title: Primary congenital pulmonary hypoplasia of a neonate.
abstract: Pulmonary hypoplasia is a rare but usually lethal disease. We report a full-term male neonate who presented with respiratory failure immediately after birth. Chest X-ray revealed a small lung volume despite advanced ventilator support. Respiratory failure persisted and this baby died at 40.5 hours of age. The autopsy showed a lung-to-birth weight ratio of 0.69% and a radial alveoli count of 2.97. All this information confirmed the diagnosis of primary congenital pulmonary hypoplasia.
authors.affiliation: Department of Pediatrics, Taipei Veterans General Hospital, Taipei, Taiwan, ROC.
authors.forename: Jui-Sheng
authors.initials: JS
authors.lastname: Hsu
authors.forename: Yu-Sheng
authors.initials: YS
authors.lastname: Lee
authors.forename: Chin-Hsuan
authors.initials: CH
authors.lastname: Lin
authors.forename: Fen-Yau
authors.initials: FY
authors.lastname: Li
authors.forename: Mei-Jy
authors.initials: MJ
authors.lastname: Jeng
authors.forename: Wen-Jue
authors.initials: WJ
authors.lastname: Soong
authors.forename: Sue-Jen
authors.initials: SJ
authors.lastname: Chen
authors.forename: Ren-Bin
authors.initials: RB
authors.lastname: Tang
mesh_terms: D006801:Humans; D007231:Infant, Newborn; D008168:Lung / Q000002:abnormalities*; D008297:Male; D013902:Radiography, Thoracic; D012127:Respiratory Distress Syndrome, Newborn / Q000209:etiology