title: A case of undifferentiated embryonic liver sarcoma mimicking cystic hydatid disease in an endemic region of the world.
abstract: Undifferentiated embryonic liver sarcoma (UELS) is a rare highly malignant neoplasm that predominantly occurs in children between 5 and 10 years of age. The typical radiologic appearance on ultrasound and computed tomography of UELS shows a large septated mass having combined cystic and solid components. These radiographic features, however, are not specific to UELS and are shared by other more common and benign diseases of the liver. For example, cystic hydatid disease (CHD), caused by larvae of the Echinococcus tapeworm, is the most common indication for hepatic operations in children residing in endemic regions of the world. Undifferentiated embryonic liver sarcoma and CHD are 2 diseases that share overlapping presenting features of patient age, symptoms, and radiologic appearance. Surgeons who operate in Echinococcal endemic regions must be aware that not all hepatic cystic masses are necessarily CHD and may be other more rare malignant diseases such as UELS.
authors.affiliation: Department of Pediatric Surgery, Faculty of Medicine, Ataturk University, Erzurum, Turkey. ak_oral@hotmail.com
authors.forename: Akgun
authors.initials: A
authors.lastname: Oral
authors.forename: Murat
authors.initials: M
authors.lastname: Yigiter
authors.forename: Elif
authors.initials: E
authors.lastname: Demirci
authors.forename: Zuhal Keskin
authors.initials: ZK
authors.lastname: Yildirim
authors.forename: Mecit
authors.initials: M
authors.lastname: Kantarci
authors.forename: Ahmet Bedii
authors.initials: AB
authors.lastname: Salman
mesh_terms: D015746:Abdominal Pain / Q000209:etiology; D015766:Albendazole / Q000627:therapeutic use; D000871:Anthelmintics / Q000627:therapeutic use; D000971:Antineoplastic Combined Chemotherapy Protocols / Q000627:therapeutic use; D016190:Carboplatin / Q000008:administration & dosage; D002648:Child; D003951:Diagnostic Errors; D004317:Doxorubicin / Q000008:administration & dosage; D004444:Echinococcosis, Hepatic / Q000175:diagnosis / Q000000981:diagnostic imaging* / Q000453:epidemiology; D019353:Endemic Diseases; D006498:Hepatectomy; D006801:Humans; D007069:Ifosfamide / Q000008:administration & dosage; D008113:Liver Neoplasms / Q000175:diagnosis / Q000000981:diagnostic imaging* / Q000188:drug therapy / Q000601:surgery; D008297:Male; D009373:Neoplasms, Germ Cell and Embryonal / Q000175:diagnosis / Q000000981:diagnostic imaging* / Q000188:drug therapy / Q000601:surgery; D014057:Tomography, X-Ray Computed; D014421:Turkey / Q000453:epidemiology; D014750:Vincristine / Q000008:administration & dosage
chemical_list: D000871:Anthelmintics; D014750:Vincristine; D004317:Doxorubicin; D016190:Carboplatin; D015766:Albendazole; D007069:Ifosfamide