Torsade de pointes in Kearns-Sayre syndrome.
A 47-year-old woman with Kearns-Sayre syndrome (KSS) and an implanted pacemaker for complete heart block was admitted to the intensive care unit following a cardiac arrest due to ventricular tachycardia (torsade de pointes) in the setting of QT prolongation. Complete heart blocks and ventricular tachycardia are implicated as mechanisms of sudden deaths in KSS; such patients may require pacemaker implantation and implantation of an automatic implantable cardioverter-defibrillator.
Department of Intensive Care, Brugmann University Hospital, Brussels, Belgium.
Stéphan
S
Wilmin
David
D
De Bels
Sebastien
S
Knecht
Philippe
P
Gottignies
Marie-Dominique
MD
Gazagnes
Jacques
J
Devriendt
D005260:Female; D006801:Humans; D007625:Kearns-Sayre Syndrome / Q000150:complications* / Q000175:diagnosis*; D008875:Middle Aged; D016171:Torsades de Pointes / Q000150:complications* / Q000175:diagnosis*