Large focal nodular hyperplasia and extrahepatic portosystemic shunt in a male patient: multi-modality imaging features.
Congenital extrahepatic portocaval shunt is a rare condition that is described mostly in female patients. We report an unusual case of a young adult male patient with type 1 congenital extrahepatic portocaval shunt with associated development of a focal nodular hyperplasia on a background of regenerative nodules. With multi-slice CT utilisation, there is increased detection of portocaval malformation in asymptomatic patients. This congenital variant is clinically significant with associated development of hepatocellular lesions, hepatic dysfunction and/or encephalopathy.
Department of Radiology, Royal Prince Alfred Hospital, Camperdown, Sydney, Australia. yuxuansophie@yahoo.com.au
Yu Xuan
YX
Kitzing
James
J
Gallagher
Richard
R
Waugh
D000328:Adult; D001165:Arteriovenous Malformations / Q000150:complications / Q000000981:diagnostic imaging* / Q000473:pathology*; D003287:Contrast Media; D020518:Focal Nodular Hyperplasia / Q000150:complications / Q000000981:diagnostic imaging* / Q000473:pathology*; D019786:Gadolinium DTPA; D006801:Humans; D008279:Magnetic Resonance Imaging / Q000379:methods; D008297:Male; D011168:Portal System / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000473:pathology; D011856:Radiographic Image Enhancement / Q000379:methods; D014057:Tomography, X-Ray Computed / Q000379:methods; D055815:Young Adult
D003287:Contrast Media; C073590:gadolinium ethoxybenzyl DTPA; D019786:Gadolinium DTPA