Oral rehabilitation of children with ectodermal dysplasia.
The aim of this study was to describe the clinical treatment of young patients, affected by ectodermal dysplasia (ED), and to possibly establish clinical guidelines. The study design was case series. ED syndromes (EDs) are a heterogeneous group of inherited diseases characterised by abnormal development of tissues of ectodermal origin. The most common form of EDs is X linked hypohidrotic ED (HED). Characteristic triad of HED is oligo-anodontia, hypotricosis, hypo-anhydrosis. Oligo-anodontia is one of the most severe impairment, since it affects chewing, swallowing, speech, esthetics and social relation. Early prosthetic rehabilitation (at 2-3 years of age), with partial or complete dentures, is essential to improve oral function and reduce the social impairment.
Unit of Dentistry for Disables Department of Oral Science, Alma Mater Studiorum, University of Bologna, Bologna, Italy.
Marco
M
Montanari
Michele
M
Callea
Filippo
F
Battelli
Gabriela
G
Piana
D002648:Child; D002675:Child, Preschool; D003824:Denture, Complete; D003829:Denture, Partial; D053358:Ectodermal Dysplasia 1, Anhidrotic / Q000503:physiopathology / Q000534:rehabilitation*; D004955:Esthetics, Dental; D006801:Humans; D008297:Male; D008409:Mastication; D013060:Speech