title: Improvement of mouth opening for a patient with fibrodysplasia ossificans progressiva: a case report.
abstract: The aim of this article is to describe the care of a patient with fibrodysplasia ossificans progressiva (FOP) and to provide dentists with a guide for how to safely care for patients with FOP. Treatment improved the patient's limited mouth opening. FOP is a rare autosomal dominant disorder characterized by congenital malformation of the fingers and toes by heterotopic ossification progressiva of the connective tissue. This ossification causes a limitation in osteoradicular mobility, mainly affecting the spine, shoulders, hips, and peripheral joints. The disease can manifest from pregnancy until adulthood, with no greater prevalence associated with race or gender. Although rare, the disease can be easily identified by its clinical features, and diagnosis can be confirmed by a radiographic examination. There is no known effective treatment for this disease. All therapeutic treatment must be conservative to avoid any condition that may cause heterotopic ossification. Guidelines to prevent new ossifications are important for patients with FOP. Dental professionals should be cautious in planning treatment, avoiding anesthesia, especially in the mandible, to prevent ankylosis of the temporo-mandibular joints. The prevention of dental caries is essential to avoid the need for more invasive treatment.
authors: Department of Dentistry, Pontifical Catholic University of Minas Gerais, Belo Horizonte, Minas Gerais, Brazil.
authors: Júlia Maria
authors: JM
authors: Braga
authors: Maria Fernanda Andrade Marques
authors: MF
authors: Silva
authors: Luis Cândido Pinto da
authors: LC
authors: Silva
authors: Paulo Isaías
authors: PI
authors: Seraidarian
authors: Roberval de Almeida
authors: Rde A
authors: Cruz
mesh_terms: D000844:Ankylosis / Q000517:prevention & control; D002114:Calcinosis / Q000175:diagnosis; D005081:Exercise Therapy / Q000295:instrumentation; D006801:Humans; D020247:Myofunctional Therapy / Q000295:instrumentation; D009221:Myositis Ossificans / Q000175:diagnosis / Q000628:therapy*; D009999:Ossification, Heterotopic / Q000175:diagnosis; D016059:Range of Motion, Articular / Q000502:physiology*; D013705:Temporomandibular Joint Disorders / Q000517:prevention & control / Q000628:therapy*