title: [A case of lymphogranulomatosis in a patient with type 1 neurofibromatosis].
abstract: Neurofibromatosis is a common monogenic disease in man; its incidence is at least 1:3000-1:4000 population. It is inherited in the autosomal dominant mode with high penetrance and variable expression. A patient presenting with type 1 neurofibromatosis since the age of 3 mo who developed lymphogranulomatosis is reported. The patient 1 life prognosis is presently determined by the competing pathology. It is emphasized that neurofibromatosis is associated with different forms of lung lesions and creates a risk of neoplastic (including malignant) growth.
authors.forename: O A
authors.initials: OA
authors.lastname: Tsvetkova
authors.forename: G B
authors.initials: GB
authors.lastname: Abdullaeva
mesh_terms: D000328:Adult; D005260:Female; D006099:Granuloma / Q000175:diagnosis / Q000473:pathology; D006689:Hodgkin Disease / Q000175:diagnosis* / Q000473:pathology; D006801:Humans; D016403:Lymphoma, Large B-Cell, Diffuse / Q000175:diagnosis / Q000473:pathology; D009456:Neurofibromatosis 1 / Q000175:diagnosis* / Q000473:pathology; D011379:Prognosis; D036542:Tomography, Spiral Computed; D055815:Young Adult