title: Prune belly syndrome.
abstract: The majority of paediatric surgeons will encounter a patient with prune belly syndrome (PBS) only a few times in their clinical practice. There have been many opposing views in the literature regarding the pathogenesis and management of this complex condition. A detailed review was conducted using PubMed to identify key publications involving PBS. This article discusses the evolution of our understanding of the pathogenesis and diagnosis of PBS, including its typical characteristics. We describe the management options available for bilateral intra-abdominal testes, the deficient abdominal wall, the dilated urinary system and examine the evidence base used to support the current approaches employed.
authors.affiliation: Douglas Cohen Department of Paediatric Surgery, The Children's Hospital at Westmead, Sydney Medical School, The University of Sydney, Sydney, NSW, Australia.
authors.forename: S
authors.initials: S
authors.lastname: Hassett
authors.forename: G H H
authors.initials: GH
authors.lastname: Smith
authors.forename: A J A
authors.initials: AJ
authors.lastname: Holland
mesh_terms: D002648:Child; D003952:Diagnostic Imaging / Q000379:methods*; D014943:Global Health; D006801:Humans; D015994:Incidence; D008297:Male; D011535:Prune Belly Syndrome / Q000175:diagnosis / Q000453:epidemiology / Q000601:surgery; D019651:Plastic Surgery Procedures / Q000379:methods*