title: A surgical strategy for cor triatriatum atrial septal defect--A1 lam subclass.
abstract: Atrial fibrillation and a heart murmur were diagnosed in a 68-year-old woman during a routine medical examination. She presented 2 years later with pulmonary edema. A transthoracic echocardiography examination revealed a tunneled atrial septal defect (ASD) and severe tricuspid regurgitation. Transesophageal echocardiography and 3-dimensional computed tomography evaluations revealed multiple intracardiac defects, including abnormal atrial septation suggestive of a typical cor triatriatum sinistrum (A1 Lam subclass), a rare congenital defect in adults. The patient underwent tricuspid valve repair with concomitant closure of the ASD by using the cor triatriatum curtain to form an autologous transposition flap. The intraoperative transesophageal and predischarge imaging evaluations confirmed an excellent repair. The patient made a swift recovery and demonstrated improvement in her symptoms at follow-up. This previously undescribed technique eliminates the need for a prosthetic implant and is applicable in >80% of cor triatriatum cases in which an ASD exists.
authors.affiliation: Department of Cardiothoracic Surgery, Lancashire Cardiac Centre, Blackpool, UK. khoshbinuk@yahoo.co.uk
authors.forename: Espeed
authors.initials: E
authors.lastname: Khoshbin
authors.forename: Augustine
authors.initials: A
authors.lastname: Tang
authors.forename: Adrian
authors.initials: A
authors.lastname: Brodison
authors.forename: Franco
authors.initials: F
authors.lastname: Sogliani
mesh_terms: D000015:Abnormalities, Multiple / Q000175:diagnosis / Q000601:surgery; D000368:Aged; D001281:Atrial Fibrillation / Q000175:diagnosis / Q000209:etiology; D006348:Cardiac Surgical Procedures / Q000379:methods*; D003310:Cor Triatriatum / Q000175:diagnosis* / Q000601:surgery*; D017548:Echocardiography, Transesophageal / Q000379:methods; D005260:Female; D005500:Follow-Up Studies; D006337:Heart Murmurs / Q000175:diagnosis / Q000209:etiology; D006344:Heart Septal Defects, Atrial / Q000175:diagnosis* / Q000601:surgery*; D006801:Humans; D021621:Imaging, Three-Dimensional; D035583:Rare Diseases; D018570:Risk Assessment; D014057:Tomography, X-Ray Computed / Q000379:methods; D016896:Treatment Outcome