Primary leiomyosarcoma of the pulmonary artery: a case of a 20-month survivor after incomplete surgical resection.
We report a 53-year-old man who presented with dyspnea and low-grade fever. Cardiac ultrasound showed pulmonary hypertension and an ill-defined echogenic mass within the pulmonary trunk. Computed tomography scan revealed an inhomogeneous mass which filled the main pulmonary trunk with near-total occlusion, and extended into both pulmonary arteries. Anticoagulant therapy was administered based on a presumptive diagnosis of pulmonary thromboembolism. Positron-emission tomography scan was useful for differentiating the mass, which was determined as a pulmonary artery sarcoma by surgical resection. Although complete resection was impossible, the patient survived for 20 months with adjuvant chemotherapy and medical treatment.
Department of Cardiology, National Hospital Organization, Ibusuki Hospital, Japan. k-kashima@ibusuki2.hosp.go.jp
Katsuro
K
Kashima
Erika
E
Yamashita
Hiroko
H
Mataki
Goichi
G
Yotsumoto
Mitsuharu
M
Nomoto
Masahiro
M
Sonoda
Shuichi
S
Hanada
D003937:Diagnosis, Differential; D017809:Fatal Outcome; D019788:Fluorodeoxyglucose F18; D006801:Humans; D007890:Leiomyosarcoma / Q000175:diagnosis* / Q000000981:diagnostic imaging / Q000601:surgery*; D008297:Male; D008875:Middle Aged; D018365:Neoplasm, Residual / Q000175:diagnosis; D049268:Positron-Emission Tomography; D011651:Pulmonary Artery / Q000000981:diagnostic imaging; D011655:Pulmonary Embolism / Q000175:diagnosis; D019275:Radiopharmaceuticals; D019043:Vascular Neoplasms / Q000175:diagnosis* / Q000000981:diagnostic imaging / Q000601:surgery*
D019275:Radiopharmaceuticals; D019788:Fluorodeoxyglucose F18