title: Atypical presentation of geniculate ganglion venous malformation in a child: conductive hearing loss without facial weakness.
abstract: We describe an unusual presentation of geniculate ganglion venous malformation, a rare facial nerve lesion, emphasizing the importance of the differential diagnosis, imaging characteristics, and controversies in management. A child presented with moderate right-sided conductive hearing loss and a House-Brackmann grade I facial nerve function bilaterally. Computed tomography and magnetic resonance imaging showed a mass demonstrating features consistent with a geniculate ganglion venous malformation. To our knowledge, this is the first pediatric case of geniculate ganglion venous malformation presenting solely with conductive hearing loss. Proper management requires differentiating this condition from other geniculate and temporal bone lesions.
authors.affiliation: Alfred I. duPont Hospital for Children, Wilmington, DE 19899, USA.
authors.forename: Julie A
authors.initials: JA
authors.lastname: Ames
authors.forename: Jessica R
authors.initials: JR
authors.lastname: Levi
authors.forename: Douglas R
authors.initials: DR
authors.lastname: Johnston
authors.forename: Colin A
authors.initials: CA
authors.lastname: Drake
authors.forename: Thomas O
authors.initials: TO
authors.lastname: Willcox
authors.forename: Robert C
authors.initials: RC
authors.lastname: O'Reilly
mesh_terms: D002648:Child; D005830:Geniculate Ganglion / Q000098:blood supply* / Q000000981:diagnostic imaging; D006314:Hearing Loss, Conductive / Q000209:etiology*; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D014057:Tomography, X-Ray Computed; D054079:Vascular Malformations / Q000150:complications / Q000175:diagnosis*; D014680:Veins