title: Type V aplasia cutis congenita: case report, review of the literature, and proposed treatment algorithm.
abstract: Aplasia cutis congenita (ACC) is the congenital absence of skin. There are a number of different classifications based on distribution and associated findings. Type V ACC is unique in that the lesions are typically symmetric and found primarily on the trunk but can also include the upper and lower extremities. Type V is associated with the loss of a monozygotic co-twin during the late first or early second trimester. Here we present an extensive case of type V ACC and a review of the literature, including a summary of treatment and outcomes. From the available literature, it appears that there is no benefit from early surgical intervention, and therefore we propose a treatment algorithm that starts with conservative management.
authors.affiliation: Division of NeonatologyDepartment of PediatricsDepartment of Pediatric Dermatology, Doernbecher Neonatal Care Center, Oregon Health and Science University, Portland, OregonCasey Eye Institute, Oregon Health and Science University, Portland, OregonDepartment of Pediatric Plastic and Reconstructive Surgery, Oregon Health and Science University, Portland, Oregon.
authors.forename: Daniel
authors.initials: D
authors.lastname: Morrow
authors.forename: Robert
authors.initials: R
authors.lastname: Schelonka
authors.forename: Alfons
authors.initials: A
authors.lastname: Krol
authors.forename: Michael
authors.initials: M
authors.lastname: Davies
authors.forename: Anna
authors.initials: A
authors.lastname: Kuang
mesh_terms: D000465:Algorithms; D004200:Diseases in Twins / Q000473:pathology* / Q000601:surgery* / Q000628:therapy; D004476:Ectodermal Dysplasia / Q000473:pathology* / Q000601:surgery* / Q000628:therapy; D005260:Female; D005313:Fetal Death; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D017592:Skin Care; D014430:Twins, Monozygotic