Noncompaction of the myocardium coexistent with bronchiectasis and polycystic kidney disease.
Noncompaction of the ventricular myocardium (NCM) is a disorder of unknown aetiology characterised by numerous, prominent ventricular trabeculations and deep intertrabecular recesses. Polycystic kidney disease (PKD) is characterised by the formation of multiple cysts in the kidneys and liver and, less frequently, in the pancreas. Cardiovascular abnormalities in PKD involve hypertension, mitral valve prolapse, intracranial aneurysms and pulmonary abnormalities include primary ciliary dyskinesia and bronchiectasis. Several case reports have described the possible association between PKD and NCM. However, NCM, PKD and bronchiectasis have not previously been correlated. This is the first case of NCM coupled with PKD and bronchiectasis.
Division of Cardiology, Cardiac and Vascular Center, Department of Medicine, Samsung Changwon Hospital, Sungkyunkwan University School of Medicine, Changwon, Republic of Korea.
Ki Hoon
KH
Kim
Bong Gun
BG
Song
Man Je
MJ
Park
Hyoun Soo
HS
Lee
Hea Sung
HS
Ok
Byeong Ki
BK
Kim
Gu Hyun
GH
Kang
Yong Hwan
YH
Park
Woo Jung
WJ
Chun
Ju Hyeon
JH
Oh
D001987:Bronchiectasis / Q000209:etiology / Q000473:pathology / Q000503:physiopathology; D006332:Cardiomegaly / Q000209:etiology / Q000473:pathology / Q000503:physiopathology; D005260:Female; D006801:Humans; D008875:Middle Aged; D007690:Polycystic Kidney Diseases / Q000150:complications / Q000473:pathology / Q000503:physiopathology