title: Type 2 Abernethy malformation presenting as a portal vein-coronary sinus fistula.
abstract: We report the case of a child with Abernethy malformation with an anomalous connection between the portal vein and the coronary sinus. After 30 months of close follow-up, the patient developed hepatoblastoma, a previously documented complication of the Abernethy malformation. This case reports a unique variant of Abernethy malformation and documents the first reported case of hepatoblastoma in a patient with type 2 Abernethy malformation.
authors.affiliation: Children's Hospital of Wisconsin/Herma Heart Center, Milwaukee, WI 53226, USA. Rloomba@mcw.edu
authors.forename: Rohit S
authors.initials: RS
authors.lastname: Loomba
authors.forename: Grzegorz W
authors.initials: GW
authors.lastname: Telega
authors.forename: Todd M
authors.initials: TM
authors.lastname: Gudausky
mesh_terms: D002675:Child, Preschool; D054326:Coronary Sinus / Q000002:abnormalities*; D004200:Diseases in Twins / Q000150:complications / Q000151:congenital / Q000175:diagnosis*; D017809:Fatal Outcome; D018197:Hepatoblastoma / Q000175:diagnosis* / Q000209:etiology; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D008113:Liver Neoplasms / Q000175:diagnosis* / Q000209:etiology; D008297:Male; D011169:Portal Vein / Q000002:abnormalities*; D016157:Vascular Fistula / Q000150:complications / Q000151:congenital / Q000175:diagnosis*