General anaesthesia in an adult patient with Morquio syndrom with emphasis on airway issues.
Patients with Morquio syndrome possess a number of characteristics which may complicate an anaesthetic procedure. The most important is that a deposition of mucopolysaccharides in the soft tissues of the oro-pharynx distorts the airway, making the airway management difficult, while the atlanto-axial instability puts these patients at risk of subluxation and quadriparesis. As the endotracheal intubation in Morquio syndrome patients may be difficult or even impossible, we recommend the technique of awake fiberoptic intubation to be considered. Our approach to awake fiberoptic intubation in an adult patient is described in this case report.
Department of Anesthesiology, Radboud University Nijmegen Medical, Centre, Huispost 630, route 633, Postbus 9101, 6500 HB Nijmegen, The Netherlands. L.Kadic@anes.umcn.nl
Lajla
L
Kadic
Jacques J
JJ
Driessen
D000328:Adult; D058109:Airway Management / Q000379:methods*; D000768:Anesthesia, General / Q000379:methods*; D019644:Arthroplasty, Replacement, Hip; D001268:Atlanto-Axial Joint / Q000502:physiology; D005336:Fiber Optic Technology; D006801:Humans; D007442:Intubation, Intratracheal; D007593:Joint Instability / Q000150:complications; D008297:Male; D009055:Mouth / Q000000981:diagnostic imaging; D009085:Mucopolysaccharidosis IV / Q000150:complications* / Q000000981:diagnostic imaging; D009960:Oropharynx / Q000000981:diagnostic imaging / Q000502:physiology; D011229:Preanesthetic Medication; D011859:Radiography; D013131:Spine / Q000000981:diagnostic imaging