title: A rare case of isolated congenital right ventricular inflow obstruction due to the presence of an intraventricular muscular shelf.
abstract: A 56-year-old man presented with anasarca and a 40-lb weight gain that had occurred over the course of 3 to 4 weeks. He had a history of permanent atrial fibrillation and a congenital anomaly of the right ventricular inflow tract. This defect consisted of a muscular shelf in the right ventricular inflow tract, which encased the tricuspid subvalvular apparatus in such a manner that it created tricuspid stenosis. The clinical consequences of this anatomic and hemodynamic situation were a massively dilated right atrium, permanent atrial fibrillation, and clinical evidence of right-sided heart failure, including fluid retention and ascites. The patient underwent surgical resection of the muscular shelf, which was followed by progressive resolution of the ascites and fluid retention.
authors.affiliation: Sackler School of Medicine, New York, New York 10065, USA.
authors.forename: Giovanni J
authors.initials: GJ
authors.lastname: Nanna
authors.forename: Michael G
authors.initials: MG
authors.lastname: Nanna
authors.forename: Danielle
authors.initials: D
authors.lastname: Muchnik
authors.forename: Joseph J
authors.initials: JJ
authors.lastname: DeRose
authors.forename: Seshasayee
authors.initials: S
authors.lastname: Narasimhan
mesh_terms: D001201:Ascites / Q000209:etiology; D001281:Atrial Fibrillation / Q000209:etiology; D006328:Cardiac Catheterization; D006348:Cardiac Surgical Procedures; D006332:Cardiomegaly / Q000209:etiology; D018618:Echocardiography, Doppler, Color; D006330:Heart Defects, Congenital / Q000150:complications / Q000175:diagnosis* / Q000503:physiopathology / Q000601:surgery; D006333:Heart Failure / Q000209:etiology; D006352:Heart Ventricles / Q000002:abnormalities* / Q000503:physiopathology / Q000601:surgery; D006439:Hemodynamics; D006801:Humans; D008297:Male; D008875:Middle Aged; D010210:Papillary Muscles / Q000002:abnormalities* / Q000503:physiopathology / Q000601:surgery; D016896:Treatment Outcome; D014264:Tricuspid Valve Stenosis / Q000150:complications / Q000175:diagnosis* / Q000503:physiopathology / Q000601:surgery