title: Febrile ulceronecrotic Mucha-Habermann disease (pityriasis lichenoides et varioliformis acuta fulminans) presenting as Stevens-Johnson syndrome.
abstract: We present two pediatric patients with pityriasis lichenoides et varioliformis acuta fulminans whose admitting diagnosis was Stevens Johnson Syndrome. The patients were successfully treated with methotrexate and prednisone. These cases highlight the importance of early recognition and treatment of this disease to prevent further morbidity and a potentially fatal prognosis.
authors.affiliation: Department of Dermatology, Wake Forest Baptist Health, Winston-Salem, NC 27104, USA.
authors.forename: William S
authors.initials: WS
authors.lastname: Kaufman
authors.forename: Elizabeth K
authors.initials: EK
authors.lastname: McNamara
authors.forename: Ashley R
authors.initials: AR
authors.lastname: Curtis
authors.forename: Payman
authors.initials: P
authors.lastname: Kosari
authors.forename: Joseph L
authors.initials: JL
authors.lastname: Jorizzo
authors.forename: Daniel P
authors.initials: DP
authors.lastname: Krowchuk
mesh_terms: D000900:Anti-Bacterial Agents / Q000627:therapeutic use; D002981:Clindamycin / Q000627:therapeutic use; D003879:Dermatologic Agents / Q000627:therapeutic use; D004359:Drug Therapy, Combination; D005260:Female; D006561:Herpes Simplex / Q000175:diagnosis* / Q000188:drug therapy; D006801:Humans; D007223:Infant; D008727:Methotrexate / Q000627:therapeutic use; D017514:Pityriasis Lichenoides / Q000175:diagnosis* / Q000188:drug therapy; D011241:Prednisone / Q000627:therapeutic use; D012883:Skin Ulcer / Q000175:diagnosis* / Q000188:drug therapy; D013262:Stevens-Johnson Syndrome / Q000175:diagnosis*; D016896:Treatment Outcome; D014640:Vancomycin / Q000627:therapeutic use
chemical_list: D000900:Anti-Bacterial Agents; D003879:Dermatologic Agents; D002981:Clindamycin; D014640:Vancomycin; D011241:Prednisone; D008727:Methotrexate