title: Magnetic resonance imaging in Hirayama disease.
abstract: Hirayama disease (HD) is a rare type of cervical myelopathy related to flexion of the neck characterized by progressive muscular weakness and atrophy of the distal upper limbs most frequently seen in young males. HD is thought to be secondary to an abnormal anterior displacement of the posterior dura with secondary compression of the lower cervical spinal cord and chronic injury to the anterior gray matter horns. We present two patients with HD and discuss its pathophysiology and imaging characteristics.
authors.affiliation: Department of Radiology, Fundacion Cardioinfantil - Instituto de Cardiología, Bogota, Colombia.
authors.forename: María Catalina
authors.initials: MC
authors.lastname: Vargas
authors.forename: Mauricio
authors.initials: M
authors.lastname: Castillo
mesh_terms: D000328:Adult; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D018908:Muscle Weakness / Q000209:etiology; D009133:Muscular Atrophy / Q000209:etiology; D009333:Neck / Q000473:pathology; D013116:Spinal Cord / Q000473:pathology; D014897:Spinal Muscular Atrophies of Childhood / Q000175:diagnosis*; D034941:Upper Extremity; D055815:Young Adult