[Anaesthesia in patients with arthrogryposis].
Arthrogryposis is a rare congenital syndrome, characterised by multiple joint contractures. Children suffering from this disease often need surgical interventions to correct musculoskeletal abnormalities. Among problems which may be encountered are a difficult airway, myopathy, difficulties with peripheral iv placement, and the possibility of  intraoperative hyperthermia.  In three described cases, we used thiopentone and cis-atracurium to induce anaesthesia, which was then maintained with nitrous-oxide and fentanyl. In one case sevoflurane was also used. No problems with intubation or hyperthermia were encountered.
Department of Anaesthesiology and Intensive Therapy, District Hospital of Trauma Surgery in Piekary Śląskie, ul. Bytomska 62, 41-940 Piekary Śląskie. egornik@wp.pl
Ewa
E
Górnik-Właszczuk
Jacek
J
Majewski
Rafał
R
Szczygieł
Jarosław
J
Kurak
D000768:Anesthesia, General / Q000379:methods*; D018685:Anesthetics, Inhalation / Q000008:administration & dosage*; D018686:Anesthetics, Intravenous / Q000008:administration & dosage*; D001176:Arthrogryposis / Q000601:surgery*; D001279:Atracurium / Q000008:administration & dosage; D002648:Child; D004359:Drug Therapy, Combination; D005260:Female; D006801:Humans; D008297:Male; D003473:Neuromuscular Nondepolarizing Agents / Q000008:administration & dosage*; D009609:Nitrous Oxide / Q000008:administration & dosage; D013874:Thiopental / Q000008:administration & dosage; D016896:Treatment Outcome
D018685:Anesthetics, Inhalation; D018686:Anesthetics, Intravenous; D003473:Neuromuscular Nondepolarizing Agents; D001279:Atracurium; D013874:Thiopental; D009609:Nitrous Oxide