title: Rare sarcoma presented as sinusitis.
abstract: Myxofibrosarcoma (MFS) also known as myxoid variant of malignant fibrous histocytoma is one of the most common soft tissue sarcomas of the extremities in adult and elderly patients with rare occurrences in head and neck region. Low-grade MFS is unusual among low-grade sarcomas because it often recurs relentlessly and multiplies despite wide local resection with gross negative margins. We report a case of extreme rarity and a tumour of aggressive nature in the maxillary sinus, which presented with non-specific sinonasal symptoms and we present a review of the radiological and histopathological characteristics of this rare tumour and recent evidence of management.
authors.affiliation: ENT, Barts and The London Hospitals, Whitechapel, UK. ali@taghi.org.uk
authors.forename: Ali S
authors.initials: AS
authors.lastname: Taghi
authors.forename: Ahmed
authors.initials: A
authors.lastname: Ali
authors.forename: Romana
authors.initials: R
authors.lastname: Kuchai
authors.forename: Hesham
authors.initials: H
authors.lastname: Saleh
mesh_terms: D001706:Biopsy; D003937:Diagnosis, Differential; D004724:Endoscopy; D005260:Female; D051677:Histiocytoma, Malignant Fibrous / Q000175:diagnosis* / Q000473:pathology / Q000601:surgery; D006801:Humans; D008437:Maxilla / Q000473:pathology / Q000601:surgery; D008443:Maxillary Sinus / Q000473:pathology / Q000601:surgery; D008444:Maxillary Sinus Neoplasms / Q000175:diagnosis* / Q000473:pathology / Q000601:surgery; D015523:Maxillary Sinusitis / Q000175:diagnosis* / Q000473:pathology / Q000601:surgery; D008875:Middle Aged; D009361:Neoplasm Invasiveness; D012086:Reoperation; D012227:Rhinosporidiosis; D014057:Tomography, X-Ray Computed; D020390:Tooth Socket / Q000473:pathology / Q000601:surgery