title: Angiosarcoma of the scalp associated with Xeroderma pigmentosum.
abstract: Xeroderma pigmentosum (XP) is a rare autosomal recessive genodermatosis associated with hypersensitivity to ultraviolet light due to defects in Deoxyribonucleic acid (DNA) repair. These patients have more than a 1000-fold increased risk of developing skin cancers. Although multiple cutaneous malignancies are common, the simultaneous occurrence of angiosarcoma and basal cell carcinoma is a rare phenomenon. We report a case of a 25-year-old male with XP with angiosarcoma scalp and basal cell carcinoma of face and occiput and discuss the treatment of this aggressive neoplasm with a review of the literature pertaining to it.
authors.affiliation: Department of Head and Neck Surgical Oncology, Tata Memorial Hospital, Mumbai, Maharashtra, India.
authors.forename: Shilpi
authors.initials: S
authors.lastname: Sharma
authors.forename: Anuja D
authors.initials: AD
authors.lastname: Deshmukh
authors.forename: Munita M
authors.initials: MM
authors.lastname: Bal
authors.forename: Devendra A
authors.initials: DA
authors.lastname: Chaukar
authors.forename: Anil K
authors.initials: AK
authors.lastname: Dcruz