title: Festival food coma in cystic fibrosis.
abstract: Children with cystic fibrosis liver disease and portal hypertension are at risk of developing acute hepatic encephalopathy. Even in the presence of normal synthetic liver function these children may have porto-systemic shunting. We report a case of an adolosecent who had cystic fibrosis liver disease and presented with life threatening hepatinc encephalopathy. This case illustrates that it is necessary to consider an appropriate dietary regimen in adolosecents with liver disease to prevent hepatic decompensation.
authors.affiliation: Departments of Respiratory Medicine, The Children's Hospital at Westmead, Sydney, Australia. chetan.pandit@health.nsw.gov.au
authors.forename: Chetan
authors.initials: C
authors.lastname: Pandit
authors.forename: Christie
authors.initials: C
authors.lastname: Graham
authors.forename: Hiran
authors.initials: H
authors.lastname: Selvadurai
authors.forename: Kevin
authors.initials: K
authors.lastname: Gaskin
authors.forename: Peter
authors.initials: P
authors.lastname: Cooper
authors.forename: Peter
authors.initials: P
authors.lastname: van Asperen
mesh_terms: D000293:Adolescent; D003550:Cystic Fibrosis / Q000150:complications*; D005247:Feeding Behavior; D006501:Hepatic Encephalopathy / Q000209:etiology*; D006693:Holidays; D006801:Humans; D022124:Hyperammonemia / Q000209:etiology*; D008103:Liver Cirrhosis / Q000150:complications*; D008297:Male; D011506:Proteins / Q000009:adverse effects*
chemical_list: D011506:Proteins