Ewing sarcoma/primitive neuroectodermal tumor (PNET) of the vulva. Case report and review of the literature.
Ewing sarcoma is a rare highly malignant neoplasm that is mostly encountered as a primary bone tumor of childhood. Extra osseous occurrence is less frequent and cases involving the vulva are very rare with only twelve reported to date. We report the case of a Ewing sarcoma that presented as a vulvar mass in a 28-year-old Lebanese lady and briefly review the differential diagnosis as well as the published literature regarding the clinical presentation and prognosis.
Department of Obstetric and Gynecology, Saint George Hospital, University Medical Center, Beirut, Lebanon.
Elie N
EN
Anastasiades
Sawsan A
SA
El Abiad
Camil J
CJ
Chouairy
D000328:Adult; D001859:Bone Neoplasms / Q000188:drug therapy / Q000556:secondary; D017809:Fatal Outcome; D005260:Female; D006801:Humans; D012512:Sarcoma, Ewing / Q000473:pathology* / Q000556:secondary / Q000628:therapy; D014846:Vulvar Neoplasms / Q000473:pathology* / Q000628:therapy