Hemihydranencephaly: rare disease with key to secrets of the brain.
A 21-year-old male presented to us in status epilepticus. On investigation, he was found to have an extremely rare disorder called 'hemihydranencephaly'. Review of literature revealed that hemihydranencephaly was not always incompatible with life and that research into this disorder would help in understanding the development, functioning, untapped potential and reorganisation capacity of the brain.
Department of Medicine, KMC, Manipal, Karnataka, India.
Lorraine S
LS
Dias
K N
KN
Shivashankara
G
G
Vivek
D006801:Humans; D006832:Hydranencephaly / Q000150:complications / Q000175:diagnosis*; D008279:Magnetic Resonance Imaging; D008297:Male; D013226:Status Epilepticus / Q000209:etiology*; D055815:Young Adult