title: [Enterocolitis as a complication of late-diagnosed Hirschsprung disease].
abstract: Enterocolitis is the most serious complication of Hirschsprung disease. Early management of these patients can decrease the severity of this complication. Hirschsprung disease is more common in patients with trisomy 21 than in the general population. Furthermore, the risk of developing enterocolitis is higher in this population. We report on an infant with trisomy 21 who developed enterocolitis as a complication of Hirschsprung disease that was diagnosed late when the infant presented with septic shock leading to death of the patient.
authors: Service des urgences pédiatriques, hôpital Armand-Trousseau, 26, avenue du Docteur-Arnold-Netter, 75571 Paris cedex 12, France. claire.tournier@trs.aphp.fr
authors: C
authors: C
authors: Tournier-Astruc
authors: F
authors: F
authors: Auber
authors: S
authors: S
authors: Renolleau
authors: N
authors: N
authors: de Suremain
authors: C
authors: C
authors: Bourgain-Nguyen
authors: J-B
authors: JB
authors: Armengaud
authors: A-L
authors: AL
authors: Delamar
authors: C
authors: C
authors: Batard
authors: M
authors: M
authors: Agogue
authors: R
authors: R
authors: Carbajal
mesh_terms: D057210:Delayed Diagnosis; D004314:Down Syndrome; D004760:Enterocolitis / Q000209:etiology*; D017809:Fatal Outcome; D006627:Hirschsprung Disease / Q000175:diagnosis*; D006801:Humans; D007223:Infant; D008297:Male; D012772:Shock, Septic / Q000209:etiology