title: Giant congenital nevus with plexiform neurofibroma and malignant peripheral nerve sheath tumor.
abstract: A female patient with a giant congenital nevus associated with plexiform neurinoma and malignant peripheral nerve sheath tumor (MPNST) on head and neck is presented. We theoretically discuss possibilities of mutual origin all three entities, including the Boland theory of neurochristopaty. The clinical, surgical, and histologic aspects of the disease are discussed. Only one similar case in written literature was described.
authors.affiliation: City Hospital Pakrac, Division of Otorhinolaryngology, Pakrac, Croatia. dr.azen@vip.hr
authors.forename: Drazen
authors.initials: D
authors.lastname: Shejbal
authors.forename: Vladimir
authors.initials: V
authors.lastname: Bedekovic
authors.forename: Hrvoje
authors.initials: H
authors.lastname: Cupic
mesh_terms: D000293:Adolescent; D005260:Female; D006258:Head and Neck Neoplasms / Q000151:congenital / Q000473:pathology* / Q000601:surgery; D006801:Humans; D009378:Neoplasms, Multiple Primary; D018317:Nerve Sheath Neoplasms / Q000151:congenital / Q000473:pathology* / Q000601:surgery; D018318:Neurofibroma, Plexiform / Q000151:congenital / Q000473:pathology* / Q000601:surgery; D009506:Nevus / Q000151:congenital / Q000473:pathology* / Q000601:surgery; D016896:Treatment Outcome