Dental anomalies in Richieri-Costa-Pereira syndrome.
OBJECTIVE
The objective of this study was to investigate the prevalence of dental anomalies in individuals with Richieri-Costa-Pereira syndrome.


METHODS
A total of 13 individuals with Richieri-Costa-Pereira syndrome who were older than 8 years with at least 1 available panoramic radiograph were assessed. Dental anomalies were evaluated clinically and radiographically and classified as hyperplastic, hypoplastic, or heterotopic and as alterations of shape, number, position, and structure. Enamel alterations were classified by the DDE index.


RESULTS
All individuals exhibited anomalies, with predominance of hypoplastic disorders, mainly agenesis of mandibular incisors and second premolars and demarcated creamy-white enamel opacities primarily affecting the maxillary premolars.


CONCLUSIONS
Individuals with Richieri-Costa Pereira syndrome exhibit high prevalence of tooth agenesis, especially mandibular incisors and premolars, as well as high frequency of enamel opacities. These findings are compatible with the mandibular cleft observed in all individuals and also reflect the hypoplastic characteristic of the syndrome.
Hospital for Rehabilitation of Craniofacial Anomalies, University of São Paulo, Bauru, Brazil.
Janete Mary Baaclini Galante
JM
Severini
Gisele
G
da Silva Dalben
Antonio
A
Richieri-Costa
Terumi Okada
TO
Ozawa
D000293:Adolescent; D000328:Adult; D002648:Child; D003025:Clubfoot / Q000150:complications*; D005260:Female; D006228:Hand Deformities, Congenital / Q000150:complications*; D006801:Humans; D008297:Male; D010855:Pierre Robin Syndrome / Q000150:complications*; D011862:Radiography, Panoramic; D014071:Tooth Abnormalities / Q000175:diagnosis*