title: Fibrodysplasia ossificans progressiva: anesthetic management in complex orthopedic spine procedures.
abstract: Fibrodysplasia ossificans progressiva (FOP) is a rare disorder of the connective tissue leading to progressive tissue ossification and immobilization. Soft-tissue trauma may exacerbate this condition, causing further ossification. Multisystem involvement includes restrictive lung disease, cervical ankylosis with limited mouth opening, and cardiac dysfunction. A 39-year-old woman with FOP presented with multiple orthopedic spine and femur fractures sustained from a fall. Anesthetic management was complicated by airway, pulmonary, and positioning challenges. Neuromonitoring allowed identification of spinal cord ischemia while avoiding a wake-up test.
authors: Department of Anesthesiology, Upstate Medical University, Syracuse, NY 13210, USA. GorjiR@upstate.edu
authors: Reza
authors: R
authors: Gorji
authors: Fenghua
authors: F
authors: Li
authors: Robert
authors: R
authors: Nastasi
authors: Sarah
authors: S
authors: Stuart
mesh_terms: D000058:Accidental Falls; D000328:Adult; D000758:Anesthesia / Q000379:methods*; D005260:Female; D005264:Femoral Fractures / Q000209:etiology / Q000601:surgery*; D006801:Humans; D016343:Monitoring, Intraoperative; D009221:Myositis Ossificans / Q000150:complications* / Q000503:physiopathology; D019637:Orthopedic Procedures / Q000379:methods; D020760:Spinal Cord Ischemia / Q000175:diagnosis / Q000209:etiology; D016103:Spinal Fractures / Q000209:etiology / Q000601:surgery*