title: Adenoid cystic carcinoma of skene glands:  a rare origin in the female genital tract and the characteristic clinical course.
abstract: Adenoid cystic carcinoma (ACC) is a relatively uncommon malignancy that most frequently arises in the salivary glands. In the genital tract, approximately 60 cases of ACC that originated from Bartholin glands have been reported to date. In this report, we describe a case of ACC that arose from Skene glands, a very rare origin for this disease. In this patient, the disease had an indolent clinical course, with few symptoms other than localized pain. During the surgical operation, the tumor was found to have invaded more extensively than had been estimated preoperatively, and it required pelvic exenteration with radical vulvectomy. Although the precise preoperative assessment and the preparation for an extended operation are difficult, they are necessary for the successful treatment of this rare disease.
authors.affiliation: Department of Gynecology and Obstetrics, Graduate School of Medicine, Kyoto University, Kyoto, Japan.
authors.forename: Yusuke
authors.initials: Y
authors.lastname: Ueda
authors.forename: Masaki
authors.initials: M
authors.lastname: Mandai
authors.forename: Noriomi
authors.initials: N
authors.lastname: Matsumura
authors.forename: Tsukasa
authors.initials: T
authors.lastname: Baba
authors.forename: Ayako
authors.initials: A
authors.lastname: Suzuki
authors.forename: Yumiko
authors.initials: Y
authors.lastname: Yoshioka
authors.forename: Kenzo
authors.initials: K
authors.lastname: Kosaka
authors.forename: Ikuo
authors.initials: I
authors.lastname: Konishi
mesh_terms: D003528:Carcinoma, Adenoid Cystic / Q000175:diagnosis / Q000473:pathology* / Q000601:surgery; D005260:Female; D006801:Humans; D008875:Middle Aged; D014523:Urethral Neoplasms / Q000175:diagnosis / Q000473:pathology* / Q000601:surgery