Ruptured inferior mesenteric artery aneurysm in a patient with a type 1 neurofibromatosis.
We describe the case of a 61-year-old woman having a type 1 neurofibromatosis (von Recklinghausen disease), whose acute abdominal pain revealed a voluminous retroperitoneal hemorrhage caused by a 25-mm ruptured inferior mesenteric artery aneurysm. She underwent emergent aneurysm and left colonic resection. This report of a rare digestive artery aneurysm rupture, which added to increasing reports of vascular abnormalities in type 1 neurofibromatosis patients, underlines the need to maintain a high suspicion index of a vascular etiology in case of any abdominal complaint in these patients.
General and Visceral Surgery Department, Saint Antoine Hospital, St. Antoine, Paris, France.
Laure
L
Kerger
Andre
A
Tomescot
Najim
N
Chafai
D015746:Abdominal Pain / Q000209:etiology; D059787:Acute Pain / Q000209:etiology; D017542:Aneurysm, Ruptured / Q000000981:diagnostic imaging / Q000209:etiology* / Q000601:surgery; D003082:Colectomy; D005260:Female; D006470:Hemorrhage / Q000209:etiology; D006801:Humans; D059325:Intra-Abdominal Hypertension / Q000209:etiology; D017537:Mesenteric Artery, Inferior / Q000000981:diagnostic imaging / Q000601:surgery; D008875:Middle Aged; D009456:Neurofibromatosis 1 / Q000150:complications* / Q000175:diagnosis; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome; D014656:Vascular Surgical Procedures