Congenital bronchopulmonary foregut malformation initially diagnosed as esophageal atresia type C: challenging diagnosis and treatment.
Communicating bronchopulmonary foregut malformations are extremely rare congenital malformations, characterized by a communicating fistula between an isolated part of the respiratory system and the esophagus or the stomach. In this article, we present a case of esophageal atresia type C, later diagnosed as a rare form of a communicating bronchopulmonary foregut malformation, an esophageal atresia combined with right main bronchus originating from the lower esophagus. Therapeutic resection of the right lung was complicated by postpneumonectomy syndrome.
Paediatric Surgical Centre of Amsterdam, Emma Children's Hospital AMC and VU University Medical Centre, Amsterdam, The Netherlands. doekeboersma@gmail.com
Doeke
D
Boersma
Bart G
BG
Koot
Erik Jonas
EJ
van der Griendt
Rick R
RR
van Rijn
Alida F
AF
van der Steeg
D000015:Abnormalities, Multiple / Q000175:diagnosis* / Q000601:surgery; D001980:Bronchi / Q000002:abnormalities*; D003937:Diagnosis, Differential; D004933:Esophageal Atresia / Q000145:classification / Q000175:diagnosis*; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D014138:Tracheoesophageal Fistula / Q000150:complications / Q000151:congenital* / Q000175:diagnosis* / Q000601:surgery