Extracorporeal membrane oxygenation support of a severe metabolic crisis in a child with methylmalonic acidemia.
A 9-year-old female, with mut phenotype of methylmalonic acidemia who developed severe vasoplegic shock during a metabolic crisis, was successfully supported with venoarterial extracorporeal membrane oxygenation.
Department of Critical Care, Texas Children's Hospital, Houston, 77030, USA.
Ryan J
RJ
Stark
Bindi J
BJ
Naik-Mathuria
Fong W
FW
Lam
Oluyinka O
OO
Olutoye
V Reid
VR
Sutton
Lara S
LS
Shekerdemian
D000592:Amino Acid Metabolism, Inborn Errors / Q000235:genetics* / Q000473:pathology*; D002648:Child; D015199:Extracorporeal Membrane Oxygenation; D005260:Female; D006801:Humans; D008764:Methylmalonic Acid / Q000378:metabolism; D010641:Phenotype; D012131:Respiratory Insufficiency / Q000209:etiology; D016896:Treatment Outcome; D056987:Vasoplegia / Q000209:etiology
D008764:Methylmalonic Acid