Aneurysmal subarachnoid haemorrhage in Parry-Rhomberg syndrome.
Parry-Romberg syndrome (PRS) or progressive hemi facial atrophy syndrome is a rare condition of unknown aetiology that is characterised by progressive unilateral facial and cranial atrophic changes of skin, subcutaneous tissues and bone. The authors describe a 37-year-old female with a history of PRS, who presented with a subarachnoid haemorrhage secondary to rupture of a 9 mm fusiform aneurysm of the posterior cerebral artery. There was an associated external carotid arterio-venous fistula noted with this aneurysm. The aneurysm was treated by endovascular route and was successfully coiled. Follow-up angiogram revealed spontaneous resolution of the fistula with good occlusion of the aneurysm. The aetio-pathogenesis of this rare occurrence, literature review and its management is discussed.
Department of Neurosurgery, Cork University Hospital, Cork, Ireland.
Derek
D
Kuechler
Chandrasekaran
C
Kaliaperumal
Alfrazdaq
A
Hassan
Noel
N
Fanning
Gerry
G
Wyse
Michael
M
O'Sullivan
D000328:Adult; D017542:Aneurysm, Ruptured / Q000150:complications* / Q000601:surgery; D057510:Endovascular Procedures; D005150:Facial Hemiatrophy / Q000150:complications*; D005260:Female; D006801:Humans; D020769:Posterior Cerebral Artery / Q000601:surgery; D012422:Rupture, Spontaneous / Q000150:complications / Q000601:surgery; D013345:Subarachnoid Hemorrhage / Q000209:etiology* / Q000601:surgery