title: Hennebert's sign in superior semicircular canal dehiscence syndrome: a video case report.
abstract: Superior semicircular canal dehiscence (SSCD) syndrome has been called the great otologic mimicker because its presentation overlaps with otosclerosis, Meniere's disease, perilymphatic fistula, and patulous eustachian tube. A valuable examination finding that can help distinguish SSCD syndrome from other pathologic conditions is the presence of Hennebert's sign, in which pressure changes in the external auditory canal evoke stereotyped eye movements that align in the plane of the dehiscent semicircular canal. This video case report demonstrates Hennebert's sign associated with SSCD syndrome and discusses its pathophysiological basis.
authors.affiliation: Division of Head and Neck Surgery, Memorial Sloan-Kettering Cancer Center, New York, New York, USA.
authors.forename: Andrew G
authors.initials: AG
authors.lastname: Shuman
authors.forename: Syed S
authors.initials: SS
authors.lastname: Rizvi
authors.forename: Chantale W
authors.initials: CW
authors.lastname: Pirouet
authors.forename: Katherine D
authors.initials: KD
authors.lastname: Heidenreich
mesh_terms: D002385:Cataplexy / Q000175:diagnosis / Q000209:etiology*; D003937:Diagnosis, Differential; D018450:Disease Progression; D006801:Humans; D007759:Labyrinth Diseases / Q000150:complications* / Q000175:diagnosis; D008297:Male; D008875:Middle Aged; D038781:Otoscopy; D012665:Semicircular Canals; D013577:Syndrome; D014057:Tomography, X-Ray Computed