title: Dental management of PHACE syndrome under general anesthesia.
abstract: PHACE syndrome was first described by Dr. Ilonia Frieden and colleagues in 1996. It is an under-recognized rather than a very rare condition among patients with large facial hemangiomas. It is challenging as it has significant neurological, vascular and airway implications. Vascular malformations compromising cerebral blood flow predispose the patient to strokes and seizures. Subglottic hemangiomas, if present, could bleed during intubation. Meticulous neurological monitoring is mandatory in those undergoing repair of the great vessels. We describe the perioperative management of a child with PHACE syndrome subjected to dental treatment under general anesthesia.
authors.affiliation: Department of Pediatric Dentistry, TN Medical College and BYL Nair Hospital Dental College, Mumbai, India.
authors.forename: S
authors.initials: S
authors.lastname: Fernandes
authors.forename: A
authors.initials: A
authors.lastname: Kakade
authors.forename: A M
authors.initials: AM
authors.lastname: Jetpurwala
authors.forename: B
authors.initials: B
authors.lastname: Patil
authors.forename: S
authors.initials: S
authors.lastname: Jain
authors.forename: P
authors.initials: P
authors.lastname: Kasar
mesh_terms: D000766:Anesthesia, Dental / Q000379:methods*; D000768:Anesthesia, General / Q000379:methods*; D018685:Anesthetics, Inhalation / Q000008:administration & dosage; D018686:Anesthetics, Intravenous / Q000008:administration & dosage; D001017:Aortic Coarctation / Q000150:complications*; D002675:Child, Preschool; D003442:Crowns; D003730:Dental Care for Persons with Disabilities; D003731:Dental Caries / Q000150:complications / Q000628:therapy*; D003788:Dental Pulp Diseases / Q000150:complications / Q000628:therapy*; D003793:Dental Restoration, Permanent; D005124:Eye Abnormalities / Q000150:complications*; D005283:Fentanyl / Q000032:analysis; D006801:Humans; D008297:Male; D008738:Methyl Ethers / Q000008:administration & dosage; D020752:Neurocutaneous Syndromes / Q000150:complications*; D012390:Root Canal Therapy; D000077149:Sevoflurane; D014081:Tooth Extraction
chemical_list: D018685:Anesthetics, Inhalation; D018686:Anesthetics, Intravenous; D008738:Methyl Ethers; D000077149:Sevoflurane; D005283:Fentanyl