title: Two-step surgery for a unique case of idiopathic female pseudohermaphroditism. Surgical treatment in an exceptional combined uro-genital malformation.
abstract: A 15 years-old patient was brought to our attention in June 2010 with a complex genito-urinary malformation: fusion of the labia majora and a partial union of labia minora, common urinary and vaginal meatus and clitoromegaly. The patient had a normal sexual feminine hormonal development. After diagnostic iter the patient underwent surgery twice. No signs of hormonal deficency was shown authorizing us to approach the disease as a congenital malformation due to an abnormality of intrauterine development. So surgical treatment was carried out, considering it as the gold standard for this type of malformations. It's considerable to emphasize that the association between clitoromegaly and fusion of the lower third of the urethra with the vagina has not been previously reported in the literature.
authors.affiliation: Sapienza University of Rome, Rome, Italy.
authors.forename: Nicolò
authors.initials: N
authors.lastname: Scuderi
authors.forename: Giovanni
authors.initials: G
authors.lastname: Alei
authors.forename: Michele
authors.initials: M
authors.lastname: Maruccia
authors.forename: Piero
authors.initials: P
authors.lastname: Letizia
authors.forename: Valentina
authors.initials: V
authors.lastname: Sorvillo
authors.forename: Francesco
authors.initials: F
authors.lastname: Ricottilli
authors.forename: Lavinia
authors.initials: L
authors.lastname: Alei
authors.forename: Maria Giuseppina
authors.initials: MG
authors.lastname: Onesti
mesh_terms: D058489:46, XX Disorders of Sex Development / Q000601:surgery*; D000293:Adolescent; D005260:Female; D013509:Gynecologic Surgical Procedures / Q000379:methods; D006801:Humans; D013520:Urologic Surgical Procedures / Q000379:methods