Type A quadricuspid aortic valve and ascending aorta aneurysm: a rare combination.
Quadricuspid aortic valve (QAV) is a rare congenital anomaly associated with aortic valve insufficiency and significant morbidity, and requires the replacement or, rarely, the repair of the malfunctioning heart valve. A QAV associated with an ascending aorta aneurysm is an extremely rare anatomic combination with a hypothetical, but not clear, shared embryological etiology. To date, only two cases of type B QAV with ascending aorta aneurysm have been reported. Herein is described the first ever case of a 38-year-old male suffering from severe symptomatic aortic valve regurgitation due to a type A QAV, associated with an ascending aorta aneurism, who underwent a successful combined replacement of the aortic valve and ascending aorta.
Department of Cardio-vascular Surgery, University Hospital of Lausanne (CHUV), CH-1011, Lausanne, Switzerland.
Enrico
E
Ferrari
Carlo
C
Marcucci
Aurelien
A
Roumy
Ludwig Karl
LK
von Segesser
D000328:Adult; D001014:Aortic Aneurysm / Q000150:complications*; D001021:Aortic Valve / Q000002:abnormalities*; D001022:Aortic Valve Insufficiency / Q000209:etiology*; D006801:Humans; D008297:Male