title: Concomitant occurrence of hypohyperdontia in a patient with Marfan syndrome: a review of the literature and report of a case.
abstract: Marfan syndrome is an autosomal dominant genetic disorder of connective tissue origin that can affect multiple organs. Various oral manifestations have been associated with this syndrome. Hypohyperdontia is a condition of mixed numeric variations that presents a combination of hypodontia with hyperdontia within a single human dentition. The purpose of this paper is to report a case of Marfan syndrome with a concomitant occurrence of hypohyperdontia. A narrative review was also included to describe the other syndromes that had been associated with concomitant hypohyperdontia.
authors.affiliation: Paediatric Dentistry and Orthodontics, Faculty of Dentistry, University of Hong Kong, China.
authors.forename: Sreekanth K
authors.initials: SK
authors.lastname: Mallineni
authors.forename: Jayakumar
authors.initials: J
authors.lastname: Jayaraman
authors.forename: Cynthia K Y
authors.initials: CK
authors.lastname: Yiu
authors.forename: Nigel M
authors.initials: NM
authors.lastname: King
mesh_terms: D000015:Abnormalities, Multiple; D000848:Anodontia; D002675:Child, Preschool; D006801:Humans; D008297:Male; D008382:Marfan Syndrome / Q000503:physiopathology; D014096:Tooth, Supernumerary