title: 3p deletion syndrome: implications for cochlear implantation.
abstract: OBJECTIVE
  To describe the role of cochlear implantation in patients with 3p deletion syndrome. Additionally, this paper will review non-mastoid approaches to the cochlea potentially used in cases of mastoid abnormalities.
  
  
  METHODS
  A 23-month-old child with 3p deletion syndrome (3pDS) presented with suspected hearing loss and characteristic craniofacial abnormalities. Bilateral sensorineural hearing loss (SNHL) was confirmed. Temporal bone computed tomography showed poorly developed mastoids bilaterally.
  
  
  METHODS
  Cochlear implantation was successfully undertaken using a retro-auricular transmeatal approach.
  
  
  CONCLUSIONS
  SNHL is commonly encountered in patients with 3pDS and can be improved by cochlear implantation. In this patient population, particular attention must be given to pre-operative imaging and possible altered mastoid anatomy may exist. In doing so, intra-operative complications can be avoided.
authors.affiliation: Department of Otolaryngology - Head and Neck Surgery, Virginia Commonwealth University, Richmond, VA 23298-0146, USA. dcoelho@mcvh-vcu.edu
authors.forename: Daniel H
authors.initials: DH
authors.lastname: Coelho
authors.forename: Yula
authors.initials: Y
authors.lastname: Taormina
authors.forename: Jaime
authors.initials: J
authors.lastname: Moore
authors.forename: Kelley
authors.initials: K
authors.lastname: Dodson
authors.forename: Aristides
authors.initials: A
authors.lastname: Sismanis
mesh_terms: D002872:Chromosome Deletion; D002893:Chromosomes, Human, Pair 3 / Q000235:genetics; D019929:Cochlear Implantation / Q000379:methods*; D019465:Craniofacial Abnormalities / Q000000981:diagnostic imaging / Q000235:genetics*; D006312:Hearing Loss, Bilateral / Q000235:genetics / Q000601:surgery; D006319:Hearing Loss, Sensorineural / Q000235:genetics* / Q000601:surgery*; D006801:Humans; D007223:Infant; D008297:Male; D008416:Mastoid / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000601:surgery; D011859:Radiography