Successful treatment of plastic bronchitis with low fat diet and subsequent thoracic duct ligation in child with fontan physiology.
Plastic bronchitis is a rare condition characterized by the formation and expectoration of long, branching bronchial casts that develop in the tracheobronchial tree and cause airway obstruction. Plastic bronchitis has become increasingly recognized as a feared complication of the Fontan operation with a mortality of up to 50%. We report an 11 year old boy who developed severe plastic bronchitis following Fontan repair and the successful long-term control of cast formation utilizing a low-fat diet and subsequent thoracic duct ligation.
Department of Pediatrics, University of Arizona College of Medicine, Tucson, Arizona USA.
K
K
Parikh
M H
MH
Witte
R
R
Samson
M
M
Teodori
J B
JB
Carpenter
M C
MC
Lowe
W
W
Morgan
C
C
Hardin
M
M
Brown
Y
Y
Naughton
S
S
Sinha
B J
BJ
Barber
D001991:Bronchitis / Q000178:diet therapy* / Q000209:etiology; D001999:Bronchoscopy; D002648:Child; D003131:Combined Modality Therapy; D018752:Diet, Fat-Restricted; D018729:Fontan Procedure / Q000009:adverse effects*; D006801:Humans; D008026:Ligation; D008297:Male; D011183:Postoperative Complications; D011379:Prognosis; D013897:Thoracic Duct / Q000601:surgery*