title: Congenital malignant rhabdoid tumor of the scalp.
abstract: BACKGROUND
  Malignant rhabdoid tumors (MRT) are rare but aggressive tumors presenting in the pediatric population. First thought a variant of Wilms' tumor in the kidney, it is recognized as presenting at renal, central nervous system and other extra-renal primary sites. It is uniformly of very poor prognosis, however.
  
  
  METHODS
  We present a case of congenital MRT of the scalp, which we believe to be the first described at this site. The clinical and histopathological features of the tumor are discussed in light of the current literature on MRT at other sites. The bleak prognosis at this site appears to be no different from others - the child succumbed at 10 months old despite surgical resection and initial excellent response to chemotherapy.
  
  
  CONCLUSIONS
  Malignant rhabdoid tumor has a very poor prognosis and needs to be considered in the differential diagnosis of similar lesions by clinicians involved in pediatric head and neck care.
authors.affiliation: Craniofacial Centre, Great Ormond Street Hospital for Children, Great Ormond Street, London WC1N 3JH, UK. alicobb@yahoo.com
authors.forename: Alistair R M
authors.initials: AR
authors.lastname: Cobb
authors.forename: Neil J
authors.initials: NJ
authors.lastname: Sebire
authors.forename: John
authors.initials: J
authors.lastname: Anderson
authors.forename: David
authors.initials: D
authors.lastname: Dunaway
mesh_terms: D001932:Brain Neoplasms / Q000556:secondary; D003937:Diagnosis, Differential; D017809:Fatal Outcome; D005260:Female; D006258:Head and Neck Neoplasms / Q000151:congenital*; D006391:Hemangioma / Q000175:diagnosis; D006801:Humans; D007223:Infant; D009364:Neoplasm Recurrence, Local / Q000473:pathology; D018335:Rhabdoid Tumor / Q000151:congenital* / Q000556:secondary; D012535:Scalp / Q000473:pathology*; D012878:Skin Neoplasms / Q000151:congenital*; D013724:Teratoma / Q000175:diagnosis