title: Presyrinx in a child with acquired Chiari I malformation.
abstract: Spinal cord signal abnormality resulting from alterations in cerebrospinal fluid flow at the craniocervical junction has been termed a presyrinx state. This condition has been described in the adult literature in association with a variety of conditions that cause obstruction to normal cerebrospinal fluid flow. We present a case of presyrinx in a child in the setting of acquired Chiari I malformation caused by lumboperitoneal overshunting. Awareness of the potentially reversible nature of this condition might allow for intervention before irreversible neurological damage has occurred.
authors.affiliation: Department of Radiology, Seattle Children's Hospital, 4800 Sand Point Way NE, Seattle, WA 98105, USA. jnixon@uw.edu
authors.forename: Jason N
authors.initials: JN
authors.lastname: Nixon
authors.forename: Luana A
authors.initials: LA
authors.lastname: Stanescu
authors.forename: Edward
authors.initials: E
authors.lastname: Weinberger
mesh_terms: D001139:Arnold-Chiari Malformation / Q000473:pathology* / Q000601:surgery*; D002557:Cerebrospinal Fluid Shunts; D004487:Edema / Q000473:pathology* / Q000601:surgery*; D006801:Humans; D007223:Infant; D008297:Male; D013595:Syringomyelia / Q000473:pathology* / Q000601:surgery*; D016896:Treatment Outcome