title: Congenital ossicular chain anomalies associated with a mobile stapes footplate: surgical results for 23 ears.
abstract: OBJECTIVE
  We describe the audiometric results following surgery in a consecutive series of patients with a congenital ossicular middle ear disorder that was associated with a mobile stapes footplate.
  
  
  METHODS
  We performed a retrospective analysis of patient charts from a tertiary referral center. A total of 23 patients (23 ears) underwent exploratory tympanotomy and ossicular reconstruction between 1986 and 2001. The main outcome measure was the audiometric results.
  
  
  RESULTS
  Overall, we observed a mean gain in air conduction pure tone average of 17 dB (from 47 dB to 30 dB), a sensorineural deterioration of 3 dB, and a mean postoperative air-bone gap of 19 dB (mean preoperative air-bone gap of 38 dB). The air-bone gap closure was 20 dB or less in 15 of the 23 cases (65%), in agreement with the few results reported in the literature. Moreover, the audiometric results remained stable. In the syndromic group, the mean gain in air conduction was only 13 dB, which was worse than that observed for the nonsyndromic ears.
  
  
  CONCLUSIONS
  Surgery for congenital ossicular chain anomalies with a concomitant mobile stapes footplate provides positive audiometric outcomes. Most ears had some sensorineural impairment (10 to 20 dB), which influenced the final hearing level attained after surgery. Preoperative assessment is mandatory to search for syndromal diagnoses, which might be important for patient counseling and prognosis.
authors.affiliation: Department of Otorhinolaryngology, Donders Institute for Neuroscience, Nijmegen, the Netherlands.
authors.forename: Henricus G X M
authors.initials: HG
authors.lastname: Thomeer
authors.forename: Henricus P M
authors.initials: HP
authors.lastname: Kunst
authors.forename: Cor W R J
authors.initials: CW
authors.lastname: Cremers
mesh_terms: D000293:Adolescent; D000328:Adult; D001301:Audiometry, Pure-Tone; D001309:Auditory Threshold; D001844:Bone Conduction; D002648:Child; D004429:Ear Ossicles / Q000002:abnormalities* / Q000601:surgery*; D005260:Female; D006319:Hearing Loss, Sensorineural / Q000601:surgery; D006801:Humans; D008297:Male; D008875:Middle Aged; D012189:Retrospective Studies; D013199:Stapes / Q000002:abnormalities*; D013200:Stapes Mobilization; D055815:Young Adult