title: Intermittent cyanosis years after a Mustard repair for dextro-transposition of the great arteries.
abstract: A 28-year-old woman, who as an infant had undergone the Mustard atrial switch procedure for dextro-transposition of the great arteries, presented with a baffle leak and consequent intermittent cyanosis. In addition, an occlusive thrombus had formed in the systemic venous baffle after a failed attempt to remove infected pacemaker leads. Corrective surgery was successful. In addition to the case of our patient, we discuss long-term sequelae of the atrial switch procedure that present challenges in patient care.
authors.affiliation: Texas Adult Congenital Heart Program, Texas Children's Hospital, Section of Cardiology, Department of Pediatrics and Medicine, Baylor College of Medicine, Houston, Texas 77030, USA.
authors.forename: Anita
authors.initials: A
authors.lastname: Saraf
authors.forename: Wayne J
authors.initials: WJ
authors.lastname: Franklin
authors.forename: Christopher S
authors.initials: CS
authors.lastname: Snyder
authors.forename: Charles D
authors.initials: CD
authors.lastname: Fraser
authors.forename: Jorge D
authors.initials: JD
authors.lastname: Salazar
mesh_terms: D000328:Adult; D006348:Cardiac Surgical Procedures / Q000009:adverse effects*; D017023:Coronary Angiography; D003490:Cyanosis / Q000175:diagnosis / Q000209:etiology* / Q000601:surgery; D017548:Echocardiography, Transesophageal; D005260:Female; D006801:Humans; D010138:Pacemaker, Artificial / Q000009:adverse effects*; D016459:Prosthesis-Related Infections / Q000175:diagnosis / Q000209:etiology / Q000601:surgery*; D012086:Reoperation; D012804:Sick Sinus Syndrome / Q000209:etiology / Q000601:surgery*; D013927:Thrombosis / Q000175:diagnosis / Q000209:etiology / Q000601:surgery*; D013997:Time Factors; D014188:Transposition of Great Vessels / Q000601:surgery*; D016896:Treatment Outcome
keywords: Cardiac surgical procedures/methods; electrodes, implanted/adverse effects; heart defects, congenital/surgery; postoperative complications; reoperation; transposition of great vessels/complications; treatment outcome