Prenatal diagnosis of long QT syndrome: implications for delivery room and neonatal management.
This case describes the prenatal diagnosis and integrated peripartum management of a foetus with 2:1 atrioventricular block and torsade de pointes due to congenital long QT syndrome. The unique issues related to the detection of intrauterine conduction abnormalities and ventricular arrhythmias, along with the immediate postnatal care, have been described as an interesting teaching case with successful outcome.
Division of Cardiology, Children's National Medical Center, Washington, DC 20010, USA.
E Anne
EA
Greene
Charles I
CI
Berul
Mary T
MT
Donofrio
D054537:Atrioventricular Block / Q000209:etiology*; D015150:Echocardiography, Doppler; D005260:Female; D006340:Heart Rate, Fetal; D006801:Humans; D007231:Infant, Newborn; D008133:Long QT Syndrome / Q000150:complications / Q000151:congenital* / Q000628:therapy; D018743:Perinatal Care / Q000379:methods*; D058725:Peripartum Period; D011247:Pregnancy; D011296:Prenatal Diagnosis; D016171:Torsades de Pointes / Q000209:etiology*; D016216:Ultrasonography, Prenatal