Facial morphology and occlusion of a patient with fibrodysplasia ossificans progressiva (FOP): a case report.
Fibrodysplasia ossificans progressiva (FOP) is a rare disease characterized by postnatal heterotopic ossification (HO). When HO affects the masticatory muscles, mouth opening becomes restricted. This paper presents the changes in facial morphology and occlusion of a patient with FOP who was followed from the age of 8 to age 21. At the initial examination, he had a severely protruded maxilla and Angle Class II Division 1 malocclusion. His mouth opening was restricted (5.0 mm). He had a large overjet and this enabled him to clean his teeth and to eat. Orthodontic correction was not planned, and his facial growth was closely followed with attention to his oral hygiene. The maxillary protrusion and a low mandibular plane angle became more prominent as the patient aged. His mandible rotated in a counterclockwise direction. His molars had delayed eruption or were impacted and seven were extracted. His mouth opening increased slightly and his oral hygiene improved to excellent.
Department of Oral-Maxillofacial Surgery, Dentistry and Orthodontics, The University of Tokyo Hospital, Tokyo, Japan. susami-ora@h.u-tokyo.ac.jp
Takafumi
T
Susami
Yoshiyuki
Y
Mori
Kazumi
K
Tamura
Kazumi
K
Ohkubo
Kouhei
K
Nagahama
Naoko
N
Takahashi
Natsuko
N
Uchino
Kiwako
K
Uwatoko
Nobuhiko
N
Haga
Tsuyoshi
T
Takato
D002508:Cephalometry; D002648:Child; D017742:Dental Care for Chronically Ill; D006801:Humans; D008297:Male; D008312:Malocclusion, Angle Class II / Q000209:etiology; D008334:Mandible / Q000002:abnormalities; D008437:Maxilla / Q000002:abnormalities; D008445:Maxillofacial Development; D009221:Myositis Ossificans / Q000150:complications / Q000473:pathology*; D009910:Oral Hygiene; D009999:Ossification, Heterotopic / Q000209:etiology; D011378:Prognathism / Q000209:etiology