title: Endoscopic endonasal resection of the odontoid peg for paediatric basilar invagination.
abstract: Osteogenesis imperfecta (OI) is a genetic disorder whose primary manifestations are fractures, bone deformity and bone pain. Brainstem compression due to basilar invagination is a rare and potentially life-threatening complication of OI. Children with this condition often require significant medical input and multiple admissions to hospital. Traditionally, anterior decompression is carried out through an open trans-oral route. We describe an endoscopic endonasal approach for resection of the peg in a child with OI and basilar invagination. We believe this approach provides an excellent alternative with minimal morbidity and decreased length of stay especially in the paediatric population.
authors.affiliation: Department of Neurosurgery, Sheffield Children's NHS Foundation Trust, Sheffield, UK. saurabh.sinha@sth.nhs.uk
authors.forename: Saurabh
authors.initials: S
authors.lastname: Sinha
authors.forename: Showkat
authors.initials: S
authors.lastname: Mirza
authors.forename: Nick
authors.initials: N
authors.lastname: Bishop
authors.forename: Hesham
authors.initials: H
authors.lastname: Zaki
authors.forename: John
authors.initials: J
authors.lastname: McMullan
mesh_terms: D000293:Adolescent; D001933:Brain Stem; D003251:Constriction, Pathologic / Q000209:etiology / Q000601:surgery; D019299:Decompression, Surgical / Q000379:methods*; D005260:Female; D006801:Humans; D008279:Magnetic Resonance Imaging; D057605:Natural Orifice Endoscopic Surgery / Q000379:methods*; D009666:Nose; D009809:Odontoid Process / Q000601:surgery*; D010013:Osteogenesis Imperfecta / Q000150:complications*; D013117:Spinal Cord Compression / Q000209:etiology / Q000601:surgery*; D013123:Spinal Fusion / Q000379:methods; D014057:Tomography, X-Ray Computed