Kartagener's syndrome--anaesthetic considerations for ENT surgery.
Kartagener's syndrome is a rare autosomal recessive disorder presenting a triad of sinusitis, bronchicetasis and situs inversus with dextrocardia. It occurs in 50% of patients with situs inversus. The most important anesthetic implications of Kartegener's syndrome surgery are assessement of pulmonary and cardiac structure and function. We present a case of 43-year-old woman with chronic rhinosinusitis with polyps and bilateral sectetory otitis media. The chest radiograph and CT scans showed dextrocardia and situs inversus with chronic bronchitis without bronchiectasis. Spirometry showed forced expiratory volume in one second (FEV1) of 2.66 L and forced vital capacity (FVC) of 3.62 L. Electroechography showed no cardiac abnormalities with 55-60% of EF. The anesthetic implications of Kartagener's syndrome are varied. The regional or general anesthesia might be involved with sinus surgery, ear surgery, pulmonary surgery, infertility or abdominal and cardiac surgery. The main anesthetic considerations among patients with Kartagener's syndrome are related to the pulmonary function which include preoperative respiratory infections due to bronchiectasis. We should also monitor potentially occluded congenital heart diseases. Kartagener's syndrome is a rare disease and when the patient need an operation we have to consider surgery with regional or general anesthesia. The general anesthesia would be safe after complete preanaesthetic examination of the patient. The ECG, chest CT scans, spirometry and echocardiography are mandatory before the operation.
Katedra i Klinika Otolaryngologii i Onkologii Laryngologicznej Collegium Medium w Bydgoszczy, UMK w Toruniu. pburduk@wp.pl
Pawel K
PK
Burduk
Katarzyna
K
Wawrzyniak
Wojciech
W
Kazmierczak
Krzysztof
K
Kusza
D000328:Adult; D000768:Anesthesia, General / Q000379:methods*; D002908:Chronic Disease; D000075202:Contraindications; D004452:Echocardiography; D004562:Electrocardiography; D005260:Female; D006330:Heart Defects, Congenital / Q000175:diagnosis*; D006801:Humans; D007619:Kartagener Syndrome / Q000175:diagnosis* / Q000601:surgery*; D009296:Nasal Cavity / Q000601:surgery*; D009298:Nasal Polyps / Q000000981:diagnostic imaging / Q000601:surgery; D010034:Otitis Media with Effusion / Q000601:surgery; D011300:Preoperative Care / Q000379:methods*; D012852:Sinusitis / Q000601:surgery; D013147:Spirometry; D014057:Tomography, X-Ray Computed