title: Bilateral adrenal EBV-associated smooth muscle tumors in a child with a natural killer cell deficiency.
abstract: EBV-associated smooth muscle tumors are found in immunocompromised patients, most commonly HIV/AIDS. We present a 12-year-old girl with the first documented case of EBV-related smooth muscle tumors in the presence of a rare classic NK cell deficiency. This sheds light on the role of NK cells in controlling EBV-related smooth muscle tumors.
authors.affiliation: Dalhousie Medical School, Dalhousie University, Halifax, Nova Scotia, Canada.
authors.forename: Rachel K
authors.initials: RK
authors.lastname: Shaw
authors.forename: Andrew C
authors.initials: AC
authors.lastname: Issekutz
authors.forename: Robert
authors.initials: R
authors.lastname: Fraser
authors.forename: Pierre
authors.initials: P
authors.lastname: Schmit
authors.forename: Barb
authors.initials: B
authors.lastname: Morash
authors.forename: Linda
authors.initials: L
authors.lastname: Monaco-Shawver
authors.forename: Jordan S
authors.initials: JS
authors.lastname: Orange
authors.forename: Conrad V
authors.initials: CV
authors.lastname: Fernandez
mesh_terms: D000311:Adrenal Glands / Q000473:pathology* / Q000821:virology; D002648:Child; D020031:Epstein-Barr Virus Infections / Q000276:immunology / Q000821:virology; D005260:Female; D004854:Herpesvirus 4, Human / Q000472:pathogenicity*; D006801:Humans; D016867:Immunocompromised Host; D007694:Killer Cells, Natural / Q000473:pathology*; D018235:Smooth Muscle Tumor / Q000473:pathology* / Q000821:virology