Benign mediastinal lymphadenopathy presenting as cor triatriatum.
This report describes a patient with a superior mediastinal mass and extensive intrathoracic lymphadenopathy referred for oncologic care. During her evaluation, an abnormal cardiovascular examination resulted in an echocardiographic evaluation and an unanticipated diagnosis of a highly obstructive left atrial cor triatriatum was uncovered. The patient underwent repair of cor triatriatum and lymph node biopsy shortly after the diagnosis was made. The biopsies revealed reactive lymph nodes with lymphatic dilation and no inflammatory or neoplastic features. To our knowledge, this case represents the first pediatric example of extensive mediastinal lymphadenopathy mimicking the appearance of a malignant process as a result of severe pulmonary venous hypertension.
Department of Cardiology, Nationwide Children's Hospital, Columbus, Ohio, USA. cory.noel@nationwidechildrens.org
Cory V
CV
Noel
Jessica
J
Pollard
Lester
L
Permut
Mark
M
Ferguson
Brandy
B
Hattendorf
D001706:Biopsy; D006348:Cardiac Surgical Procedures; D002648:Child; D003310:Cor Triatriatum / Q000150:complications* / Q000175:diagnosis / Q000503:physiopathology / Q000601:surgery; D017548:Echocardiography, Transesophageal; D005260:Female; D006801:Humans; D008206:Lymphatic Diseases / Q000175:diagnosis / Q000209:etiology*; D008482:Mediastinum; D011237:Predictive Value of Tests; D011667:Pulmonary Veins / Q000503:physiopathology*; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome; D014690:Venous Pressure