title: Diagnosis and management of congenital rectourethral fistula in a child with long tubular duplication of the colon and Klippel-Feil syndrome.
abstract: We describe a unique association of congenital rectourethral fistula with long tubular duplication of the colon in a boy with Klippel-Feil syndrome and Sprengel deformity. He presented with a rectourethral fistula after surgical repair of a tubular duplication of the terminal ileum, colon, and proximal rectum. Preoperative identification of the fistula was challenging and was only achieved after cystoscopy with injection of methylene blue under pressure through Foley catheters placed into the anus and distal stoma of a colostomy. Surgical repair was performed through the posterior sagittal approach. The patient is doing well after 4 years of follow-up.
authors.affiliation: Department of Pediatric Urology, Pediatric Surgery Service, Hospital de Clínicas de Porto Alegre, Porto Alegre, RS, Brazil. dudaccosta@terra.com.br
authors.forename: Eduardo Corrêa
authors.initials: EC
authors.lastname: Costa
authors.forename: Cristina Targa
authors.initials: CT
authors.lastname: Ferreira
authors.forename: João Luiz Pippi
authors.initials: JL
authors.lastname: Salle
authors.forename: José Carlos
authors.initials: JC
authors.lastname: Fraga
mesh_terms: D003106:Colon / Q000002:abnormalities*; D003125:Colostomy; D003248:Constipation / Q000209:etiology; D003558:Cystoscopy; D006801:Humans; D007223:Infant; D007714:Klippel-Feil Syndrome / Q000150:complications*; D008297:Male; D008751:Methylene Blue; D012003:Rectal Fistula / Q000151:congenital* / Q000175:diagnosis / Q000601:surgery; D014522:Urethral Diseases / Q000151:congenital* / Q000175:diagnosis / Q000601:surgery; D014548:Urinary Fistula / Q000151:congenital* / Q000175:diagnosis / Q000601:surgery
chemical_list: D008751:Methylene Blue