title: Large pulmonary artery aneurysm associated with Marfan syndrome.
abstract: Pulmonary artery aneurysms are rare, and published data on the subject are limited. The first case of Marfan syndrome associated with a large pulmonary artery aneurysm complicated by pulmonary artery thrombi and pulmonary hypertension is described. Serial echocardiograms showed progressive dilation of the aneurysm, which reached a massive size of 90 mm. Cardiac catheterization, pulmonary angiography and computed tomography angiography were used in the preoperative evaluation. The patient died suddenly while awaiting a decision for surgical intervention, thereby underscoring the need for aggressive management.
authors.affiliation: National Heart Centre, Singapore;
authors.forename: Peter
authors.initials: P
authors.lastname: Ting
authors.forename: Bodh I
authors.initials: BI
authors.lastname: Jugdutt
authors.forename: Ju
authors.initials: J
authors.lastname: Le Tan