Ganglioneuroma in the papilla of Vater with neurofibromatosis type 1: report of a case.
Ganglioneuromas (GNs) are rare benign tumors and their association with neurofibromatosis type 1 (NF-1) is especially uncommon. We report in this article the case of a young woman, subjected to diagnostic work-up because of abdominal pain. Endoscopy and histology revealed not only a GN in the papilla of Vater, but also NF-1. Because of the size and macroscopic features of the lesion, we performed pancreatoduodenectomy, from which she recovered uneventfully. Histological examination of the resected tumor confirmed a diagnosis of GN.
Department of Surgery, Medical Faculty of Pécs University, Rákóczi u. 2, 7623 Pécs, Hungary.
Róbert
R
Papp
József
J
Baracs
András
A
Papp
Tamás
T
Tornóczki
Aron
A
Vincze
Ors Péter
OP
Horváth
Dezső
D
Kelemen
D000328:Adult; D014670:Ampulla of Vater / Q000601:surgery*; D003138:Common Bile Duct Neoplasms / Q000175:diagnosis / Q000209:etiology* / Q000473:pathology / Q000601:surgery*; D005260:Female; D005729:Ganglioneuroma / Q000175:diagnosis / Q000209:etiology* / Q000473:pathology / Q000601:surgery*; D006801:Humans; D009456:Neurofibromatosis 1 / Q000150:complications*; D016577:Pancreaticoduodenectomy; D016896:Treatment Outcome