Total right pulmonary venous return to the inferior vena cava: a rare variant of Scimitar syndrome.
Scimitar syndrome is a rare congenital disorder characterized by a partial, or rarely total, unilateral anomalous pulmonary venous return to the inferior vena cava. This anomaly has a distinctive bimodal presentation with the infantile form having a higher incidence, severity and mortality than the adult form, which is usually asymptomatic on diagnosis. We present the case of a 36-year-old-male transferred to our institution due to incidental anomalous vascular findings on contrast enhanced chest tomography while being evaluated for dyspnea on exertion. Patient underwent right and left heart catheterization with evidence of left-to-right shunt secondary to complete anomalous right pulmonary venous return. Patient was referred to a cardiovascular surgeon with expertise in congenital heart disease for definitive surgical correction.
Cardiology Section, University of Puerto Rico School of Medicine Internal Medicine Department, San Juan. rmarmorato@gmail.com
Rossella
R
Marmorato-Rivera
Hector
H
Banchs-Pieretti
Francisco
F
Parrilla-Quinones
Pablo
P
Altieri-Nieto
Enrique
E
Carrion
Cid
C
Quintana-Rodríguez
Jose
J
Maldonado-Vargas
D006801:Humans; D033162:Incidental Findings; D011667:Pulmonary Veins; D012587:Scimitar Syndrome; D013909:Thorax; D014682:Vena Cava, Inferior