title: Lhermitte - Duclos disease with syrinx: case report and literature review.
abstract: BACKGROUND
  Lhermitte-Duclos disease is typified by a hamartomatous lesion of     the cerebellum. It is usually seen in females. The usual presentation is of     raised intracranial pressure along with cerebellar signs.
  
  
  METHODS
  We report     an 18-year-old female patient who presented to us with history of headache and     gait ataxia and was observed to have Lhermitte-Duclos disease with cervical cord     syrinx on imaging.
  
  
  CONCLUSIONS
  To our knowledge this is the fifth case of     Lhermitte-Duclos disease with syringomyelia in the pediatric age group. The     treatment of this condition is decompression of the lesion. Malignant     transformation never occurs and the prognosis is excellent.
authors.affiliation: SKIMS, Department of Neurosurgery, Kashmir, India.
authors.forename: Khursheed
authors.initials: K
authors.lastname: Nayil
authors.forename: Maqbool
authors.initials: M
authors.lastname: Wani
authors.forename: Altaf
authors.initials: A
authors.lastname: Ramzan
authors.forename: Feroze
authors.initials: F
authors.lastname: Shaheen
authors.forename: Iqbal
authors.initials: I
authors.lastname: Lone
authors.forename: Abrar
authors.initials: A
authors.lastname: Wani
mesh_terms: D000293:Adolescent; D002531:Cerebellum / Q000473:pathology / Q000503:physiopathology / Q000601:surgery; D002552:Cerebral Ventricles / Q000473:pathology / Q000503:physiopathology / Q000601:surgery; D019299:Decompression, Surgical / Q000379:methods; D005260:Female; D006222:Hamartoma / Q000150:complications / Q000473:pathology* / Q000503:physiopathology; D006223:Hamartoma Syndrome, Multiple / Q000150:complications / Q000473:pathology* / Q000503:physiopathology; D006801:Humans; D006849:Hydrocephalus / Q000209:etiology / Q000473:pathology* / Q000503:physiopathology; D013116:Spinal Cord / Q000473:pathology / Q000503:physiopathology; D013595:Syringomyelia / Q000209:etiology / Q000473:pathology* / Q000503:physiopathology; D017287:Ventriculoperitoneal Shunt / Q000379:methods