Effect of a physical exercise program in a patient with Marfan syndrome and ventricular dysfunction.
Marfan syndrome (MS) is an autosomal dominant disorder that affects multiple organs and systems. Several cardiac alterations are present, with the main ones being aortic root and ascending aorta dilatation, mitral valve prolapse and left ventricle (LV) dilatation. Aerobic exercise has not shown to be a non-drug therapy that promotes anti-remodeling effect in patients with heart failure. This case report describes the echocardiographic changes in a patient with Marfan syndrome during four years of cardiovascular physical therapy.
Universidade Federal de São Paulo - UNIFESP, São Paulo, SP, Brazil. wmusettimedeiros@hotmail.com
Wladimir Musetti
WM
Medeiros
Paulo Alberto
PA
Peres
Antônio Carlos
AC
Carvalho
Carlos
C
Gun
Fábio Augusto
FA
De Luca
D000328:Adult; D015150:Echocardiography, Doppler; D015444:Exercise / Q000502:physiology; D005081:Exercise Therapy; D005240:Feasibility Studies; D006801:Humans; D008297:Male; D008382:Marfan Syndrome / Q000503:physiopathology / Q000628:therapy*; D016896:Treatment Outcome; D018487:Ventricular Dysfunction, Left / Q000503:physiopathology / Q000628:therapy*