title: Right subclavian artery aneurysm in an adolescent with a bicuspid aortic valve.
abstract: Bicuspic aortic valve is the most common congenital cardiac anomaly (Fedak et al. 106:900-904, 2002), and it is associated with other structural anomalies of the aorta, such as coarctation, suggesting a common embryologic developmental mechanism (Mergan et al. 104:118-119, 2004). In more than a half of patients, it is associated with progressive dilation and aneurysm formation of the aorta (Warnes 89:965-966, 2003) despite normally functioning bicuspid aortic valves. In this context, aneurysms of the right subclavian artery are extremely rare, and even more so when associated with a right-sided aortic arch that has a left aberrant subclavian artery with a Kommerell diverticulum, as found in the reported case. These aneurysms represent a significant risk for thromboembolism and rupture, and elective surgical management should be advised, even for asymptomatic cases.
authors.affiliation: Department of Pediatric Cardiology, Hospital Pediátrico Carmona da Mota, Av. Afonso Romão, Santo António dos Olivais, 3000-602, Coimbra, Portugal.
authors.forename: J
authors.initials: J
authors.lastname: Marinho
authors.forename: A
authors.initials: A
authors.lastname: Pires
authors.forename: G
authors.initials: G
authors.lastname: Sousa
authors.forename: E
authors.initials: E
authors.lastname: Castela
mesh_terms: D000015:Abnormalities, Multiple; D000293:Adolescent; D000783:Aneurysm / Q000151:congenital* / Q000175:diagnosis; D001021:Aortic Valve / Q000002:abnormalities*; D000082882:Bicuspid Aortic Valve Disease; D003937:Diagnosis, Differential; D004452:Echocardiography; D006349:Heart Valve Diseases / Q000175:diagnosis*; D006801:Humans; D008297:Male; D013348:Subclavian Artery; D014057:Tomography, X-Ray Computed