title: Bicuspid pulmonary valve with atrial septal defect leading to pulmonary aneurysm.
abstract: Pulmonary artery aneurysms are rare. We describe 2 adult patients with pulmonary artery aneurysm with normal pulmonary pressure associated with bicuspid pulmonary valve and atrial septal defect. One patient presented with moderate pulmonary valve stenosis and was treated with open surgery; the other patient had a small atrial septal defect and mild pulmonary valve insufficiency and is periodically still being evaluated. Hemodynamic alterations associated with a pulmonary artery aneurysm are described; the influence of additional volume overload and intrinsic wall abnormalities in pulmonary valvular lesions as potential triggers for the development of these aneurysms are analyzed and therapeutic strategies are discussed.
authors.affiliation: Department of Cardiac Surgery, University Hospital Leuven, Leuven, Belgium. gogomotto@livedoor.com
authors.forename: Motohiko
authors.initials: M
authors.lastname: Goda
authors.forename: Werner
authors.initials: W
authors.lastname: Budts
authors.forename: Els
authors.initials: E
authors.lastname: Troost
authors.forename: Bart
authors.initials: B
authors.lastname: Meyns
mesh_terms: D000328:Adult; D000783:Aneurysm / Q000000981:diagnostic imaging / Q000209:etiology* / Q000601:surgery*; D000792:Angiography; D017548:Echocardiography, Transesophageal / Q000379:methods; D005260:Female; D005500:Follow-Up Studies; D006330:Heart Defects, Congenital / Q000150:complications / Q000175:diagnosis; D006344:Heart Septal Defects, Atrial / Q000150:complications* / Q000175:diagnosis / Q000601:surgery; D006801:Humans; D008297:Male; D008875:Middle Aged; D008943:Mitral Valve / Q000002:abnormalities* / Q000601:surgery; D011651:Pulmonary Artery / Q000000981:diagnostic imaging*; D011664:Pulmonary Valve / Q000002:abnormalities / Q000601:surgery; D011666:Pulmonary Valve Stenosis / Q000150:complications* / Q000175:diagnosis / Q000601:surgery; D018570:Risk Assessment; D013536:Suture Techniques; D016896:Treatment Outcome; D014656:Vascular Surgical Procedures / Q000379:methods