title: Pediatric clear cell sarcoma of the kidney with cavoatrial thrombus.
abstract: Clear cell sarcoma of the kidney (CCSK) is a rare renal tumor. Only 4 cases of CCSK with vascular thrombus have been reported, and 2 of these were pediatric cases. One of the children had an intraatrial thrombus as well. We describe a 3-year-old boy who was diagnosed as having a Wilms tumor but did not respond to preresection chemotherapy. He underwent complete resection of the tumor under cardiopulmonary bypass. Histologic examination indicated that the tumor was a CCSK. The patient was then managed with appropriate chemotherapy and radiation therapy and is well 16 months after diagnosis.
authors.affiliation: Department of Pediatric Surgery, All India Institute of Medical Sciences, New Delhi, India.
authors.forename: Nidhi
authors.initials: N
authors.lastname: Sugandhi
authors.forename: Gayatri
authors.initials: G
authors.lastname: Munghate
authors.forename: Dhananjay P
authors.initials: DP
authors.lastname: Malankar
authors.forename: Shambhunath
authors.initials: S
authors.lastname: Das
authors.forename: Akshya Kumar
authors.initials: AK
authors.lastname: Bisoi
authors.forename: Arun Kumar
authors.initials: AK
authors.lastname: Gupta
authors.forename: Sandeep
authors.initials: S
authors.lastname: Agarwala
mesh_terms: D000971:Antineoplastic Combined Chemotherapy Protocols / Q000008:administration & dosage / Q000627:therapeutic use; D002315:Cardiopulmonary Bypass; D002675:Child, Preschool; D003131:Combined Modality Therapy; D003520:Cyclophosphamide / Q000008:administration & dosage; D003609:Dactinomycin / Q000008:administration & dosage; D003951:Diagnostic Errors; D004317:Doxorubicin / Q000008:administration & dosage; D005047:Etoposide / Q000008:administration & dosage; D006325:Heart Atria / Q000000981:diagnostic imaging / Q000473:pathology* / Q000601:surgery; D006503:Hepatic Veins / Q000000981:diagnostic imaging / Q000473:pathology / Q000601:surgery; D006801:Humans; D007680:Kidney Neoplasms / Q000150:complications / Q000175:diagnosis* / Q000188:drug therapy / Q000473:pathology / Q000532:radiotherapy / Q000601:surgery; D008297:Male; D020360:Neoadjuvant Therapy; D009392:Nephrectomy / Q000379:methods*; D018227:Sarcoma, Clear Cell / Q000150:complications / Q000175:diagnosis* / Q000188:drug therapy / Q000473:pathology / Q000532:radiotherapy / Q000601:surgery; D017131:Thrombectomy; D014057:Tomography, X-Ray Computed; D014463:Ultrasonography; D014682:Vena Cava, Inferior / Q000000981:diagnostic imaging / Q000473:pathology* / Q000601:surgery; D020246:Venous Thrombosis / Q000000981:diagnostic imaging / Q000209:etiology* / Q000601:surgery; D014750:Vincristine / Q000008:administration & dosage; D009396:Wilms Tumor / Q000175:diagnosis
chemical_list: D003609:Dactinomycin; D014750:Vincristine; D005047:Etoposide; D004317:Doxorubicin; D003520:Cyclophosphamide