title: Independent mobility after early introduction of a power wheelchair in spinal muscular atrophy.
abstract: Weakness resulting from spinal muscular atrophy causes severe limitations in functional mobility. The early introduction of power mobility has potential to enhance development and mitigate disability. These outcomes are achieved by simulating normal skill acquisition and by promoting motor learning, visuospatial system development, self-exploration, cognition, and social development. There are few reports on early power mobility in spinal muscular atrophy, and it is typically not prescribed until school age. The authors evaluated 6 children under age 2 years with neuromuscular disease (5 spinal muscular atrophy, 1 congenital muscular dystrophy) for power mobility. Parents recorded the practice hours necessary to achieve independence using the Power Mobility Skills Checklist. Four children achieved independence in all items on the checklist by 7.9 months (range: 73-458 days). Introduction of early power mobility is feasible in spinal muscular atrophy patients under age 2 years and should be introduced in late infancy when children typically acquire locomotor skills.
authors: Neurology Department, Columbia University Medical Center, New York, NY 10032, USA. sld2120@columbia.edu
authors: Sally
authors: S
authors: Dunaway
authors: Jacqueline
authors: J
authors: Montes
authors: Jessica
authors: J
authors: O'Hagen
authors: Douglas M
authors: DM
authors: Sproule
authors: Darryl C De
authors: DC
authors: Vivo
authors: Petra
authors: P
authors: Kaufmann
mesh_terms: D000203:Activities of Daily Living / Q000145:classification* / Q000523:psychology; D002675:Child, Preschool; D003286:Contracture / Q000175:diagnosis / Q000534:rehabilitation*; D004185:Disability Evaluation; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D007223:Infant; D008297:Male; D019957:Motor Skills Disorders / Q000175:diagnosis / Q000534:rehabilitation*; D009136:Muscular Dystrophies / Q000151:congenital* / Q000175:diagnosis / Q000534:rehabilitation; D010865:Pilot Projects; D014897:Spinal Muscular Atrophies of Childhood / Q000175:diagnosis / Q000534:rehabilitation*; D014910:Wheelchairs