[Alertness is its own reward: adult type Hirschprung's disease--clinical description of first two cases in Israel].
Hirschprung disease is well known. The basic pathogenesis is lack of parasympathetic ganglia in the large bowel wall, part of it, or all of it. The absence of these ganglia paralyzes the involved segment leading to obstruction. Almost all babies are diagnosed and operated upon in their first year. Few rare cases manage to grow and reach maturity without diagnosis. These patients are characterized by severe constipation and grade III-IV hemorrhoids. This is adult type Hirschprung's disease. Two first cases in Israel were diagnosed, patients were operated upon, and recovered. Adult type Hirschprung's disease is reviewed and various surgical options are discussed.
Department of Surgery, Elisha Hospital, Haifa.
Samuel
S
Argov
Olga
O
Levandovsky
Hedviga
H
Kerner
Ofer
O
Ben-Yizhak
Uriel
U
Klinehouse
Ptahia
P
Reissman
D000293:Adolescent; D000328:Adult; D000367:Age Factors; D003248:Constipation / Q000209:etiology*; D005260:Female; D005726:Ganglia, Parasympathetic / Q000378:metabolism; D006484:Hemorrhoids / Q000209:etiology*; D006627:Hirschsprung Disease / Q000175:diagnosis* / Q000503:physiopathology / Q000601:surgery; D006801:Humans; D007557:Israel; D008297:Male