Superior mesenteric artery syndrome in a patient with Charcot Marie Tooth disease.
The extrinsic compression of the third part of the duodenum as it passes through the aorto-mesenteric angle is known as the superior mesenteric artery syndrome (SMAS). This syndrome is a rare mechanical cause of upper intestinal obstruction, with a reported incidence of between 0.2% and 0.78%. Clinical manifestations of SMAS may be chronic or acute; chronic symptoms include intermittent gastric pain, fullness and occasional episodes of postprandial vomiting, while acute symptoms include incoercible vomiting, oral intolerance, mainly epigastric abdominal distension and abdominal pain. Surgery is recommended only when initial conservative treatment fails. Here, we report what appears to be the third published case of SMAS associated with hereditary motor and sensory neuropathy or Charcot Marie Tooth disease.
Óscar Dario Gómez Beltrán, Amparo Valverde Martínez, María del Carmen Pérez Manrique, Joaquín Sánchez Rodríguez, Enrique Lizárraga Febres, Sebastián Rufián Peña, Department of General Surgery, Reina Sofía Teaching Hospital, Córdoba 14004, Spain.
Oscar Dario Gómez
OD
Beltrán
Amparo Valverde
AV
Martínez
María Del Carmen Pérez
Mdel C
Manrique
Joaquín Sánchez
JS
Rodríguez
Enrique Lizárraga
EL
Febres
Sebastián Rufián
SR
Peña