title: Partial nephrectomy for a large renal lymphatic malformation in a child presenting with hypertension.
abstract: A 9-year-old girl had hypertension (systolic blood pressure of 125 mm Hg) noted at an annual well child visit. An ultrasound study demonstrated a large right renal cystic mass. A partial nephrectomy was performed. The surgical specimen was 9.7 × 9.4 × 6.4 cm and weighed 413.2 g. The tumor stained diffusely positive for smooth muscle actin and focally positive for factor VIII. Final histologic diagnosis was primary intrarenal lymphatic malformation. The case is unusual because of the presentation, size of the mass, as well as the therapeutic approach of partial nephrectomy.
authors.affiliation: Department of Urology, Stony Brook University Medical Center, Stony Brook, NY 11794, USA. wai.lee.8@hsc.stonybrook.edu
authors.forename: Wai
authors.initials: W
authors.lastname: Lee
authors.forename: Praneeth
authors.initials: P
authors.lastname: Vemulapalli
authors.forename: Frederick
authors.initials: F
authors.lastname: Miller
authors.forename: Jonathan
authors.initials: J
authors.lastname: Melquist
authors.forename: Thomas K
authors.initials: TK
authors.lastname: Lee
authors.forename: Frank S
authors.initials: FS
authors.lastname: Darras
mesh_terms: D002648:Child; D005260:Female; D006801:Humans; D006973:Hypertension / Q000209:etiology; D007668:Kidney; D044148:Lymphatic Abnormalities / Q000150:complications / Q000175:diagnosis / Q000601:surgery*; D009392:Nephrectomy / Q000379:methods*