A case of Sotos syndrome treated with distraction osteogenesis in maxilla and mandible.
Sotos syndrome is inherited in an autosomal-dominant manner and is characterized by increased birth weight, excessive growth, advanced bone age, and distinctive facial features, including dolichocephaly, hypertelorism, and a prominent mandible. We treated a jaw deformity due to Sotos syndrome consisting of malocclusion due to a narrow maxillary dental arch and mandibular retrusion from hypoplasia of the rami. The patient was a 17-year-old man. Malocclusion due to a narrow maxillary dental arch and mandibular retrusion was diagnosed. Rapid maxillary expansion with Lines corticotomy and mandibular advancement with distraction osteogenesis were performed. The maxilla was expanded laterally a total of 3 mm and the mandible prolonged 12 mm in the posterior area of the mandibular body. Subsequently, orthodontic treatment was continued. At present, 5 years after surgery, occlusion remains good and stable.
Division of Oral and Maxillofacial Surgery, Department of Clinical Oral Health Science, Suidobashi Hospital, Tokyo Dental College, 2-9-18 Misaki-cho, Chiyoda-ku, Tokyo 101-0061, Japan. takano@tdc.ac.jp
Masayuki
M
Takano
Kiyohiro
K
Kasahara
Chiharu
C
Ogawa
Hidenori
H
Katada
Kenji
K
Sueishi
D000293:Adolescent; D003724:Dental Arch / Q000601:surgery; D006801:Humans; D008297:Male; D008310:Malocclusion / Q000601:surgery; D008334:Mandible / Q000002:abnormalities* / Q000601:surgery; D019186:Mandibular Advancement / Q000379:methods*; D008437:Maxilla / Q000002:abnormalities* / Q000601:surgery; D019857:Osteogenesis, Distraction / Q000379:methods*; D010155:Palatal Expansion Technique; D011862:Radiography, Panoramic; D063173:Retrognathia / Q000601:surgery*; D058495:Sotos Syndrome / Q000175:diagnosis / Q000601:surgery*