Surgical treatment of cardiovascular complications in patients with Marfan syndrome: a report of two cases and literature review.
Cardiovascular disease is the main cause of morbidity and mortality in patients with Marfan syndrome. The most life threatening complication is aortic root aneurysms leading to aortic dissection or rupture. It can be prevented by regular aortic follow-up and prophylactic aortic surgery. Modern aortic surgery has led to a substantial increase in the life expectancy of these patients. We report two cases of Marfan syndrome with cardiovascular complications. Their management is discussed according to the most recent literature.
Department of Cardiovascular Surgery, University Hospital of Liège, Belgium.
S
S
Bruls
M A
MA
Radermecker
E
E
Creemers
P
P
Bonnet
E
E
Nellessen
H
H
Van Damme
L
L
De Leval
J O
JO
Defraigne
D019917:Blood Vessel Prosthesis Implantation; D016027:Heart Transplantation; D006801:Humans; D008297:Male; D008382:Marfan Syndrome / Q000150:complications* / Q000175:diagnosis / Q000601:surgery*; D008875:Middle Aged; D055815:Young Adult