title: Repair of "simple" total anomalous pulmonary venous connection: a review from the Pediatric Cardiac Care Consortium.
abstract: BACKGROUND
  Outcomes for repair of total anomalous pulmonary venous connection (TAPVC) from individual institutions suggest a significant improvement in mortality over the past several decades. The purpose of this study is to review the outcomes after repair of TAPVC from a large multiinstitutional registry.
  
  
  METHODS
  A retrospective review of the multiinstitutional database, the Pediatric Cardiac Care Consortium (PCCC), was used to identify patients with the diagnosis of TAPVC who underwent complete correction between 1982 and 2007. Data reviewed included age, decade of primary operation, anatomic type, presentation, and in-hospital mortality.
  
  
  RESULTS
  Of the 118,084 surgical procedures submitted to the PCCC, 2,191 (1.9%) consisted of primary surgical correction of TAPVC. Sixty-one percent of the cohort was male, with 6.8% reported as premature. Overall in-hospital surgical mortality for simple TAPVC was 13%. Mortality was 20% from 1982 to 1989, 16% from 1990 to 1999, and 8% from 2000 to 2007. Obstruction to the anomalous pulmonary venous connection occurred in 29%, with a mortality of 26%.
  
  
  CONCLUSIONS
  Surgical outcomes from repair of congenital cardiac anomalies have significantly improved over the past several decades. Multiinstitutional large databases are needed to confirm results published from single-institution experiences. Although improvements in surgical repair of TAPVC have occurred over the past three decades, specific subtypes still experience significant mortality.
authors.affiliation: Division of Cardiothoracic Surgery, University of Minnesota, Minneapolis, Minnesota, USA. stlou012@umn.edu
authors.forename: James D
authors.initials: JD
authors.lastname: St Louis
authors.forename: Brian A
authors.initials: BA
authors.lastname: Harvey
authors.forename: Jeremiah S
authors.initials: JS
authors.lastname: Menk
authors.forename: Geetha
authors.initials: G
authors.lastname: Raghuveer
authors.forename: James E
authors.initials: JE
authors.lastname: O'Brien
authors.forename: Roosevelt
authors.initials: R
authors.lastname: Bryant
authors.forename: Lazaros
authors.initials: L
authors.lastname: Kochilas
mesh_terms: D000293:Adolescent; D002648:Child; D002675:Child, Preschool; D005260:Female; D017052:Hospital Mortality; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D008297:Male; D011667:Pulmonary Veins / Q000002:abnormalities* / Q000601:surgery*; D012189:Retrospective Studies