title: Craniofacial fibrous dysplasia (CFD) of the maxilla in an 11-year old boy: a case report.
abstract: We present the case of a surgically treated 11-year old boy with a diagnosis of craniomaxillofacial fibrous dysplasia (CFD) in the maxillary sinus. When first seen in the outpatient clinic of our department he had minimal symptoms. After initial radiological diagnostics by computed tomography scans (CT-scans) the patient was treated operatively by radical excision of the tumor. The radiographs showed the typical intramedullary located and well-defined lesions, which eroded the cortical bone with the typical appearance of fibrous dysplasia. The histopathology showed the typical curved extending fibrous trabeculae in C, O and Y-shape which were embedded in a moderately cellular morphologically inconspicuous stroma, confirming the initial suspicion of fibrous dysplasia of the maxillary bone. Cone beam tomography was a valuable tool in determining the re-ossification of bone at the affected side. Local resection can be curative in limited disease.
authors.affiliation: Department of Oral and Cranio-Maxillofacial Surgery, University Medical Center Hamburg Eppendorf, University of Hamburg, Martinistr. 52, 20246 Hamburg, Germany. a.assaf@uke.uni-hamburg.de
authors.forename: Alexandre T
authors.initials: AT
authors.lastname: Assaf
authors.forename: Andreas W
authors.initials: AW
authors.lastname: Benecke
authors.forename: Björn
authors.initials: B
authors.lastname: Riecke
authors.forename: Jozef
authors.initials: J
authors.lastname: Zustin
authors.forename: Andreas W
authors.initials: AW
authors.lastname: Fuhrmann
authors.forename: Max
authors.initials: M
authors.lastname: Heiland
authors.forename: Reinhard E
authors.initials: RE
authors.lastname: Friedrich
mesh_terms: D002648:Child; D054893:Cone-Beam Computed Tomography / Q000379:methods; D005357:Fibrous Dysplasia of Bone / Q000175:diagnosis* / Q000601:surgery; D005500:Follow-Up Studies; D006801:Humans; D008297:Male; D008439:Maxillary Diseases / Q000175:diagnosis* / Q000601:surgery; D008443:Maxillary Sinus / Q000473:pathology; D010012:Osteogenesis / Q000502:physiology; D014057:Tomography, X-Ray Computed / Q000379:methods