Absent pulmonary valve syndrome coexisting with coarctation of aorta in an adult.
The combination of absent pulmonary valve syndrome with coarctation of aorta is extremely uncommon and pathogenetically intriguing. This unusual association, which defies popular theories of pathogenesis of coarctation, may need to be looked at in the light of the current concepts regarding the morphogenesis of ventricular outflow tracts and aortic arch and the role of neural crest cells in both. A 19-year-old man with this combination underwent single-stage surgical correction though median sternotomy. The surgical management of this condition in adulthood has not been reported before.
Department of Pediatric Cardiology and Cardiac Surgery, Institute of Cardio Vascular Diseases, Madras Medical Mission, Chennai, India.
Monika K
MK
Kotecha
Soman R
SR
Krishnamanohar
Raghavannair S
RS
Kumar
D001017:Aortic Coarctation / Q000150:complications*; D006801:Humans; D017404:In Situ Hybridization, Fluorescence; D008297:Male; D061330:Multidetector Computed Tomography; D011664:Pulmonary Valve / Q000002:abnormalities*; D013771:Tetralogy of Fallot / Q000601:surgery*; D055815:Young Adult