title: A multidisciplinary approach to the treatment of oral manifestations associated with Beckwith-Wiedemann syndrome: a long-term case report.
abstract: BACKGROUND
  Beckwith-Wiedemann syndrome (BWS) is a congenital disorder that involves a somatic overgrowth during the patient's first years of life. Exomphalos, macroglossia and gigantism are the main clinical symptoms.
  
  
  METHODS
  The authors describe a 15-year follow-up in a patient with BWS. They focus on a multidisciplinary approach to treating the patient's oral manifestations from age 9 months. The approach included an initial physiotherapy treatment, a partial glossectomy, a first phase of orthopedic treatment with a tongue crib and chin cap, and a second phase of orthodontic treatment with an edgewise appliance.
  
  
  CONCLUSIONS
  To obtain long-term positive and stable results, an appropriate treatment plan for patients with BWS and dentoskeletal alterations, including macroglossia, requires surgical tongue reduction when the patient is young, combined with physiotherapeutic phases and orthopedic and orthodontic treatment.
authors: Pediatric Dentistry Unit, School of Medicine and Dentistry, Santiago de Compostela University, Spain.
authors: Maria Teresa
authors: MT
authors: Abeleira
authors: Juan Manuel
authors: JM
authors: Seoane-Romero
authors: Mercedes
authors: M
authors: Outumuro
authors: Flor
authors: F
authors: Caamaño
authors: David
authors: D
authors: Suárez
authors: Inmaculada Tomás
authors: IT
authors: Carmona
mesh_terms: D001506:Beckwith-Wiedemann Syndrome / Q000150:complications*; D005115:Extraoral Traction Appliances; D005500:Follow-Up Studies; D005927:Glossectomy; D006801:Humans; D007223:Infant; D008137:Longitudinal Studies; D008260:Macroglossia / Q000601:surgery; D008265:Macrostomia / Q000628:therapy; D008297:Male; D008313:Malocclusion, Angle Class III / Q000628:therapy; D008334:Mandible / Q000254:growth & development; D008437:Maxilla / Q000254:growth & development; D009059:Mouth Diseases / Q000628:therapy*; D020247:Myofunctional Therapy / Q000295:instrumentation / Q000379:methods; D024343:Open Bite / Q000628:therapy; D016382:Orthodontic Appliance Design; D010155:Palatal Expansion Technique / Q000295:instrumentation; D010347:Patient Care Planning; D010348:Patient Care Team; D026741:Physical Therapy Modalities; D014087:Tooth Movement Techniques