An unusual presentation of hemophilia B: pseudotumor of proximal tibia.
Hemophilia is one of the most common genetically inherited causes of bleeding disorders. The usual presentation is continuous bleeding from a wound. Very seldom, it presents as a pseudotumor of bone. When left untreated, it may induce compression and pressure necrosis of adjacent structures. Careful evaluation and a high index of suspicion are usually required to arrive at the correct diagnosis. In this article, we report the case of a 10-year-old boy with hemophilia B (Christmas disease) that presented as a pseudotumor producing a large defect in the proximal tibia.
Department of Orthopedic Syrgery, Maulana Azad Medical College and Lok Nayak Hospital, New Delhi, India.
Saurav
S
Mittal
Sumit
S
Arora
Shilpa
S
Khanna
Lalit
L
Maini
V K
VK
Gautam
D000900:Anti-Bacterial Agents / Q000627:therapeutic use; D016913:Blood Component Transfusion; D001859:Bone Neoplasms / Q000175:diagnosis*; D001915:Braces; D002648:Child; D003029:Coagulants / Q000627:therapeutic use; D003937:Diagnosis, Differential; D005164:Factor IX / Q000008:administration & dosage; D002836:Hemophilia B / Q000150:complications / Q000175:diagnosis* / Q000628:therapy; D006470:Hemorrhage / Q000175:diagnosis* / Q000209:etiology; D006801:Humans; D007719:Knee Joint / Q000473:pathology; D008297:Male; D013977:Tibia / Q000473:pathology*; D016896:Treatment Outcome
D000900:Anti-Bacterial Agents; D003029:Coagulants; D005164:Factor IX