title: Pulmonary tumor thrombotic microangiopathy with cor pulmonale due to desmoplastic small round cell tumor.
abstract: A 12-year-old boy presented acutely after an episode of syncope with perioral cyanosis. He died 19 hours after admission due to cor pulmonale as a complication of metastatic desmoplastic small round cell tumor in the lungs with associated tumor thrombotic microangiopathy.
authors.affiliation: Department of Pathology, Robert Wood Johnson Medical School, New Brunswick, NJ 08903, USA. sadimiet@umdnj.edu
authors.forename: Evita T
authors.initials: ET
authors.lastname: Sadimin
authors.forename: Adrienne G
authors.initials: AG
authors.lastname: Collier
authors.forename: Joseph W
authors.initials: JW
authors.lastname: Gaffney
authors.forename: Billie
authors.initials: B
authors.lastname: Fyfe
mesh_terms: D002648:Child; D058405:Desmoplastic Small Round Cell Tumor / Q000150:complications*; D017809:Fatal Outcome; D006801:Humans; D008175:Lung Neoplasms / Q000150:complications*; D008297:Male; D011660:Pulmonary Heart Disease / Q000209:etiology*; D057049:Thrombotic Microangiopathies / Q000209:etiology*