title: Benign chondroid syringoma of the orbit: a rare cause of exophtalmos.
abstract: Chondroid syringoma (CS) of the orbit is an extremely rare benign neoplasm. To the best of our knowledege, this is the second case reported in the english litérature.We report a case of a 41-year-old woman with orbital CS. This tumor developed slowly over 8 years causing indolor, no axil, exophtalmos of the left eye. Computed tomography demonstrated an isodense intraorbital tumor with homogeneous enhancement without bony erosion. On Magnetic resonance imaging the tumor was isointense on T1-weighted imaging, slightly hyper intense on T2-weighted imaging, and enhanced after Gadolinium administration. The patient was operated via left lateral orbitotomy. At surgery the mass was well circumscribed, extraconal, very firm and did not invade or adhere to other structures. The tumor was removed in toto. The diagnosis was confirmed by histopathological examination, the lesion was nodular, and there was differentiation toward the adnexal ductal epithelium with chondromyxoid and adipocytic differentiation in the stroma. No recurrence was seen with one year follow-up.CS should be included in the differential diagnosis of intra-orbital tumors. Complete resection remains the best therapeutic option to prevent recurrence. Close followup is recommended because malignant transformation, although rare, is possible.
authors.affiliation: Departments of Neurosurgery and Anatomopathology Mohammed V Military Teaching Hospital, Mohammed V Souissi University, Rabat, Morocco. hothout_dr@hotmail.com
authors.forename: Hatim
authors.initials: H
authors.lastname: Belfquih
authors.forename: Brahim
authors.initials: B
authors.lastname: El Mostarchid
authors.forename: Mohamed
authors.initials: M
authors.lastname: Oukabli
authors.forename: Ali
authors.initials: A
authors.lastname: Akhaddar
authors.forename: Mohammed
authors.initials: M
authors.lastname: Boucetta
mesh_terms: D008949:Adenoma, Pleomorphic / Q000175:diagnosis / Q000473:pathology*; D000328:Adult; D003937:Diagnosis, Differential; D005094:Exophthalmos / Q000209:etiology*; D005260:Female; D006801:Humans; D008279:Magnetic Resonance Imaging; D009915:Orbit / Q000000981:diagnostic imaging / Q000473:pathology*; D009918:Orbital Neoplasms / Q000000981:diagnostic imaging / Q000473:pathology*; D014057:Tomography, X-Ray Computed