title: Aggressive angiomyxoma of the vulva in a patient with systemic lupus erythematosus.
abstract: Aggressive angiomyxoma is a rare, slow-growing mesenchymal neoplasm with a tendency to recur. It mainly involves the pelvis, vulva, perineum, vagina, and urinary bladder in adult women of reproductive age group. We describe a 26-year-old female with large swellings of both labia majora which was histologically diagnosed as aggressive angiomyxoma. She also had systemic lupus erythematosus. The swelling was surgically removed and she had no recurrence at 1-year follow-up. Although it is a rare tumor, it must be considered as a differential diagnosis for any mass in the perineum or soft tissue of the pelvis. Long-term follow-up is necessary for early diagnosis of local recurrence.
authors.affiliation: Department of Dermatology and Venereology, All India Institute of Medical Sciences, New Delhi, India.
authors.forename: P
authors.initials: P
authors.lastname: Pahwa
authors.forename: B K
authors.initials: BK
authors.lastname: Khaitan
authors.forename: A
authors.initials: A
authors.lastname: Rao
authors.forename: A
authors.initials: A
authors.lastname: Kriplani
authors.forename: R
authors.initials: R
authors.lastname: Mahey
authors.forename: K C
authors.initials: KC
authors.lastname: Subbarao
mesh_terms: D000328:Adult; D005076:Exanthema / Q000150:complications / Q000473:pathology; D005260:Female; D006801:Humans; D008180:Lupus Erythematosus, Systemic / Q000150:complications*; D009232:Myxoma / Q000150:complications* / Q000473:pathology* / Q000601:surgery; D012720:Severity of Illness Index; D014844:Vulva / Q000473:pathology*; D014846:Vulvar Neoplasms / Q000150:complications* / Q000473:pathology* / Q000601:surgery