Hereditary sclerosing poikiloderma.
Hereditary sclerosing poikiloderma (HSP) is a very rare disease. The clinical features are principally widespread poikiloderma and linear hyperkeratotic and sclerotic bands. We report an 18-yr-old male who presented reticular hyperpigmented lesions on the trunk and extremities since 2-yr-old. Also, linear sclerosing bands appeared on both antecubital and popliteal fossae after yr. Histopathologic finding showed dense sclerotic collagen fibers with telangiectasia in the upper dermis and fragmentations of damaged elastic fibers in the elastic stain, consistent with HSP. We report the first Korean case of HSP.
Department of Dermatology, College of Medicine, Yeungnam University, Daegu, Korea.
Hyo Jin
HJ
Lee
Dong Hoon
DH
Shin
Jong Soo
JS
Choi
Ki Hong
KH
Kim
D000015:Abnormalities, Multiple; D000293:Adolescent; D004547:Elastic Tissue / Q000473:pathology; D005385:Fingers / Q000002:abnormalities; D006801:Humans; D017495:Hyperpigmentation / Q000473:pathology; D008297:Male; D008844:Micrognathism / Q000473:pathology; D011038:Rothmund-Thomson Syndrome / Q000175:diagnosis* / Q000473:pathology; D012598:Sclerosis / Q000473:pathology; D012871:Skin Diseases / Q000175:diagnosis / Q000473:pathology