Herlyn-Werner-Wunderlich syndrome: a rare cause of pelvic pain in adolescent girls.
The Herlyn-Werner-Wunderlich syndrome is a rare congenital anomaly characterised by uterus didelphys with blind hemivagina and ipsilateral renal agenesis. It usually presents after menarche with progressive pelvic pain during menses secondary to haematocolpos. Awareness is necessary in order to diagnose and treat this disorder properly before complications occur. MRI is the preferred modality for the delineation of uterine malformation. When renal anomalies are encountered, a screening should also be made for congenital abnormalities of the reproductive tract and vice versa. The authors report a case of a girl with this condition who had a prenatal diagnose of right renal agenesis and presented at 13 years old with pelvic pain caused by haematocolpos.
Paediatrics, Hospital Central Funchal, Funchal, Portugal. anac.aveiro@gmail.com
Ana Cristina
AC
Aveiro
Victor
V
Miranda
António Jorge
AJ
Cabral
Sidónia
S
Nunes
Filomeno
F
Paulo
Conceição
C
Freitas
D000015:Abnormalities, Multiple / Q000175:diagnosis*; D000293:Adolescent; D003937:Diagnosis, Differential; D003952:Diagnostic Imaging; D005260:Female; D006801:Humans; D007668:Kidney / Q000002:abnormalities*; D009095:Mullerian Ducts / Q000002:abnormalities*; D017699:Pelvic Pain / Q000209:etiology*; D013577:Syndrome; D014599:Uterus / Q000002:abnormalities*; D014621:Vagina / Q000002:abnormalities* / Q000601:surgery