title: Surgical correction of aorto-pulmonary window: a rare and lethal cause of pulmonary hypertension.
abstract: Aorto-pulmonary window is a relatively rare congenital cardiac malformation with an overall incidence of 0.1%. Pulmonary hypertension develops quickly if the lesion is left untreated hence early surgical intervention is warranted after diagnosis. The surgery for correction of APW has evolved over years, currently an open repair on cardiopulmonary bypass (CPB) with a single patch technique yields good results. Mortality is affected by association of pulmonary hypertension and other cardiac malformations. We present a case of an infant with a large type II APW with a relatively low pulmonary vascular resistance. Hospital stay was complicated because of pulmonary arterial disease making it an important reason for correction in the first few months of life.
authors.affiliation: School of Medicine, Aga Khan University, Karachi, Pakistan.
authors.forename: Adeel Ahmed
authors.initials: AA
authors.lastname: Shamim
authors.forename: Mubashir Zareen
authors.initials: MZ
authors.lastname: Khan
authors.forename: Mehnaz Ahmed
authors.initials: MA
authors.lastname: Atiq
authors.forename: Mansoor Ahmed
authors.initials: MA
authors.lastname: Khan
authors.forename: Muhammad Muneer
authors.initials: MM
authors.lastname: Amanullah
mesh_terms: D001028:Aortopulmonary Septal Defect / Q000601:surgery*; D006348:Cardiac Surgical Procedures / Q000379:methods*; D002315:Cardiopulmonary Bypass; D006801:Humans; D007223:Infant; D007902:Length of Stay; D008297:Male; D012720:Severity of Illness Index; D016896:Treatment Outcome