Case of progressive facial hemiatrophy with cervical sympathetic hyperactivity as underlying aetiology.
OBJECTIVE
We report a case of progressive facial hemiatrophy with cervical sympathetic hyperactivity as a possible underlying aetiology, based on clinical findings, three-dimensional computed tomography and thermographic imaging.


METHODS
We present a case report in which we describe the investigation and clinical course of progressive facial hemiatrophy, and we also review the world literature on this condition.


RESULTS
To our knowledge, this is the first report in the world literature of progressive facial hemiatrophy with cervical sympathetic hyperactivity indicated as a possible underlying aetiology, based on clinical findings, three-dimensional computed tomography and thermographic imaging.


CONCLUSIONS
This syndrome may lead to atrophy of the subcutaneous adipose tissue with hyperfunction of the vegetative system. Although this is a rare syndrome, otolaryngologists should be aware of its symptoms, aetiology and treatment.
Department of Otolaryngology, Hitachi General Hospital, Ibaraki, Japan. h-monobe@chime.ocn.ne.jp
H
H
Monobe
K
K
Miyano
R
R
Kagoya
H
H
Tojima
D000368:Aged; D001831:Body Temperature / Q000502:physiology; D001862:Bone Resorption / Q000000981:diagnostic imaging / Q000209:etiology; D018450:Disease Progression; D005150:Facial Hemiatrophy / Q000175:diagnosis / Q000209:etiology* / Q000628:therapy; D005260:Female; D006801:Humans; D006945:Hyperhidrosis / Q000175:diagnosis / Q000209:etiology; D007259:Infrared Rays / Q000627:therapeutic use; D008336:Mandibular Diseases / Q000000981:diagnostic imaging* / Q000473:pathology; D010789:Phototherapy / Q000295:instrumentation / Q000379:methods*; D011859:Radiography; D013233:Stellate Ganglion; D013564:Sympathetic Nervous System / Q000503:physiopathology*; D013817:Thermography; D016896:Treatment Outcome