Biliary duplication cyst with heterotopic gastric mucosa resulting in obstruction of the biliary system: a case report.
Biliary tract duplication cysts with heterotopic gastric mucosa are rare congenital anomalies, with our case representing only the fourth reported case in the literature. An 8-year-old girl with several months of abdominal pain was found to have a complex cystic mass communicating with the biliary system via the common hepatic duct. Intraoperatively, inflammation caused by the cystic mass was found to have resulted in a Mirizzi-like syndrome, with a nearly complete obstruction at the confluence of the left and right hepatic ducts. Histopathologic examination of the biliary mass revealed it to be a duplication cyst lined by heterotopic gastric mucosa with secondary ulceration and fibrosis. Biliary duplication cysts are a rare but important process that should be considered in a child with a mass in the portal triad and biliary obstruction.
Section of Pediatric Surgery, C.S. Mott Children's Hospital, University of Michigan, Ann Arbor, MI 48109-5245, USA.
Jina
J
Kim
Marcus D
MD
Jarboe
Meghan A
MA
Arnold
Michael A
MA
DiPietro
David A
DA
Bloom
Daniel H
DH
Teitelbaum
D015746:Abdominal Pain / Q000209:etiology; D000713:Anastomosis, Roux-en-Y; D001649:Bile Duct Diseases / Q000209:etiology; D002648:Child; D002758:Cholangiography; D002760:Cholangiopancreatography, Endoscopic Retrograde; D015529:Choledochal Cyst / Q000150:complications / Q000000981:diagnostic imaging / Q000601:surgery*; D002779:Cholestasis / Q000209:etiology* / Q000601:surgery; D002828:Choristoma; D004108:Dilatation, Pathologic / Q000209:etiology; D005260:Female; D005753:Gastric Mucosa; D006500:Hepatic Duct, Common / Q000002:abnormalities; D006801:Humans; D006932:Hyperbilirubinemia / Q000209:etiology; D007583:Jejunum / Q000601:surgery; D008099:Liver / Q000601:surgery; D015641:Radiography, Interventional; D014456:Ulcer / Q000209:etiology