title: Flexor digitorum superficialis opposition tendon transfer improves hand function in children with Charcot-Marie-Tooth disease: case series.
abstract: Charcot-Marie-Tooth disease limits hand function. Tendon transfer has not been reported in pediatric CMT. We report two severely affected children following long finger flexor digitorum superficialis opposition tendon transfer. Improvement was noted in palmar abduction, (30°/40°), opposition, (thumb to all digits), and acquisition of pincer, palmar, and lateral pinch with measureable force (1 lb). Dexterity testing improved on the 9 Hole Peg Test (1.03 s/77 s, 22 s) and Functional Dexterity Test (13 s/33 s, 88 s). Functional improvements were observed in self feeding, clothing management, and play. These cases support flexor digitorum superficialis opposition tendon transfer surgery to improve hand function in children with CMT.
authors.affiliation: The Children's Hospital of Philadelphia Philadelphia, PA 19104, USA. Estilow@email.chop.edu
authors.forename: T
authors.initials: T
authors.lastname: Estilow
authors.forename: S H
authors.initials: SH
authors.lastname: Kozin
authors.forename: A M
authors.initials: AM
authors.lastname: Glanzman
authors.forename: J
authors.initials: J
authors.lastname: Burns
authors.forename: R S
authors.initials: RS
authors.lastname: Finkel
mesh_terms: D002607:Charcot-Marie-Tooth Disease / Q000175:diagnosis / Q000601:surgery*; D002648:Child; D005260:Female; D006225:Hand / Q000503:physiopathology / Q000601:surgery*; D006801:Humans; D013709:Tendon Transfer / Q000379:methods; D013710:Tendons / Q000601:surgery*; D013933:Thumb / Q000503:physiopathology / Q000601:surgery; D016896:Treatment Outcome