Extralobar pulmonary sequestration with an unusual venous drainage to the portal vein: preoperative diagnosis and excision by video-assisted thoracoscopy.
Pulmonary sequestration is an uncommon congenital malformation of the lung that can be classified as intralobar or extralobar (ELS). Approximately 90% of ELS occur in the left hemithorax. Approximately 10% of ELS may present below the diaphragm. Both types of sequestrations are characterized by pulmonary tissue that does not communicate with the bronchial tree. The arterial blood supply to 80% ELS is through a direct branch of the thoracic or abdominal aorta, in 15% via another systemic artery and 5% from the pulmonary artery. The venous drainage of ELS is variable, predominantly into the systemic circulation (via the azygos vein, hemiazygos vein, or inferior vena cava). Approximately 25% drain completely or partially through the pulmonary veins. We report an extremely rare case of ELS with unusual venous drainage to the portal vein.
Division of Pediatric Surgery, University Hospital of Joan XXIII, 43007 Tarragona, Spain. rskrabski@gmail.com
Robert
R
Skrabski
Yolanda
Y
Royo
Ida
I
Di Crosta
Carlos
C
Pueyo
Tomas
T
Sempere
Joaquín
J
Maldonado
D000015:Abnormalities, Multiple / Q000175:diagnosis* / Q000601:surgery*; D001998:Bronchopulmonary Sequestration / Q000150:complications / Q000175:diagnosis* / Q000601:surgery*; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D011169:Portal Vein / Q000002:abnormalities*; D011300:Preoperative Care; D020775:Thoracic Surgery, Video-Assisted