title: Fibroblastic low-grade malignant peripheral nerve sheath tumor in the orbit.
abstract: Malignant peripheral nerve-sheath tumors (MPNSTs) are rare, poorly defined spindle cell sarcomas, and they are accompanied by heterologous elements in some cases. Among them, a fibroblastic element is one of the rarest and has been mentioned in some organs in several publications, but not in the orbit. The authors report a case of fibroblastic low-grade MPNSTs in the orbit. The mass was removed surgically, and the patient has been under close observation without evidence of disease recurrence for 2 years.
authors.affiliation: Department of Ophthalmology, Samsung Medical Center, Sungkyunkwan University School of Medicine, Seoul, Korea.
authors.forename: Jong Chul
authors.initials: JC
authors.lastname: Han
authors.forename: Yoon-Duck
authors.initials: YD
authors.lastname: Kim
authors.forename: Yeon-Lim
authors.initials: YL
authors.lastname: Suh
authors.forename: Mi Jung
authors.initials: MJ
authors.lastname: Kwon
authors.forename: Kyung In
authors.initials: KI
authors.lastname: Woo
mesh_terms: D005260:Female; D005347:Fibroblasts / Q000473:pathology; D006801:Humans; D008279:Magnetic Resonance Imaging; D008875:Middle Aged; D060787:Neoplasm Grading; D018317:Nerve Sheath Neoplasms / Q000473:pathology* / Q000601:surgery; D013508:Ophthalmologic Surgical Procedures; D009918:Orbital Neoplasms / Q000473:pathology* / Q000601:surgery