title: Life threatening hyperkalemia in a neonate with pseudo-hypoaldosteronism.
abstract: Pseudohypoaldosteronism type 1 is a rare disorder characterized by renal resistance to aldosterone which may present with a salt wasting crisis in infancy. We report a neonate with hyponatremia, severe dehydration and refractory life threatening hyperkalemia who was treated with dietary sodium chloride supplementation, potassium binding resins and fluid replacement therapy which proved to be lifesaving.
authors: Department of Neonatology, Shifa International Hospital, Islamabad.
authors: Shehla
authors: S
authors: Choudhry
authors: Yawar
authors: Y
authors: Najam
mesh_terms: D000893:Anti-Inflammatory Agents / Q000627:therapeutic use; D003937:Diagnosis, Differential; D005438:Fludrocortisone / Q000627:therapeutic use; D005440:Fluid Therapy; D006801:Humans; D006947:Hyperkalemia / Q000175:diagnosis* / Q000628:therapy*; D007231:Infant, Newborn; D008297:Male; D011137:Polystyrenes / Q000627:therapeutic use; D011546:Pseudohypoaldosteronism / Q000175:diagnosis* / Q000628:therapy*; D017693:Sodium Bicarbonate / Q000627:therapeutic use; D012965:Sodium Chloride / Q000627:therapeutic use
chemical_list: D000893:Anti-Inflammatory Agents; D011137:Polystyrenes; D012965:Sodium Chloride; C003321:polystyrene sulfonic acid; D017693:Sodium Bicarbonate; D005438:Fludrocortisone