title: Dental care management in a child with recessive dystrophic epidermolysis bullosa.
abstract: Epidermolysis bullosa (EB) is a heterogeneous group of rare genetic disorders characterized by marked fragility of the skin and mucous membranes in which vesiculobullous lesions occur in response to trauma, heat or no apparent cause. The recessive form of EB presents the greatest oral alterations including repeated blistering and scar formation leading to limited oral opening, ankyloglossia, tongue denudation, microstomia, vestibule obliteration and predisposition to oral carcinoma. Routine dental care may cause bullae formation on the lips and oral mucosa. Together with the ingestion of soft and frequently carbohydrate food, these anomalies lead to a high caries risk. This paper documents a case of a child diagnosed with recessive dystrophic epidermolysis bullosa (RDEB); describes the phases and difficulties of dental treatment and the measures that dentists and health care providers should adopt in order to provide a safe and effective dental treatment as well as earlier prevention to these patients.
authors.affiliation: Department of Pediatric Clinic, Preventive and Community Dentistry, Ribeirão Preto Dental School, University of São Paulo, Ribeirão Preto, SP, Brazil.
authors.forename: Carolina Paes
authors.initials: CP
authors.lastname: Torres
authors.forename: Jaciara Miranda
authors.initials: JM
authors.lastname: Gomes-Silva
authors.forename: Thalita Siqueira
authors.initials: TS
authors.lastname: Mellara
authors.forename: Lívia Pasqualini
authors.initials: LP
authors.lastname: Carvalho
authors.forename: Maria Cristina
authors.initials: MC
authors.lastname: Borsatto
mesh_terms: D002327:Cariostatic Agents / Q000627:therapeutic use; D002648:Child; D002921:Cicatrix / Q000209:etiology; D017742:Dental Care for Chronically Ill; D003731:Dental Caries / Q000209:etiology / Q000517:prevention & control; D003733:Dental Caries Susceptibility; D003777:Dental Prophylaxis; D016108:Epidermolysis Bullosa Dystrophica / Q000150:complications*; D005260:Female; D005460:Fluorides, Topical / Q000627:therapeutic use; D005891:Gingivitis / Q000209:etiology; D006801:Humans; D008047:Lip Diseases / Q000209:etiology; D009059:Mouth Diseases / Q000209:etiology / Q000628:therapy*; D009910:Oral Hygiene; D010347:Patient Care Planning
chemical_list: D002327:Cariostatic Agents; D005460:Fluorides, Topical