An infant who has dome-shaped papules.
JXG is a benign disorder of early childhood and primarily occurs in infants and children <2 years of age. It is characterized by solitary or multiple yellow-red nodules on the skin and, rarely, in other organs. The clinical diagnosis of solitary cutaneous JXG usually requires confirmation by biopsy. Referral to a dermatologist should be obtained to exclude other disorders if multiple lesions are present. Clinicians should rule out ocular lesions with referral to an ophthalmologist if the patient is <2 years of age and has multiple lesions of JXG. If ophthalmologic consultation reveals no ocular lesions, screening every 6 months for the first 2 years of life is advised.
Department of Pediatrics, Albany Medical Center, Albany, NY, USA.
Ajay
A
Rana
Stephen
S
de Waal Malefyt
D003937:Diagnosis, Differential; D005260:Female; D005487:Foam Cells / Q000378:metabolism; D006801:Humans; D007150:Immunohistochemistry; D007223:Infant; D014972:Xanthogranuloma, Juvenile / Q000175:diagnosis* / Q000378:metabolism / Q000473:pathology