title: Primary perivascular epithelioid cell neoplasm (PEComa) of bone: report of two cases and review of the literature.
abstract: Primary perivascular epithelioid cell neoplasms (PEComas) of bone are rare mesenchymal tumors. Histologically, they are composed predominantly of perivascular epithelioid cells and have the capacity to metastasize. PEComas have been reported within intra-abdominal and intra-pelvic organs. To the best of our knowledge, only seven primary PEComas of bone have been described in the English literature. We present two cases of PEComa of bone, one arising from the distal fibula and one from the acetabulum. Both were treated by surgical excision and one also received adjuvant chemotherapy.
authors: Department of Orthopaedic Surgery, McGill University Health Center, 1650 Cedar Avenue, Montreal, Quebec, Canada. nicholas.desy@mail.mcgill.ca
authors: Nicholas M
authors: NM
authors: Desy
authors: Mitchell
authors: M
authors: Bernstein
authors: Ayoub
authors: A
authors: Nahal
authors: Mohamed
authors: M
authors: Aziz
authors: Samuel
authors: S
authors: Kenan
authors: Robert E
authors: RE
authors: Turcotte
authors: Leonard B
authors: LB
authors: Kahn
mesh_terms: D000077:Acetabulum; D000328:Adult; D000369:Aged, 80 and over; D001859:Bone Neoplasms / Q000175:diagnosis* / Q000473:pathology / Q000628:therapy; D017024:Chemotherapy, Adjuvant; D003131:Combined Modality Therapy; D003937:Diagnosis, Differential; D017809:Fatal Outcome; D005260:Female; D005360:Fibula; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D011183:Postoperative Complications