Giant pulmonary artery aneurysm in a patient with vasoreactive pulmonary hypertension: a case report.
BACKGROUND
Pulmonary artery aneurysms are a rare condition, frequently associated with pulmonary hypertension. However, the evolution and treatment of this pathology is still not clear.


METHODS
The authors report a case of a 65-year old patient with pulmonary artery aneurysm associated with pulmonary arterial hypertension. Due to a positive vasoreactivity test, treatment with calcium channel blockers was started with near normalization of the right cardiac pressures. Nevertheless, after 20 months of treatment, the pulmonary artery aneurysm size remained unchanged with an associated severe pulmonary regurgitation and causing extrinsic compression of the main left coronary artery. Surgical correction was successfully performed.


CONCLUSIONS
This is the first case report of a pulmonary artery aneurysm described to be associated with vasoreactive pulmonary hypertension in a living patient. Although medical therapy for pulmonary hypertension was started, surgical correction of the aneurysm was executed in order to prevent its future complications.
Hospital S, Francisco Xavier-Centro Hospitalar de Lisboa Ocidental, Internal Medicine Department, Lisboa, Portugal. inesarauj@gmail.com
Inês
I
Araújo
Pilar
P
Escribano
María Jesus
MJ
Lopez-Gude
Carmen Jimenez
CJ
Lopez-Guarch
Maria Antonia
MA
Sanchez
Maria J
MJ
Ruiz-Cano
Juan
J
Delgado
Jose
J
Cortina
D000368:Aged; D000783:Aneurysm / Q000150:complications / Q000175:diagnosis / Q000503:physiopathology / Q000628:therapy*; D017130:Angioplasty; D018572:Disease-Free Survival; D004548:Elasticity; D004730:Endothelium, Vascular / Q000378:metabolism* / Q000473:pathology; D005260:Female; D006801:Humans; D006973:Hypertension / Q000150:complications / Q000175:diagnosis / Q000503:physiopathology / Q000628:therapy*; D017410:Practice Guidelines as Topic; D011651:Pulmonary Artery / Q000473:pathology / Q000601:surgery*; D011665:Pulmonary Valve Insufficiency