title: A proposal for creating a guideline for cancer registration of the fibromatosis, PEComa group, malignant lymphoma In Situ and dendritic cell tumors (III).
abstract: BACKGROUND
  Understanding the biologic behavior of a tumor is a prerequisite for tumor registration code assignment. The aim of this report was to propose appropriate behavior codes of the International Classification of Disease Oncology 3 (ICD-O3) to rare, yet pathologically interesting hematopoietic and soft tissue tumors.
  
  
  METHODS
  The Study Group for Hematopathology, the Bone and Soft Tissue Pathology Study Group, and the Cancer Registration Committee prepared the questionnaire containing provisional behavior codes of selected diseases.
  
  
  RESULTS
  In situ lesions of mantle cell and follicular lymphomas, dendritic cell tumors, and neoplasms with perivascular epithelioid cell differentiation (PEComa), not otherwise specified were classified as malignant (-/3). The fibromatosis group, with the exception of lipofibromatosis, was proposed as benign (-/0). Lipofibromatosis and several diseases that belong to the PEComa group were proposed as uncertain malignant potential (-/1). For the hematologic and soft tissue tumors, 274 and 288 members of the Korean Society of Pathologists, respectively, provided opinions through questionnaire, and most responders showed agreement with the provisional behavior code proposed.
  
  
  CONCLUSIONS
  The determination of behavior codes for the rare diseases described in this study, especially those of the PEComa group or malignant lymphoma, could be viewed as impractical and premature, but this study provides the basis for future research on this topic.
authors.affiliation: Department of Pathology, St. Vincent's Hospital, The Catholic University of Korea College of Medicine, Suwon, Korea.
authors.forename: Changyoung
authors.initials: C
authors.lastname: Yoo
authors.forename: Chang Suk
authors.initials: CS
authors.lastname: Kang
authors.forename: Yoon La
authors.initials: YL
authors.lastname: Choi
authors.forename: Hye Yoon
authors.initials: HY
authors.lastname: Kang
authors.forename: Jin Man
authors.initials: JM
authors.lastname: Kim
authors.forename: Young Hye
authors.initials: YH
authors.lastname: Koh
authors.forename: Joo Hee
authors.initials: JH
authors.lastname: Lee
authors.forename: Seung Sook
authors.initials: SS
authors.lastname: Lee
authors.forename: In Sun
authors.initials: IS
authors.lastname: Kim
authors.forename: Dong Hoon
authors.initials: DH
authors.lastname: Kim
authors.forename: Yong Ku
authors.initials: YK
authors.lastname: Park
authors.forename: Jin Hee
authors.initials: JH
authors.lastname: Sohn
keywords: Behavior code; Hematologic malignancy; ICD-O3; Soft tissue neoplasms