[Spontaneous pneumothorax and Recklinghausen's disease: a case report].
The Von Recklinghausen disease is a genetic hereditary neurofibromatosis. It causes neurofibroma, axillary and inguinal lentigines, and café-au-lait spots in the skin. It may affect the lung in 5 to 20% of cases, causing neurofibroma, infiltrative and cystic lesions, emphysematous or bubble injury leading to a chronic respiratory failure. The risk of pneumothorax in theses cases seems higher. Few reviews reported the pulmonary manifestations in the Recklinghausen disease and specially the pneumothorax as a complication while the direct relation between this neurofibromatosis and the lung disease is not clearly established yet. We report a case report of spontaneous pneumothorax with slow evolution complicating the course of a patient with Recklinghausen disease.
Service de réanimation médicale, EPS Taher Sfar, 5100 Mahdia, Tunisie.
S
S
Ayed Della
A
A
Kotti
H
H
Ben Sik Ali
S
S
Ayed
M
M
Fekih Hassen
S
S
Elatrous
D005260:Female; D006801:Humans; D008168:Lung / Q000000981:diagnostic imaging / Q000473:pathology; D008875:Middle Aged; D009456:Neurofibromatosis 1 / Q000150:complications*; D011030:Pneumothorax / Q000175:diagnosis / Q000209:etiology*; D011859:Radiography