title: Perianal rhabdomyosarcoma presenting 21 months after hamartoma excision.
abstract: Perianal rhabdomyosarcoma is a rare type of tumor with a relatively poor prognosis. We present the case of a patient who presented with a cutaneous perianal hamartoma at the age of 6 weeks. 21 months latter a recurrent mass at the excision site proved to be an embryonal rhabdomyosarcoma involving the anal sphincter. A pathologic review of the two specimens confirmed their relatedness. This report highlights the need to maintain a high level of suspicion in cases of recurrence following excision of a benign lesion.
authors.affiliation: Division of Pediatric General Surgery, Centre Hospitalier Universitaire Sainte Justine, Université de Montréal, Montreal, QC, Canada.
authors.forename: N
authors.initials: N
authors.lastname: Piché
authors.forename: N
authors.initials: N
authors.lastname: Patey
authors.forename: D
authors.initials: D
authors.lastname: Dal Soglio
authors.forename: Y
authors.initials: Y
authors.lastname: Samson
authors.forename: S
authors.initials: S
authors.lastname: Bouchard
mesh_terms: D001003:Anal Canal / Q000601:surgery; D001005:Anus Neoplasms / Q000175:diagnosis* / Q000188:drug therapy / Q000601:surgery*; D005500:Follow-Up Studies; D006222:Hamartoma / Q000601:surgery*; D006801:Humans; D007223:Infant; D008297:Male; D009364:Neoplasm Recurrence, Local / Q000175:diagnosis* / Q000188:drug therapy / Q000601:surgery; D018233:Rhabdomyosarcoma, Embryonal / Q000175:diagnosis* / Q000188:drug therapy / Q000601:surgery