title: Pulmonary lymphangiomatosis.
abstract: Lymphangiomatosis is a rare disease characterized by diffuse infiltration of lymphangiomas in the lung, bone, and other tissues. Due to its rarity, the spectrum of lymphangiomatosis is beginning to be elucidated based on case reports. The limited pathological, radiological, and clinical studies have shed light on this disease. Treatments have been tested in unblinded manner with promising results; however, further understanding of the pathogenesis of disease, as well as its natural history, is needed to facilitate drug development.
authors.affiliation: Cardiovascular and Pulmonary Branch, National Heart, Lung, and Blood Institute, National Institutes of Health, Bethesda, MD 20892-1590, USA.
authors.forename: Melissa N
authors.initials: MN
authors.lastname: Satria
authors.forename: Gustavo
authors.initials: G
authors.lastname: Pacheco-Rodriguez
authors.forename: Joel
authors.initials: J
authors.lastname: Moss
mesh_terms: D003937:Diagnosis, Differential; D003952:Diagnostic Imaging; D006801:Humans; D008171:Lung Diseases / Q000151:congenital* / Q000175:diagnosis / Q000628:therapy; D008200:Lymphangiectasis / Q000151:congenital* / Q000175:diagnosis / Q000628:therapy; D018192:Lymphangioleiomyomatosis / Q000175:diagnosis; D012129:Respiratory Function Tests