title: Hypertrophic pachymeningitis and tracheobronchial stenosis in IgG4-related disease: case presentation and literature review.
abstract: Immunoglobulin G4 (IgG4)-related disease is a distinctive mass-forming disorder with frequent systemic involvement, most commonly in the pancreas, salivary glands and lacrimal glands. A few cases of dural involvement and one case of central airway stenosis have also been described. We report here a rare case of IgG4-related disease with intracranial hypertrophic pachymeningitis and irregular tracheobronchial stenosis. We review four previously reported cases of IgG4-related pachymeningitis. We currently lack international standards for the diagnosis of extrapancreatic IgG4-related disease. Based on the findings of the present case and those reported previously, we discuss the distinctive features of IgG4-related pachymeningitis.
authors.affiliation: Division of Rheumatic Diseases, National Center for Global Health and Medicine, Japan. hiroyuki_yjp2005@yahoo.co.jp
authors.forename: Hiroyuki
authors.initials: H
authors.lastname: Yamashita
authors.forename: Yuko
authors.initials: Y
authors.lastname: Takahashi
authors.forename: Hiroyuki
authors.initials: H
authors.lastname: Ishiura
authors.forename: Toshikazu
authors.initials: T
authors.lastname: Kano
authors.forename: Hiroshi
authors.initials: H
authors.lastname: Kaneko
authors.forename: Akio
authors.initials: A
authors.lastname: Mimori
mesh_terms: D000368:Aged; D001980:Bronchi / Q000473:pathology*; D003251:Constriction, Pathologic / Q000097:blood / Q000175:diagnosis; D006801:Humans; D006984:Hypertrophy / Q000097:blood / Q000175:diagnosis; D007074:Immunoglobulin G / Q000097:blood*; D008297:Male; D008581:Meningitis / Q000097:blood* / Q000175:diagnosis*; D014132:Trachea / Q000473:pathology*
chemical_list: D007074:Immunoglobulin G