title: Uterus didelphys with unilateral distal vaginal agenesis and ipsilateral renal agenesis: common presentation of an unusual variation.
abstract: Mullerian duct abnormalities are congenital malformations that are easily missed and can lead to incorrect diagnosis and unnecessary operative procedures. In this case, a young female presented with cyclic pelvic pain that continued after previous surgical resection of an ovarian cyst. Further investigation with clinical examinations and multimodality imaging demonstrated ipsilateral renal agenesis and a Class III Mullerian duct anomaly (MDA) requiring a second operative procedure. It is believed that this case is a variant of the described obstructed hemi-vagina with ipsilateral renal agenesis (OVIRA) anomaly as pathologically there was ipsilateral renal agenesis and complete vaginal agenesis in our case. It is imperative to have a high clinical suspicion of mullerian duct abnormalities when encountering a patient with other urogenital anomalies. This will decrease the amount of misdiagnoses, guide appropriate surgical intervention, and decrease the risk of future reproductive complications.
authors.affiliation: Department of Radiology, Long Island College Hospital, 339 Hicks Street, Brooklyn, NY 11233, USA. ladair01@gmail.com
authors.forename: Luther
authors.initials: L
authors.lastname: Adair
authors.forename: Maria
authors.initials: M
authors.lastname: Georgiades
authors.forename: Rhonda
authors.initials: R
authors.lastname: Osborne
authors.forename: Tsz
authors.initials: T
authors.lastname: Ng
mesh_terms: D000015:Abnormalities, Multiple / Q000000981:diagnostic imaging*; D000293:Adolescent; D005260:Female; D006801:Humans; D007668:Kidney / Q000002:abnormalities*; D017699:Pelvic Pain / Q000209:etiology*; D014463:Ultrasonography; D014599:Uterus / Q000002:abnormalities* / Q000601:surgery; D014621:Vagina / Q000002:abnormalities* / Q000601:surgery