title: Living-donor lobar lung transplantation for rapidly progressive interstitial pneumonia associated with clinically amyopathic dermatomyositis: report of a case.
abstract: Diffuse interstitial pneumonia (IP) associated with collagen disease is a rare indication for lung transplantation. The manifestations of collagen disease are variable and dermatomyositis (DM) is often considered a contraindication for lung transplantation because of active myositis and a high incidence of malignancy. Furthermore, clinically amyopathic dermatomyositis (C-ADM) is associated with rapidly progressive IP resulting in a poor prognosis. Bilateral living-donor lobar lung was transplanted in a 52-year-old female with rapidly progressive IP associated with C-ADM, and the postoperative course was uneventful. To our knowledge, this case represents the first living-donor lobar lung transplantation for a patient with rapidly progressive IP associated with C-ADM.
authors.affiliation: Department of Thoracic Surgery, Kyoto University, 54 Shogoin-Kawahara-cho, Sakyo-ku, Kyoto 606-8507, Japan. tshoji@kuhp.kyoto-u.ac.jp
authors.forename: Tsuyoshi
authors.initials: T
authors.lastname: Shoji
authors.forename: Toru
authors.initials: T
authors.lastname: Bando
authors.forename: Takuji
authors.initials: T
authors.lastname: Fujinaga
authors.forename: Fengshi
authors.initials: F
authors.lastname: Chen
authors.forename: Hajime
authors.initials: H
authors.lastname: Sasano
authors.forename: Naoichiro
authors.initials: N
authors.lastname: Yukawa
authors.forename: Tsuneyo
authors.initials: T
authors.lastname: Mimori
authors.forename: Hiroshi
authors.initials: H
authors.lastname: Date
mesh_terms: D000075202:Contraindications; D003882:Dermatomyositis / Q000150:complications*; D005260:Female; D006801:Humans; D019520:Living Donors; D017563:Lung Diseases, Interstitial / Q000150:complications / Q000601:surgery*; D016040:Lung Transplantation / Q000379:methods*; D008875:Middle Aged; D035781:Siblings