title: Desmoplastic medulloblastoma arising from an ovarian teratoma: a case report and review of the literature.
abstract: The primary neuroectodermal tumor of the ovary is extremely rare, and it manifests in 3 forms: differentiated, primitive, and anaplastic. The medulloblastoma belongs to the subgroup of primitive neuroectodermal tumor of the ovary. Only 3 cases of ovarian medulloblastoma have been reported in the literature, and all of them are presented without information about the specific pathological subtype. We present the fourth case of a 26-year-old woman who presented with abdominal fullness for months. Ultrasound exam showed a right adnexal mass with cystic feature and foci solid components. A partial oophorectomy was performed, and the mass was a desmoplastic medulloblastoma arising from an ovarian teratoma.
authors.affiliation: Mackay Memorial Hospital, New Taipei City, Taiwan.
authors.forename: Shiuan-Li
authors.initials: SL
authors.lastname: Wey
authors.forename: Chi-Kuan
authors.initials: CK
authors.lastname: Chen
authors.forename: Tze-Chien
authors.initials: TC
authors.lastname: Chen
authors.forename: Tung-Ying
authors.initials: TY
authors.lastname: Chen
mesh_terms: D000328:Adult; D014408:Biomarkers, Tumor / Q000032:analysis; D005260:Female; D006801:Humans; D007150:Immunohistochemistry; D008527:Medulloblastoma / Q000378:metabolism / Q000473:pathology*; D009378:Neoplasms, Multiple Primary / Q000378:metabolism / Q000473:pathology*; D018241:Neuroectodermal Tumors, Primitive, Peripheral / Q000378:metabolism / Q000473:pathology*; D010051:Ovarian Neoplasms / Q000378:metabolism / Q000473:pathology*; D013724:Teratoma / Q000378:metabolism / Q000473:pathology*
chemical_list: D014408:Biomarkers, Tumor
keywords: desmoplastic medulloblastoma; ovarian medulloblastoma; poorly differentiated neuroectodermal tumor; primitive neuroectodermal tumor; teratoma