Slowly progressive Foix-Chavany-Marie syndrome as a precursor of a primary progressive aphasia.
Foix-Chavany-Marie syndrome (FCMS) is a rare neurological condition usually associated with bilateral ischemic lesions of the anterior frontoparietal operculum. Here, we present a patient with slowly progressive FCMS owing to focal brain atrophy who developed a language disorder similar to that seen in a primary progressive aphasia.
Neurologische Klinik der Universität Ulm, Oberer Eselsberg 45, 89081 Ulm, Germany. ingo.uttner@uni-ulm.de
Ingo
I
Uttner
Johannes
J
Brettschneider
Alexander
A
Unrath
Axel
A
Riecker
D018888:Aphasia, Primary Progressive / Q000209:etiology / Q000473:pathology* / Q000503:physiopathology*; D001072:Apraxias / Q000209:etiology / Q000473:pathology / Q000503:physiopathology; D003680:Deglutition Disorders / Q000150:complications / Q000209:etiology / Q000473:pathology* / Q000503:physiopathology*; D004401:Dysarthria / Q000150:complications / Q000473:pathology* / Q000503:physiopathology*; D004673:Encephalomyelitis, Acute Disseminated / Q000150:complications / Q000473:pathology* / Q000503:physiopathology*; D005158:Facial Paralysis / Q000150:complications / Q000473:pathology* / Q000503:physiopathology*; D005260:Female; D057180:Frontotemporal Dementia / Q000150:complications / Q000473:pathology* / Q000503:physiopathology*; D006801:Humans; D008875:Middle Aged; D009069:Movement Disorders / Q000209:etiology / Q000473:pathology / Q000503:physiopathology