title: [Hand management in recessive dystrophic bullous epydermolysis].
abstract: OBJECTIVE
  Recessive distrofic epidermolysis bullosa creates severe hand deformities with disabling functional limitations. Hand surgeon should perform surgery when deformity inibits function, in order to restore the pinch.
  
  
  METHODS
  We present our experience on 44 patients and 58 operated hands, with the following schema: hand degloving, grafting of the first web and intraoperative dynamic splinting.
  
  
  RESULTS
  In 30 patient with an 8 years follow up, 25 had had good or excellent results, and the 5 remaining shows early recurrence.
  
  
  CONCLUSIONS
  Association of a correct surgical approach and adequate intra and post-operative rehabilitation improve hand function and a slow down inevitable recurrence.
authors.affiliation: Scuola di Chirurgia Plastica, Ricostruttiva ed Estetica, Università degli Studi di Milano, U.O.C. di Chirurgia della Mano, Multimedica IRCCS, Ospedale San Giuseppe.
authors.forename: G
authors.initials: G
authors.lastname: Pajardi
authors.forename: C
authors.initials: C
authors.lastname: Novelli
authors.forename: C
authors.initials: C
authors.lastname: Parolo
authors.forename: G
authors.initials: G
authors.lastname: Proserpio
authors.forename: M
authors.initials: M
authors.lastname: Tegon
authors.forename: S
authors.initials: S
authors.lastname: Vecchi
mesh_terms: D003286:Contracture / Q000601:surgery; D016108:Epidermolysis Bullosa Dystrophica / Q000235:genetics / Q000534:rehabilitation / Q000601:surgery*; D005500:Follow-Up Studies; D006227:Hand Deformities, Acquired / Q000235:genetics / Q000534:rehabilitation / Q000601:surgery*; D006801:Humans; D019651:Plastic Surgery Procedures / Q000379:methods; D055502:Secondary Prevention; D016038:Skin Transplantation / Q000379:methods; D016896:Treatment Outcome