title: Primary non-functioning paraganglioma of liver: a rare tumour at an unusual location.
abstract: Pheochromocytomas are rare tumours, 22% of which are extra-adrenal and are known as paragangliomas. We report a case of a young male with non-functioning paraganglioma of the liver; a very uncommon primary site. A CT scan with contrast showed a huge, highly vascular mass lesion in the right lobe of the liver and a core biopsy confirmed it to be a paraganglioma. Whole body study with iodine-131-meta-iodobenzylguanidine (MIBG) tracer highlighted the liver tumour but was negative for any other active lesions depicting that the tumour was confined to the liver. The lesion was completely resected by extended right hepatectomy and the patient had an uneventful recovery. There is no evidence of disease recurrence at 3 years of follow up.
authors.affiliation: Department of Surgery, Aga Khan University & Hospital, Karachi.
authors.forename: Muhammad Rizwan
authors.initials: MR
authors.lastname: Khan
authors.forename: Rushna
authors.initials: R
authors.lastname: Raza
authors.forename: Abdul
authors.initials: A
authors.lastname: Jabbar
authors.forename: Arsalan
authors.initials: A
authors.lastname: Ahmed
mesh_terms: D001706:Biopsy; D004621:Embolization, Therapeutic; D006498:Hepatectomy; D006801:Humans; D007457:Iodine Radioisotopes; D008113:Liver Neoplasms / Q000175:diagnosis* / Q000628:therapy; D010235:Paraganglioma / Q000175:diagnosis* / Q000628:therapy; D035583:Rare Diseases; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome; D055815:Young Adult
chemical_list: D007457:Iodine Radioisotopes