Phacomatosis melanorosea without extracutaneous features: an unusual type of phacomatosis pigmentovascularis.
Phacomatosis pigmentovascularis (PPV) represents a group of different types of didymosis (twin spotting) characterized by the coexistence of a large pigmentary nevus such as a mongolian spot, café-au-lait macule or macular nevus spilus, and an extensive telangiectatic nevus, such as nevus flammeus or nevus roseus. We describe a third case of phacomatosis melanorosea and discuss the denotation of this neologism.
Freiburg University Medical Center, Department of Dermatology, Hauptstrasse 7, 79104 Freiburg, Germany. aarnold@uhbs.ch
Andreas W
AW
Arnold
Marion U
MU
Kleine
Rudolf
R
Happle
D002675:Child, Preschool; D005260:Female; D006801:Humans; D020752:Neurocutaneous Syndromes / Q000145:classification / Q000473:pathology*