title: [Epitheliotropic lymphomas: better identification for improved treatment].
abstract: Mycosis fungoides is the most frequent cutaneous T cell lymphoma. Mycosis fungoides-related cutaneous T cell lymphomas include folliculotropic mycosis fungoides, with or without mucinosis, pagetoid reticulosis and granulomatous slack skin. Sezary syndrome is characterized by pruriginous erythroderma, adenopathies, atypical lymphocytes in the blood and a more aggressive course. B cell lymphomas represent 25 % of cutaneous lymphomas. Primary cutaneous follicle center cell lymphomas are the most frequent. They are often located on the head and trunk and have an indolent course. Primary cutaneous marginal zone B-cell lymphomas, which are more frequently multicentric and located on the limbs, also have an indolent course. In contrast, primary cutaneous diffuse large B-cell lymphomas, leg type, and primary cutaneous intravascular large B-cell lymphomas have a more aggressive course. Treatment must be adapted to each case. Unnecessarily aggressive treatments must be avoided in patients with indolent lymphomas.
authors: Dermatologie, APHP, Hôpital Saint Louis, Université Paris 7, Unité Inserm U976, Centre de Recherche sur la Peau, 1 Avenue Claude Vellefaux, 75010 Paris. martine.bagot@sls.aphp.fr
authors: Martine
authors: M
authors: Bagot
mesh_terms: D003937:Diagnosis, Differential; D006801:Humans; D008223:Lymphoma / Q000145:classification / Q000175:diagnosis* / Q000628:therapy*; D016393:Lymphoma, B-Cell / Q000175:diagnosis / Q000473:pathology / Q000628:therapy; D016410:Lymphoma, T-Cell, Cutaneous / Q000175:diagnosis / Q000473:pathology / Q000628:therapy; D009182:Mycosis Fungoides / Q000175:diagnosis* / Q000628:therapy*; D011379:Prognosis; D058996:Quality Improvement; D011787:Quality of Health Care / Q000639:trends; D012878:Skin Neoplasms / Q000175:diagnosis* / Q000628:therapy*