Portal venous gas: a clinical finding in obstructed infracardiac total anomalous pulmonary venous connection.
Total anomalous pulmonary venous connection is a cyanotic congenital heart defect that presents with a multitude of clinical presentations. We report a case of obstructive total anomalous pulmonary venous connection (TAPVC) which presented in a way that has not previously been described. An infant with mixed type obstructive TAPVC was found to have pulmonary interstitial emphysema and portal venous gas on a scout radiograph obtained prior to computed tomography scan. The presence of portal venous gas indicated a connection between the pulmonary venous system and the portal venous system infradiaphragmatically.
Pediatric Residency Program, Phoenix Children's Hospital, Phoenix, AZ 85016, USA.
Hoyoung
H
Chung
Lawrence D
LD
Lilien
D000015:Abnormalities, Multiple; D015901:Angiography, Digital Subtraction; D003937:Diagnosis, Differential; D004452:Echocardiography; D017809:Fatal Outcome; D005740:Gases; D006330:Heart Defects, Congenital / Q000175:diagnosis*; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D011169:Portal Vein / Q000002:abnormalities*; D011667:Pulmonary Veins / Q000002:abnormalities*; D014057:Tomography, X-Ray Computed; D054079:Vascular Malformations / Q000175:diagnosis*
D005740:Gases