title: Anesthetic management of an adult patient with Rett syndrome and limited mouth opening -A case report-.
abstract: Rett syndrome is a neurological disease that occurs only in females and it manifests with mental retardation, seizures, movement disorders, autistic behavior and abnormal breathing. A 19-year-old female with Rett syndrome underwent ophthalmologic surgery under general anesthesia at our institution. Airway control was difficult due to her limited mouth opening. We recommend that anesthesiologists should have proper knowledge about this disease and the patients to avoid the complications and problems that can be encountered during the perioperative period.
authors.affiliation: Department of Anesthesiology and Pain Medicine, Kyung Hee University Hospital at Gangdong, College of Medicine, Kyung Hee University, Seoul, Korea.
authors.forename: Ji-Sung
authors.initials: JS
authors.lastname: Nho
authors.forename: Dong-Shik
authors.initials: DS
authors.lastname: Shin
authors.forename: Jee-Youn
authors.initials: JY
authors.lastname: Moon
authors.forename: Jae-Woo
authors.initials: JW
authors.lastname: Yi
authors.forename: Jong-Man
authors.initials: JM
authors.lastname: Kang
authors.forename: Bong-Jae
authors.initials: BJ
authors.lastname: Lee
authors.forename: Dong-Ok
authors.initials: DO
authors.lastname: Kim
authors.forename: Jun-Young
authors.initials: JY
authors.lastname: Chung