title: Staged repair of pentalogy of Cantrell with ectopia cordis and ventricular septal defect.
abstract: Pentalogy of Cantrell is a rare congenital anomaly characterized by a combination of severe defects in the middle of the chest and abdomen including intracardiac defects. Survival rate after cardiac surgery is extremely low. We present a successful staged complete repair of an omphalocele, a ventricular septal defect and a sternal defect in a case of pentalogy of Cantrell.
authors.affiliation: Division of Pediatric Cardiac Surgery and Cardiology, University of Tsukuba, Tsukuba, Japan.
authors.forename: Yoshie
authors.initials: Y
authors.lastname: Sakasai
authors.forename: Bui Quoc
authors.initials: BQ
authors.lastname: Thang
authors.forename: Shinya
authors.initials: S
authors.lastname: Kanemoto
authors.forename: Miho
authors.initials: M
authors.lastname: Takahashi-Igari
authors.forename: Shinji
authors.initials: S
authors.lastname: Togashi
authors.forename: Hideyuki
authors.initials: H
authors.lastname: Kato
authors.forename: Yuji
authors.initials: Y
authors.lastname: Hiramatsu
mesh_terms: D002675:Child, Preschool; D054083:Ectopia Cordis / Q000175:diagnosis / Q000601:surgery*; D006345:Heart Septal Defects, Ventricular / Q000000981:diagnostic imaging / Q000601:surgery*; D006554:Hernia, Umbilical / Q000175:diagnosis / Q000601:surgery*; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D008297:Male; D058502:Pentalogy of Cantrell / Q000175:diagnosis / Q000601:surgery*; D013249:Sternum / Q000002:abnormalities / Q000601:surgery*; D014463:Ultrasonography