title: Two patients with audiovestibular sarcoidosis.
abstract: We report two patients with biopsy-proven audiovestibular sarcoidosis who presented with hearing loss, vertigo and gait ataxia. Oto-neurological investigations confirmed the presence of sensorineural hearing loss, vestibular hypofunction and abnormal auditory brainstem responses. MRI scans of the brain revealed enhancement of the vestibulo-cochlear nerves. Both patients responded to high dose oral corticosteroid treatment, although one patient has required multiple trials of immunosuppressant drug therapy because of relapsing disease.
authors.affiliation: Department of Neurology, Monash Medical School, Alfred Hospital, Melbourne, Victoria, Australia. dsz@me.com
authors.forename: David J
authors.initials: DJ
authors.lastname: Szmulewicz
authors.forename: John A
authors.initials: JA
authors.lastname: Waterston
mesh_terms: D002493:Central Nervous System Diseases / Q000150:complications / Q000188:drug therapy / Q000473:pathology*; D005260:Female; D006319:Hearing Loss, Sensorineural / Q000175:diagnosis* / Q000209:etiology; D006801:Humans; D008875:Middle Aged; D012507:Sarcoidosis / Q000150:complications / Q000188:drug therapy / Q000473:pathology*; D016896:Treatment Outcome; D000160:Vestibulocochlear Nerve Diseases / Q000175:diagnosis* / Q000209:etiology