title: Left coronary ostium isolation and aortic valve dysplasia in a young boy: a case report.
abstract: Congenital anomalies of the aortic valve represent a common malformation. Infrequently, a dysplastic aortic valve leaflet causes a severe coronary artery anomaly. Here, the case is reported of a malformed aortic valve in which the left rudimentary cusp occluded the left coronary ostium. At surgery the left coronary ostium was completely freed from the anomalous valvular tissue, a Konno operation was performed, and a 19 mm St. Jude Medical mechanical prosthesis was implanted. To date, very few reports have made of this rare malformation; moreover, to the present authors' knowledge this is the only case to have been treated.
authors.affiliation: Cardiac Surgery, Hesperia Hospital, Modena, Italy.
authors.forename: Filippo
authors.initials: F
authors.lastname: Benassi
authors.forename: Giuseppe
authors.initials: G
authors.lastname: DiBenedetto
authors.forename: Clorinda
authors.initials: C
authors.lastname: Labia
authors.forename: Guglielmo
authors.initials: G
authors.lastname: Stefanelli
mesh_terms: D001021:Aortic Valve / Q000002:abnormalities / Q000000981:diagnostic imaging / Q000503:physiopathology / Q000601:surgery*; D001022:Aortic Valve Insufficiency / Q000151:congenital / Q000175:diagnosis / Q000503:physiopathology / Q000601:surgery*; D001024:Aortic Valve Stenosis / Q000150:complications / Q000151:congenital / Q000175:diagnosis / Q000503:physiopathology / Q000601:surgery*; D001027:Aortography / Q000379:methods; D002675:Child, Preschool; D003097:Collateral Circulation; D003330:Coronary Vessel Anomalies / Q000175:diagnosis / Q000503:physiopathology / Q000601:surgery*; D004452:Echocardiography / Q000379:methods; D006350:Heart Valve Prosthesis / Q000009:adverse effects*; D019918:Heart Valve Prosthesis Implantation / Q000295:instrumentation / Q000379:methods; D006801:Humans; D017379:Hypertrophy, Left Ventricular / Q000175:diagnosis / Q000209:etiology; D008297:Male; D011182:Postoperative Care / Q000379:methods; D017755:Prosthesis Fitting / Q000295:instrumentation / Q000379:methods; D012086:Reoperation / Q000295:instrumentation / Q000379:methods; D013995:Time; D016896:Treatment Outcome