title: Splenogonadal fusion and sex reversal.
abstract: Splenogonadal fusion is a rare congenital malformation where an abnormal union occurs between the spleen and gonad or mesonephric derivatives. Although it occurs in females it is much less prevalent than in males (male:female ratio, 16:1), but this may partly be because of the inaccessibility of the female gonads leading to under-diagnosis. To our knowledge this is the first case of splenogonadal fusion associated with sex reversal reported in the literature.
authors.affiliation: Department of Paediatric Surgery, Sheffield Children's Foundation Trust Hospital, Sheffield, UK.
authors.forename: Ruth
authors.initials: R
authors.lastname: Speare
authors.forename: Julian
authors.initials: J
authors.lastname: Roberts
authors.forename: Marta
authors.initials: M
authors.lastname: Cohen
authors.forename: Jerry
authors.initials: J
authors.lastname: Wales
mesh_terms: D058531:46, XX Testicular Disorders of Sex Development / Q000150:complications / Q000473:pathology*; D005260:Female; D006059:Gonadal Dysgenesis / Q000150:complications / Q000473:pathology*; D006066:Gonads / Q000002:abnormalities*; D006801:Humans; D018636:Hypoplastic Left Heart Syndrome / Q000150:complications; D007231:Infant, Newborn; D008297:Male; D013085:Spermatic Cord / Q000002:abnormalities; D013154:Spleen / Q000002:abnormalities*