title: Mid-aortic syndrome in a 3-year-old girl successfully treated by aorto-aortic grafting and renal artery implantation into the graft.
abstract: Mid-aortic syndrome, an uncommon acquired or congenital condition characterized by segmental narrowing of the abdominal or distal descending thoracic aorta, is frequently accompanied by ostial stenosis of the aorta's branches. If left untreated, it can result in life-threatening complications secondary to severe hypertension.We report the case of a 3-year-old girl with congenital mid-aortic syndrome, who was diagnosed by chance in the course of a viral illness, and whose high blood pressure values were first dismissed as inaccurate. Attempts to achieve medical or endovascular control of her hypertension were unsuccessful. She was thereafter successfully treated by aorto-aortic bypass grafting, resection of the stenotic segments of both renal arteries, and implantation of the patent arterial segments into the graft.
authors.affiliation: Departments of Pediatric Nephrology, University Medical Centre Ljubljana, 1525 Ljubljana, Slovenia.
authors.forename: Tanja Kersnik
authors.initials: TK
authors.lastname: Levart
authors.forename: Tomislav
authors.initials: T
authors.lastname: Klokocovnik
mesh_terms: D001012:Aorta, Abdominal / Q000002:abnormalities / Q000503:physiopathology / Q000601:surgery*; D001018:Aortic Diseases / Q000151:congenital / Q000175:diagnosis / Q000503:physiopathology / Q000601:surgery*; D001027:Aortography; D001794:Blood Pressure; D019917:Blood Vessel Prosthesis Implantation / Q000379:methods*; D002675:Child, Preschool; D003251:Constriction, Pathologic; D005260:Female; D006801:Humans; D006978:Hypertension, Renovascular / Q000209:etiology / Q000503:physiopathology / Q000601:surgery; D033162:Incidental Findings; D018810:Magnetic Resonance Angiography; D012077:Renal Artery / Q000002:abnormalities / Q000503:physiopathology / Q000601:surgery*; D012078:Renal Artery Obstruction / Q000151:congenital / Q000175:diagnosis / Q000503:physiopathology / Q000601:surgery*; D013577:Syndrome; D016896:Treatment Outcome
keywords: Angioplasty, balloon; aorta, abdominal/abnormalities; aortic coarctation/etiology/surgery; arterial occlusive diseases/surgery; child; hypertension, renal/etiology/surgery; mid-aortic syndrome; reconstructive surgical procedures/methods; renal artery obstruction/surgery