title: Spontaneously healed membranous type ventricular septal defect with malaligned interventricular septal wall and double-chambered right ventricle in a 56-year-old patient.
abstract: A 56-year-old male presented with resting dyspnea and chest discomfort for several years. During transthoracic and transesophageal echocardiography, a spontaneously healed membranous type ventricular septal defect (VSD) with malaligned interventricular septal wall, aneurysmal changes, a subaortic ridge and a double-chambered right ventricle (DCRV) was observed. When combined with DCRV, VSD with malalignment between the outlet and trabecular septa was associated with tetralogy of Fallot. The subaortic ridge was due to turbulent flow caused by the malalignment-type VSD. The VSD with malaligned interventricular septal wall can be developed after aneurismal changes of a perimembranous VSD. We report here in the unusual case of a 56-year-old patient who had a pathology complex comprising DCRV, subaortic ridge, spontaneously healed membranous type VSD with malaligned interventricular septal wall, and survived with surgical treatment.
authors.affiliation: Department of Internal Medicine, School of Medicine, The Catholic University of Korea, Seoul, Korea.
authors.forename: Jung Sun
authors.initials: JS
authors.lastname: Cho
authors.forename: Ho-Joong
authors.initials: HJ
authors.lastname: Youn
authors.forename: Sung-Ho
authors.initials: SH
authors.lastname: Her
authors.forename: Soe Hee
authors.initials: SH
authors.lastname: Ahn
authors.forename: Mahn-Won
authors.initials: MW
authors.lastname: Park
authors.forename: Min Suk
authors.initials: MS
authors.lastname: Choi
authors.forename: Jae Bum
authors.initials: JB
authors.lastname: Lee
authors.forename: Jeong U
authors.initials: JU
authors.lastname: Baeg
authors.forename: Chan Seok
authors.initials: CS
authors.lastname: Park
authors.forename: Mi-Jeong
authors.initials: MJ
authors.lastname: Kim
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