title: Gorlin syndrome and bilateral ovarian fibroma.
abstract: BACKGROUND
  Gorlin syndrome (GS), also known as nevoid basal cell carcinoma syndrome (NBCCS), is a rare hereditary, autosomal dominant disease that affects various systems. Its prevalence is estimated at 1/57,000 to 1/256,000 of the population. It is characterized by basal cell carcinomas, multiple odontogenic keratocysts, skeletal abnormalities and ovarian fibroma, among other disorders.
  
  
  METHODS
  To report the case of a young patient with Gorlin syndrome and bilateral ovarian fibroma.
  
  
  CONCLUSIONS
  A 20-year old patient with Gorlin syndrome presented with facial asymmetry, broad nasal root, dental abnormalities, micrognathism, convergent strabismus, multiple pigmented lesions on the trunk and face, pectus excavatum, kyphoscoliosis and a palpable mass in the abdomen occupying the entire pelvic region.
  
  
  CONCLUSIONS
  Gorlin-Goltz syndrome is a hereditary pathology that includes numerous clinical manifestations. Diagnosis is clinical and genetic confirmation is unnecessary.
authors: Hospital Santa Casa de Misericórdia de Vitória, Vitória, ES, Brazil.
authors: Fernanda
authors: F
authors: Pirschner
authors: Pollyana Marçal
authors: PM
authors: Bastos
authors: George Luiz
authors: GL
authors: Contarato
authors: Anna Carolina Bon Lima
authors: AC
authors: Bimbato
authors: Antônio Chambô
authors: AC
authors: Filho