title: [Pseudomyxoma of the pleura and of the peritoneum -- case report of a rare disease].
abstract: BACKGROUND
  Pseudomyxoma Peritonei (PMP) is a rare condition, which arises from the abdominal cavity and it may also involve the pleural cavity occasionally. Concomitant involvement of both cavities is rare. The disease is characterized by production of mucinous ascites, and a low-grade carcinoma deriving mostly from the appendix. Pleural seeding may be due to diaphragmatic perforation during surgical intervention, tumour progression, or persistent congenital malformation between the abdominal and pleural cavities.
  
  
  METHODS
  A 44 year-old female patient was treated with pleuropulmonary involvement of pseudomyxoma. Since both the lungs and pleura were involved, radical resection could not have been carried out, and cytoreduction with intraoperative chemotherapy was applied only.
  
  
  CONCLUSIONS
  Pleural progression of pseudomyxoma is uncommon and carries a poor prognosis. Management is similar to abdominal PMP, which involves aggressive cytoreduction and local and/or systemic chemotherapy, if possible.
  
  
  CONCLUSIONS
  PMP is a very uncommon disease with poor prognosis. Extra-abdominal manifestation is rare, too. However, early recognition of the condition may enhance treatment options.
authors.affiliation: Országos Korányi TBC és Pulmonológiai Intézet, Budapest. akoskocsis@gmail.com
authors.forename: Akos
authors.initials: A
authors.lastname: Kocsis
authors.forename: Zsolt
authors.initials: Z
authors.lastname: Markóczy
authors.forename: László
authors.initials: L
authors.lastname: Agócs
authors.forename: Miklós
authors.initials: M
authors.lastname: Molnár
authors.forename: János
authors.initials: J
authors.lastname: Fillinger
authors.forename: Bernadett
authors.initials: B
authors.lastname: Lévay
authors.forename: Pál
authors.initials: P
authors.lastname: Vadász
mesh_terms: D000328:Adult; D000971:Antineoplastic Combined Chemotherapy Protocols / Q000627:therapeutic use; D042241:Early Diagnosis; D005260:Female; D006801:Humans; D007432:Intraoperative Period; D010534:Peritoneal Neoplasms / Q000000981:diagnostic imaging / Q000188:drug therapy / Q000601:surgery; D010997:Pleural Neoplasms / Q000000981:diagnostic imaging / Q000188:drug therapy / Q000601:surgery; D011379:Prognosis; D011553:Pseudomyxoma Peritonei / Q000000981:diagnostic imaging / Q000188:drug therapy / Q000601:surgery; D011859:Radiography; D035583:Rare Diseases