title: Pleuropulmonary blastoma as characteristic cause of pneumothorax.
abstract: BACKGROUND
  Pleuropulmonary blastoma (PPB) is the most common lung neoplasms in childhood. Usually presents as recurrent respiratory infections and in some cases as pneumothorax.
  
  
  METHODS
  We report the case of a 2-year-old patient that was diagnosed with PPB, that first manifested as recurrent pneumothorax. Three chest computed tomography were necessary for the diagnosis. The first 2 tomographies showed no abnormalities suggestive of malignancy. The patient had a family history of both PPB and leukemia. Three years and a half after completion of treatment, the patient is in complete remission.
  
  
  CONCLUSIONS
  PPB is an uncommon disease but is the most common pulmonary neoplasms in childhood. We must suspect it in patients with a suggestive family history and recurrent pneumothorax in the same location.
authors: Pediatric Intensive Care Unit, Hospital Infantil Universitario Niño Jesús, Madrid, Spain.
authors: Beatriz
authors: B
authors: Cabeza
authors: Gonzalo
authors: G
authors: Oñoro
authors: Alberto García
authors: AG
authors: Salido
authors: Alvaro
authors: A
authors: Lassaletta
authors: Inmaculada
authors: I
authors: de Prada
authors: Gustavo
authors: G
authors: Albi
authors: Lucas
authors: L
authors: de Mingo
authors: Ana
authors: A
authors: Serrano
mesh_terms: D002675:Child, Preschool; D005260:Female; D006801:Humans; D008175:Lung Neoplasms / Q000150:complications* / Q000473:pathology / Q000628:therapy; D011030:Pneumothorax / Q000209:etiology*; D018202:Pulmonary Blastoma / Q000150:complications* / Q000473:pathology / Q000628:therapy