title: Dissecting aneurysm in a patient with autosomal dominant polycystic kidney disease.
abstract: Autosomal dominant polycystic kidney disease (ADPKD) is primarily associated with renal failure, but it also causes systemic diseases, including cysts of other systemic organs and cerebral or visceral aneurysm. To make matters worse, life-threatening aortic diseases are associated with ADPKD in some cases. However, only a few reports of ADPKD-associated with thoracic aortic dissection have been published. Herein, we present a case of dissecting aneurysm in a patient with hypertension and ADPKD. He had been followed up for type B aortic dissection for six years. Preoperative creatinine level ranged from 2.1 to 2.4 mg/dl. We performed replacement of the thoracic aorta with prosthetic graft successfully, and postoperatively, dialysis was not required.It is very important for us to recognize the relationship between ADPKD and thoracic aortic dissection, which can cause high mortality and morbidity rates.
authors.affiliation: Department of Cardiovascular surgery, Kobe City Medical Center General Hospital, Kobe, Hyogo, Japan. naotowakimachi@hotmail.co.jp
authors.forename: Naoto
authors.initials: N
authors.lastname: Fukunaga
authors.forename: Mitsuru
authors.initials: M
authors.lastname: Yuzaki
authors.forename: Michihiro
authors.initials: M
authors.lastname: Nasu
authors.forename: Yukikatsu
authors.initials: Y
authors.lastname: Okada
mesh_terms: D000328:Adult; D000784:Aortic Dissection / Q000000981:diagnostic imaging / Q000209:etiology* / Q000601:surgery; D017545:Aortic Aneurysm, Thoracic / Q000000981:diagnostic imaging / Q000209:etiology* / Q000601:surgery; D001027:Aortography / Q000379:methods; D019917:Blood Vessel Prosthesis Implantation; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D016891:Polycystic Kidney, Autosomal Dominant / Q000150:complications* / Q000473:pathology; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome