnosis and management of extensive vascular malformations of the lower limb: part I. Clinical diagnosis.
abstract: There is significant confusion in the literature when describing vascular anomalies, and vascular malformations are often misnamed or incorrectly classified. Part I of this two-part series on the diagnosis and management of extensive vascular malformations of the lower limbs will discuss the dermatologist's role in the diagnosis of these lesions. At least nine types of vascular malformations with specific clinical and radiologic characteristics must be distinguished in the lower limbs: Klippel-Trénaunay syndrome, port-wine stain with or without hypertrophy, cutis marmorata telangiectatica congenita, macrocephaly-capillary malformation, Parkes Weber syndrome, Stewart-Bluefarb syndrome, venous malformation, glomuvenous malformation, and lymphatic malformation. This article highlights the differences in clinical appearance and discusses the differential diagnosis of extensive vascular malformations in an attempt to ensure earlier diagnosis and better outcomes for these patients.
authors: Unit of Vascular Malformations, Department of Dermatology, University Clinic of Navarra, Pamplona, Spain. predondo@unav.es
authors: Pedro
authors: P
authors: Redondo
authors: Leyre
authors: L
authors: Aguado
authors: Antonio
authors: A
authors: Martínez-Cuesta
mesh_terms: D000328:Adult; D000465:Algorithms; D002648:Child; D005918:Glomus Tumor / Q000175:diagnosis; D018324:Hemangioma, Capillary / Q000151:congenital / Q000175:diagnosis / Q000453:epidemiology; D006392:Hemangioma, Cavernous / Q000151:congenital / Q000175:diagnosis / Q000453:epidemiology; D006801:Humans; D006984:Hypertrophy; D007231:Infant, Newborn; D007715:Klippel-Trenaunay-Weber Syndrome / Q000175:diagnosis / Q000453:epidemiology; D007866:Leg / Q000098:blood supply*; D044148:Lymphatic Abnormalities / Q000175:diagnosis; D019339:Port-Wine Stain / Q000175:diagnosis / Q000453:epidemiology; D016715:Proteus Syndrome / Q000175:diagnosis; D012868:Skin Abnormalities / Q000175:diagnosis / Q000628:therapy; D013577:Syndrome; D054079:Vascular Malformations / Q000145:classification / Q000175:diagnosis* / Q000453:epidemiology / Q000628:therapy