title: Spontaneous aortic rupture in a patient with neurofibromatosis type 1.
abstract: Neurofibromatosis type I (NF-1) is a rare autosomal dominant genetic disorder occurring in 1 in 3,000 individuals. Vasculopathy is a rarely reported finding in patients with NF-1. Here, we report a case of recurrent aortic pseudoaneurysm after endovascular aneurysm repair in a 49-year-old male patient with NF-1. On the sixth postoperative day following a successful open surgical repair of an aortic pseudoaneurysm, he developed hemoperitoneum due to a delayed rupture of the mesenteric artery branch. This was treated with endovascular coil embolization. We report the clinical features and histologic findings of this rare vascular disorder with a review of the relevant literature.
authors.affiliation: Division of Vascular Surgery, Department of Surgery, Samsung Medical Center, Sungkyunkwan University School of Medicine, Seoul, Korea.
authors.forename: Yang Jin
authors.initials: YJ
authors.lastname: Park
authors.forename: Keun Myoung
authors.initials: KM
authors.lastname: Park
authors.forename: Jiyoung
authors.initials: J
authors.lastname: Oh
authors.forename: Hong Suk
authors.initials: HS
authors.lastname: Park
authors.forename: Jung-Sun
authors.initials: JS
authors.lastname: Kim
authors.forename: Young-Wook
authors.initials: YW
authors.lastname: Kim