title: Melanotic neuroectodermal tumor of infancy: case report and review of the literature.
abstract: Melanotic Neuroectodermal Tumor of Infancy (MNTI) is a rare but distinct neoplastic entity in infancy. Diagnosis is usually made before the age of 12 months. The common clinical presentation is a rapidly growing mass of the pre-maxillary area. Its surface is unevenly pigmented. To affirm the diagnosis a biopsy is necessary. Few cases of malignancy have been described (5% of cases). Adequate surgical excision is the treatment of choice. Recurrence rate is about 10 to 15% within 5 years. We report in this article the case of a newborn with MNTI illustrating that an R0 surgical excision can be correlated to a favourable prognosis. In this case the 5 years follow up didn't show any local or distant recurrence.
authors.affiliation: CHU-Lenval, Service d'ORL Pédiatrique des Hôpitaux Pédiatriques de Nice, 57 avenue de la Californie, 06200 Nice, France. camuzard.olivier@hotmail.fr
authors.forename: O
authors.initials: O
authors.lastname: Camuzard
authors.forename: O
authors.initials: O
authors.lastname: Rosello
authors.forename: C
authors.initials: C
authors.lastname: Maschi
authors.forename: L
authors.initials: L
authors.lastname: Castillo
authors.forename: A
authors.initials: A
authors.lastname: Deville
authors.forename: C
authors.initials: C
authors.lastname: Boyer
authors.forename: A
authors.initials: A
authors.lastname: Chevallier
authors.forename: S
authors.initials: S
authors.lastname: Bailleux
mesh_terms: D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D007223:Infant; D008441:Maxillary Neoplasms / Q000473:pathology* / Q000601:surgery*; D017600:Neuroectodermal Tumor, Melanotic / Q000473:pathology* / Q000601:surgery*; D016896:Treatment Outcome