title: Progressive lymphangiomatosis and Gorham's disease: case report and clinical implications.
abstract: Lymphangiomatosis is a rare proliferative disorder of the lymphatic system. The etiology is unknown, rendering it difficult to manage. This case report of lymphangiomatosis with features of Gorham's disease reveals the progressive and unexpected nature of the condition. It highlights the need for further research into the pathophysiology and management of lymphangiomatosis as current treatment options are limited.
authors.affiliation: Department of Dermatology, St George's Hospital, London, United Kingdom. kristiana.gordon@stgeorges.nhs.uk
authors.forename: K D
authors.initials: KD
authors.lastname: Gordon
authors.forename: P S
authors.initials: PS
authors.lastname: Mortimer
mesh_terms: D000903:Antibiotics, Antineoplastic / Q000627:therapeutic use; D002675:Child, Preschool; D003937:Diagnosis, Differential; D018450:Disease Progression; D005260:Female; D006801:Humans; D042601:Lymphatic Vessels / Q000002:abnormalities / Q000473:pathology; D008232:Lymphoproliferative Disorders / Q000150:complications / Q000175:diagnosis* / Q000188:drug therapy; D010015:Osteolysis, Essential / Q000150:complications / Q000175:diagnosis* / Q000188:drug therapy; D020123:Sirolimus / Q000627:therapeutic use; D057832:Watchful Waiting
chemical_list: D000903:Antibiotics, Antineoplastic; D020123:Sirolimus