Massive avascular malformations causing life threatening portal hypertension.
We present an unusual case of extensive avascular malformations (AVMs) causing non-cirrhotic portal hypertension. This phenomenon, though previously described, is a rare clinical entity which, in the setting of life threatening portal hypertension, may require vascular decompression either by surgery or a transjugular intrahepatic portosystemic shunt.
Department of Medicine, Western University, London, Ontario, Canada.
Aman
A
Arya
Nirmal
N
Kakani
Nabil
N
Hussain
Natasha
N
Chandok
D000005:Abdomen / Q000098:blood supply*; D000328:Adult; D001165:Arteriovenous Malformations / Q000150:complications* / Q000175:diagnosis / Q000503:physiopathology / Q000601:surgery; D019299:Decompression, Surgical; D004932:Esophageal and Gastric Varices / Q000209:etiology; D005260:Female; D006471:Gastrointestinal Hemorrhage / Q000209:etiology; D006801:Humans; D006975:Hypertension, Portal / Q000175:diagnosis / Q000209:etiology* / Q000503:physiopathology / Q000601:surgery; D010388:Pelvis / Q000098:blood supply*; D017082:Portal Pressure; D019168:Portasystemic Shunt, Transjugular Intrahepatic; D014057:Tomography, X-Ray Computed