title: [The man from the kingdom of the near-dead - modern treatment of pulmonary hypertension].
abstract: Pulmonary arterial hypertension (PAH) is a rare and severe condition characterised by a progressive increase in pulmonary vascular resistance. Two decades ago patients with idiopathic PAH were defined as the people from the kingdom of near- -dead because of poor survival. The progress in treatment of PAH was made, however the disease is still severe and not curable. We present a 26 year-old male patient diagnosed with idiopathic PAH. The clinical course was complicated by progressive worsening, hemoptysis and thrombocytopenia. Treatment with treprostinil and bronchial artery embolisation was started, resulting in symptomatic and functional improvement.
authors.affiliation: I Klinika Kardiologii, Uniwersytet Medyczny im. Karola Marcinkowskiego, Poznań. anna.olasinska@poczta.onet.pl
authors.forename: Anna
authors.initials: A
authors.lastname: Olasińska-Wiśniewska
authors.forename: Tatiana
authors.initials: T
authors.lastname: Mularek-Kubzdela
authors.forename: Aleksander
authors.initials: A
authors.lastname: Araszkiewicz
authors.forename: Magdalena
authors.initials: M
authors.lastname: Janus
authors.forename: Stanisław
authors.initials: S
authors.lastname: Jankiewicz
authors.forename: Anna
authors.initials: A
authors.lastname: Komosa
authors.forename: Robert
authors.initials: R
authors.lastname: Juszkat
authors.forename: Marcin
authors.initials: M
authors.lastname: Kurzyna
authors.forename: Stefan
authors.initials: S
authors.lastname: Grajek
mesh_terms: D000328:Adult; D000959:Antihypertensive Agents / Q000627:therapeutic use*; D004621:Embolization, Therapeutic / Q000379:methods*; D011464:Epoprostenol / Q000031:analogs & derivatives* / Q000627:therapeutic use; D065627:Familial Primary Pulmonary Hypertension; D006469:Hemoptysis / Q000209:etiology*; D006801:Humans; D006976:Hypertension, Pulmonary / Q000150:complications / Q000628:therapy*; D008297:Male; D013921:Thrombocytopenia / Q000209:etiology*; D016896:Treatment Outcome
chemical_list: D000959:Antihypertensive Agents; D011464:Epoprostenol; C427248:treprostinil