Right ventricular endomyocardial fibrosis.
Endomyocardial fibrosis is a variety of restrictive cardiomyopathy, in which endocardium of one or both ventricles is thickened markedly with involvement of underlying myocardium. Partial obliteration of ventricular cavities by fibrous tissue and thrombus causes diastolic dysfunction with increased resistance to ventricular filling. Systolic function is well preserved till late stages. Biventricular or isolated left ventricular involvement is common. Isolated right ventricular involvement is relatively uncommon. Case reports on endomyocardial fibrosis have declined in literature. In India, endomyocardial fibrosis is mainly reported from Kerala. A case of right ventricular endomyocardial fibrosis from West Bengal is reported here. Isolated right sided endomyocardial fibrosis, massive right atrial enlargement, complete disorganization of tricuspid valve, massive pericardial effusion, normal absolute eosinophil count and its sporadic occurrence outside 15 degrees of the equatorial belt were interesting features in this case of endomyocardial fibrosis. X-ray features were typical of pericardial effusion masking underlying endomyocardial fibrosis. Endomyocardial fibrosis is a neglected research field. It needs more attention from biomedical researchers.
Dept. of Medicine, Medical College, 88 College Street, Kolkata, PIN-700073.
Gouranga
G
Santra
Pradip Kumar
PK
Sinha
Sibaji
S
Phaujdar
Dibyendu
D
De
D000328:Adult; D000925:Anticoagulants / Q000627:therapeutic use; D002313:Cardiomyopathy, Restrictive / Q000000981:diagnostic imaging* / Q000188:drug therapy / Q000209:etiology; D002316:Cardiotonic Agents / Q000627:therapeutic use; D004077:Digoxin / Q000627:therapeutic use; D004232:Diuretics / Q000627:therapeutic use; D004452:Echocardiography; D004719:Endomyocardial Fibrosis / Q000000981:diagnostic imaging* / Q000188:drug therapy; D005260:Female; D006352:Heart Ventricles / Q000000981:diagnostic imaging* / Q000503:physiopathology; D006801:Humans; D010490:Pericardial Effusion / Q000000981:diagnostic imaging / Q000188:drug therapy; D016896:Treatment Outcome; D014261:Tricuspid Valve / Q000000981:diagnostic imaging
D000925:Anticoagulants; D002316:Cardiotonic Agents; D004232:Diuretics; D004077:Digoxin