title: Herlyn-Werner-Wunderlich syndrome--timely diagnosis is important to preserve fertility.
abstract: BACKGROUND
  Herlyn-Werner-Wunderlich syndrome is an urogenital malformation with uterus didelphys and obstructed hemivagina with ipsilateral renal agenesis. Most of these patients present after the onset of menstruation. We describe two cases diagnosed too late to prevent the complications.
  
  
  METHODS
  The first patient presented with acute abdomen one year after the onset of menstruation and had salpingectomy due to pyosalpinx. The blind hemivagina was not recognized and she had severe endometriosis. She underwent hysterectomy 8 years later. The second patient presented with foul smelling vaginal discharge when she was 21 years old. She had a simple vaginal septum resection.
  
  
  CONCLUSIONS
  In the presence of uterine cavities in a regularly menstruating girl with dysmenorrhea, the presence of both kidneys should be checked. When unilateral renal agenesis and uterus didelphys coexist the first thing that we should remember is to confirm or refute the presence of a blind vagina.
authors: İstanbul Bilim University, Avrupa Hospital, Department of Obstetrics and Gynecology, İstanbul, Turkey. nilgun.kutay@gmail.com
authors: Nilgün
authors: N
authors: Güdücü
authors: Gökçenur
authors: G
authors: Gönenç
authors: Herman
authors: H
authors: Işçi
authors: Alin Başgül
authors: AB
authors: Yiğiter
authors: Ilkkan
authors: I
authors: Dünder
mesh_terms: D000006:Abdomen, Acute; D000293:Adolescent; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D052202:Hydrocolpos / Q000151:congenital / Q000175:diagnosis* / Q000601:surgery; D007044:Hysterectomy; D007668:Kidney / Q000002:abnormalities*; D058994:Salpingectomy; D013577:Syndrome; D014564:Urogenital Abnormalities / Q000175:diagnosis* / Q000601:surgery*; D014599:Uterus / Q000002:abnormalities*; D014621:Vagina / Q000002:abnormalities*; D055815:Young Adult