Central airway obstruction due to malignant fibrous histiocytoma metastasis in a case with Mounier-Kuhn syndrome.
Malign fibrous histiocytoma is one of the most observed soft tissue sarcomas seen in the adults. The most common metastasis region is the lung and metastasis. Mounier-Kuhn syndrome is characterized by the highly dilatation of the trachea and bronchi. We may encounter with the major airway obstruction in the endoluminal or extraluminal lung and mediastinal masses or those with both components together. In this article, we would like to highlight the occurrence of a rare seen clinical situation secondary to the giant mediastinal malign fibrous histiocytoma metastasis and the clinical difficulties experienced in resolving of the main airway obstruction caused by the mass. Since the lack of the similar studies conducted previously, we found the case worth presenting.
Clinic of 7th Chest Diseases, Yedikule Chest Diseases and Chest Surgery Training and Research Hospital, Istanbul, Turkey. leventdalar@gmail.com
Levent
L
Dalar
Emel
E
Eryüksel
Filiz
F
Koşar
Ahmet Levent
AL
Karasulu
Nur
N
Urer
Sinem Nedime
SN
Sökücü
Sedat
S
Altın
D000402:Airway Obstruction / Q000175:diagnosis / Q000209:etiology* / Q000601:surgery; D001999:Bronchoscopy; D017809:Fatal Outcome; D051677:Histiocytoma, Malignant Fibrous / Q000150:complications* / Q000601:surgery; D006801:Humans; D008297:Male; D008875:Middle Aged; D009362:Neoplasm Metastasis; D015607:Stents; D014137:Tracheobronchomegaly / Q000150:complications* / Q000601:surgery