title: Chronic thromboembolic pulmonary hypertension due to upper-extremity deep vein thrombosis caused by thoracic outlet syndrome.
abstract: We report on a 20 year-old woman diagnosed with pulmonary embolism (PE) and right subclavian vein thrombosis attributable to stasis caused by right clavicular prominence. At the 10-months follow-up, the patient had developed chronic thromboembolic pulmonary hypertension (CTEPH), and treatment was begun with a dual endothelin receptor antagonist. Very few cases of deep venous thrombosis of upper limb have been reported in relation to anatomical abnormalities. This case is also exceptional because the patient developed a chronic thromboembolic pulmonary hypertension, whose incidence is estimated at 0.5% of all symptomatic PE.
authors.affiliation: Neumología, Unidad Médico-Quirúrgica de Enfermedades Respiratorias, Hospital Universitario Virgen del Rocío, Sevilla, España. Martina11@hotmail.com
authors.forename: Marta
authors.initials: M
authors.lastname: Ferrer Galván
authors.forename: Luis
authors.initials: L
authors.lastname: Jara Palomares
authors.forename: Candela
authors.initials: C
authors.lastname: Caballero Eraso
authors.forename: José Luis
authors.initials: JL
authors.lastname: López Villalobos
authors.forename: Teresa
authors.initials: T
authors.lastname: Elías Hernández
authors.forename: Remedios
authors.initials: R
authors.lastname: Otero Candelera
mesh_terms: D000959:Antihypertensive Agents / Q000627:therapeutic use; D001132:Arm / Q000098:blood supply*; D001249:Asthma / Q000150:complications; D000077300:Bosentan; D006328:Cardiac Catheterization; D004417:Dyspnea / Q000209:etiology; D005260:Female; D006801:Humans; D006976:Hypertension, Pulmonary / Q000209:etiology*; D011655:Pulmonary Embolism / Q000209:etiology*; D012907:Smoking / Q000009:adverse effects; D013449:Sulfonamides / Q000627:therapeutic use; D013575:Syncope / Q000209:etiology; D013901:Thoracic Outlet Syndrome / Q000150:complications*; D013924:Thrombophlebitis / Q000209:etiology*; D055815:Young Adult
chemical_list: D000959:Antihypertensive Agents; D013449:Sulfonamides; D000077300:Bosentan