title: A rare case of left lung hypoplasia associated with congenital pulmonary artery aneurysm and ventricular septal defect.
abstract: This report describes a 3-year-old boy who presented with hemoptysis and a history of congenital heart disease detected at the age of 3 months. Clinical and laboratory evaluation showed a large true congenital pulmonary artery aneurysm of the left main pulmonary artery occupying the entire left hemithorax and two small aneurysms in the right lung. In addition, a restricted ventricular septal defect was detected. It was evident on clinical and histologic grounds that the multiple aneurysms seen in this child stemmed from congenital weakness of the arterial wall in conjunction with increased pulmonary blood flow and elevated pulmonary artery pressure.
authors.affiliation: Department of Cardiology, Nizam's Institute of Medical Sciences, Banjara Hill Road, Punjagutta, Hyderabad, 500082, India.
authors.forename: Amar N
authors.initials: AN
authors.lastname: Patnaik
authors.forename: Ramachandra
authors.initials: R
authors.lastname: Barik
authors.forename: Sagar
authors.initials: S
authors.lastname: Babu
authors.forename: A S
authors.initials: AS
authors.lastname: Gullati
mesh_terms: D000015:Abnormalities, Multiple / Q000175:diagnosis / Q000601:surgery*; D000783:Aneurysm / Q000151:congenital* / Q000000981:diagnostic imaging* / Q000601:surgery; D001707:Biopsy, Needle; D006328:Cardiac Catheterization / Q000379:methods; D006348:Cardiac Surgical Procedures / Q000379:methods; D002675:Child, Preschool; D003131:Combined Modality Therapy; D005500:Follow-Up Studies; D006345:Heart Septal Defects, Ventricular / Q000000981:diagnostic imaging*; D006469:Hemoptysis / Q000175:diagnosis / Q000209:etiology; D006801:Humans; D007150:Immunohistochemistry; D008168:Lung / Q000002:abnormalities* / Q000473:pathology; D018810:Magnetic Resonance Angiography / Q000379:methods; D008297:Male; D011651:Pulmonary Artery; D013902:Radiography, Thoracic / Q000379:methods; D035583:Rare Diseases; D014057:Tomography, X-Ray Computed / Q000379:methods; D016896:Treatment Outcome; D014463:Ultrasonography; D014656:Vascular Surgical Procedures / Q000379:methods